Biology of Hsp47 (Serpin H1), a collagen-specific molecular chaperone

Seminars in Cell and Developmental Biology

Volumn 62, Issue , 2017, Pages 142-151

  Ito, Shinya ^a   Nagata, Kazuhiro ^a  

^a KYOTO SANGYO UNIVERSITY   (Japan)

Author keywords

Collagen; Fibrosis; Heat shock protein; Molecular chaperone; Osteogenesis imperfecta; Serpin

Indexed keywords

HEAT SHOCK PROTEIN 47; PROCOLLAGEN; COLLAGEN; PROTEIN BINDING;

BASEMENT MEMBRANE; COLLAGEN FIBRIL; GENE; GENE EXPRESSION REGULATION; GENE MUTATION; HUMAN; MOLECULAR BIOLOGY; NONHUMAN; OSTEOGENESIS IMPERFECTA; PHENOTYPE; PROTEIN PROTEIN INTERACTION; PROTEIN STRUCTURE; REVIEW; SERPINH1 GENE; ANIMAL; BIOLOGICAL MODEL; CHEMISTRY; DISEASES; METABOLISM;

ANIMALS; COLLAGEN; DISEASE; HSP47 HEAT-SHOCK PROTEINS; HUMANS; MODELS, BIOLOGICAL; PHENOTYPE; PROTEIN BINDING;

EID: 85006489381     PISSN: 10849521     EISSN: 10963634     Source Type: Journal    
DOI: 10.1016/j.semcdb.2016.11.005     Document Type: Review

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