A huntingtin-mediated fast stress response halting endosomal trafficking is defective in Huntington's disease

Human Molecular Genetics

Volumn 24, Issue 2, 2015, Pages 450-462

  Nath, Siddharth ^a   Munsie, Lise N ^b   Truant, Ray ^a  

^a MCMASTER UNIVERSITY   (Canada)

^b UNIVERSITY OF BRITISH COLUMBIA   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

HUNTINGTIN; MUTANT PROTEIN; POLYGLUTAMINE; HTT PROTEIN, HUMAN; NERVE PROTEIN;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CELL GRANULE; CELLULAR DISTRIBUTION; CELLULAR STRESS RESPONSE; CONTROLLED STUDY; CYTOSOL; DNA FLANKING REGION; ENDOSOME; ENERGY METABOLISM; GENE EXPRESSION; HEAT SHOCK; HUNTINGTON CHOREA; INTRACELLULAR TRANSPORT; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; ANIMAL; CHEMISTRY; GENETICS; HUMAN; METABOLISM; PATHOPHYSIOLOGY; PHYSIOLOGICAL STRESS; PROTEIN MOTIF; PROTEIN TRANSPORT; TRANSGENIC MOUSE;

AMINO ACID MOTIFS; ANIMALS; ENDOSOMES; HUMANS; HUNTINGTON DISEASE; MICE; MICE, TRANSGENIC; NERVE TISSUE PROTEINS; PROTEIN TRANSPORT; STRESS, PHYSIOLOGICAL;

EID: 84922424770     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddu460     Document Type: Article

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