Impaired Neural Differentiation of Induced Pluripotent Stem Cells Generated from a Mouse Model of Sandhoff Disease

PLoS ONE

Volumn 8, Issue 1, 2013, Pages

  Ogawa, Yasuhiro ^a   Tanaka, Makoto ^a   Tanabe, Miho ^a   Suzuki, Toshihiro ^a   Togawa, Tadayasu ^a   Fukushige, Tomoko ^b   Kanekura, Takuro ^b   Sakuraba, Hitoshi ^a   Oishi, Kazuhiko ^a  

^a MEIJI PHARMACEUTICAL UNIVERSITY   (Japan)

^b KAGOSHIMA UNIVERSITY   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

GANGLIOSIDE GM2;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL LINEAGE; CONTROLLED STUDY; GENE; HEXB GENE; MOUSE; NERVE CELL DEGENERATION; NERVE CELL DIFFERENTIATION; NEURAL STEM CELL; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PLURIPOTENT STEM CELL; SANDHOFF DISEASE;

ANIMALS; BETA-HEXOSAMINIDASE BETA CHAIN; CELL DIFFERENTIATION; DISEASE MODELS, ANIMAL; INDUCED PLURIPOTENT STEM CELLS; MALE; MICE; MICE, KNOCKOUT; NEURONS; PHENOTYPE; SANDHOFF DISEASE;

EID: 84873179164     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0055856     Document Type: Article

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