Sc65-Null Mice Provide Evidence for a Novel Endoplasmic Reticulum Complex Regulating Collagen Lysyl Hydroxylation

PLoS Genetics

Volumn 12, Issue 4, 2016, Pages

  Heard, Melissa E ^a   Besio, Roberta ^a,c   Weis, MaryAnn ^b   Rai, Jyoti ^b   Hudson, David M ^b   Dimori, Milena ^a   Zimmerman, Sarah M ^a   Kamykowski, Jeffrey A ^a   Hogue, William R ^a   Swain, Frances L ^a   Burdine, Marie S ^a   Mackintosh, Samuel G ^a   Tackett, Alan J ^a   Suva, Larry J ^a,d   Eyre, David R ^b   Morello, Roy ^a  

^a UNIVERSITY OF ARKANSAS FOR MEDICAL SCIENCES   (United States)

^b UNIVERSITY OF WASHINGTON SCHOOL OF MEDICINE   (United States)

^c UNIVERSITY OF PAVIA   (Italy)

^d TEXAS A AND M UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COLLAGEN; CYCLOPHILIN B; OXYGENASE; SYNAPTONEMAL COMPLEX 65; UNCLASSIFIED DRUG; AUTOANTIGEN; CYCLOPHILIN; PROCOLLAGEN LYSINE 2 OXOGLUTARATE 5 DIOXYGENASE; PROCOLLAGEN PROLINE 2 OXOGLUTARATE 4 DIOXYGENASE; PROLINE, 2-OXOGLUTARATE 3-DIOXYGENASE; SC65 PROTEIN, MOUSE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BONE MASS; COLLAGEN SYNTHESIS; CONNECTIVE TISSUE DISEASE; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; ENZYME ACTIVITY; EXON; FKBP10 GENE; GENE FREQUENCY; GENE MUTATION; GENOTYPE; HETEROZYGOSITY; HYDROXYLATION; LONG BONE; MOUSE; NONHUMAN; PROTEIN CROSS LINKING; PROTEIN DEPLETION; PROTEIN INTERACTION; PROTEIN PROCESSING; PROTEIN TARGETING; SKIN FRAGILITY; ANIMAL; BIOSYNTHESIS; BONE; C57BL MOUSE; CELL LINE; EXTRACELLULAR MATRIX; GENETICS; KNOCKOUT MOUSE; METABOLISM; OSTEOGENESIS IMPERFECTA; PATHOLOGY; PHYSIOLOGY;

ANIMALS; AUTOANTIGENS; BONE AND BONES; CELL LINE; COLLAGEN; CYCLOPHILINS; ENDOPLASMIC RETICULUM; EXTRACELLULAR MATRIX; HYDROXYLATION; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; OSTEOGENESIS IMPERFECTA; PROCOLLAGEN-LYSINE, 2-OXOGLUTARATE 5-DIOXYGENASE; PROCOLLAGEN-PROLINE DIOXYGENASE; PROTEIN PROCESSING, POST-TRANSLATIONAL;

EID: 84964815325     PISSN: 15537390     EISSN: 15537404     Source Type: Journal    
DOI: 10.1371/journal.pgen.1006002     Document Type: Article

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