Huntingtin is a scaffolding protein in the ATM oxidative DNA damage response complex

Human Molecular Genetics

Volumn 26, Issue 2, 2017, Pages 395-406

  Maiuri, Tamara ^a   Mocle, Andrew J ^a   Hung, Claudia L ^a   Xia, Jianrun ^a   van Roon Mom, Willeke M C ^b   Truant, Ray ^a  

^a MCMASTER UNIVERSITY   (Canada)

^b LEIDEN UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

ATM PROTEIN; DNA; HUNTINGTIN; REACTIVE OXYGEN METABOLITE; SCAFFOLD PROTEIN; ATM PROTEIN, HUMAN;

ALLELE; ARTICLE; CONTROLLED STUDY; DNA DAMAGE RESPONSE; ENZYME ACTIVITY; EXCISION REPAIR; FEMALE; FIBROBLAST; HUMAN; HUMAN CELL; HUNTINGTON CHOREA; MALE; MICROSCOPY; OXIDATIVE STRESS; PRIORITY JOURNAL; DNA DAMAGE; DNA REPAIR; GENETICS; METABOLISM; PATHOLOGY; PATHOPHYSIOLOGY;

ALLELES; ATAXIA TELANGIECTASIA MUTATED PROTEINS; DNA DAMAGE; DNA REPAIR; FIBROBLASTS; HUMANS; HUNTINGTIN PROTEIN; HUNTINGTON DISEASE; OXIDATIVE STRESS; REACTIVE OXYGEN SPECIES;

EID: 85016489797     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddw395     Document Type: Article

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