GGGGCC microsatellite RNA is neuritically localized, induces branching defects, and perturbs transport granule function

eLife

Volumn 4, Issue DECEMBER2015, 2015, Pages

  Burguete, Alondra Schweizer ^a   Almeida, Sandra ^b   Gao, Fen Biao ^b   Kalb, Robert ^c   Akins, Michael R ^d   Bonini, Nancy M ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b UNIVERSITY OF MASSACHUSETTS MEDICAL SCHOOL   (United States)

^c UNIVERSITY OF PENNSYLVANIA   (United States)

^d DREXEL UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

FRAGILE X MENTAL RETARDATION PROTEIN; MESSENGER RNA; MICROSATELLITE RNA; NUCLEIC ACID; POLYGLUTAMINE; UNCLASSIFIED DRUG; C9ORF72 PROTEIN, HUMAN; MICROSATELLITE DNA; PROTEIN; RNA;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ARTICLE; CELL GRANULE; CELLULAR DISTRIBUTION; CONTROLLED STUDY; DISEASE SEVERITY; DROSOPHILA; FRONTOTEMPORAL DEMENTIA; GC RICH SEQUENCE; GENETIC TRANSFECTION; GGGGCC RNA REPEAT; IN SITU HYBRIDIZATION; NERVE DEGENERATION; NERVE FIBER GROWTH; NONHUMAN; NUCLEOTIDE REPEAT; ONSET AGE; RAT; RNA TRANSPORT; SPINAL CORD NERVE CELL; ANIMAL; CELL CULTURE; DISEASE MODEL; GENETICS; HUMAN; METABOLISM; NEURITE; PATHOLOGY;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CELLS, CULTURED; CYTOPLASMIC GRANULES; DISEASE MODELS, ANIMAL; DROSOPHILA; HUMANS; MICROSATELLITE REPEATS; NEURITES; PROTEINS; RNA;

EID: 84956943850     PISSN: None     EISSN: 2050084X     Source Type: Journal    
DOI: 10.7554/eLife.08881     Document Type: Article

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