Marked reduction of Na+, K+-ATPase and creatine kinase activities induced by acute lysine administration in glutaryl-CoA dehydrogenase deficient mice

Molecular Genetics and Metabolism

Volumn 107, Issue 1-2, 2012, Pages 81-86

  Amaral, Alexandre Umpierrez ^a   Cecatto, Cristiane ^a   Seminotti, Bianca ^a   Zanatta, Ângela ^a   Fernandes, Carolina Gonçalves ^a   Busanello, Estela Natacha Brandt ^a   Braga, Luisa Macedo ^b   Ribeiro, César Augusto João ^a   de Souza, Diogo Onofre Gomes ^a   Woontner, Michael ^c   Koeller, David M ^d   Goodman, Stephen ^c   Wajner, Moacir ^a,e  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b Fundacao Estadual de Producao e Pesquisa em Saude   (Brazil)

^c UNIVERSITY OF COLORADO   (United States)

^d OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

^e HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

Author keywords

Bioenergetics; Brain; Creatine kinase activity; Glutaric acidemia type I; Glutaryl CoA dehydrogenase deficient mice; Na+, K+ ATPase activity

Indexed keywords

ADENOSINE TRIPHOSPHATASE (POTASSIUM SODIUM); ADENOSINE TRIPHOSPHATASE (POTASSIUM); CREATINE KINASE; GLUTARYL COENZYME A DEHYDROGENASE; LYSINE; SODIUM CHLORIDE;

ANIMAL EXPERIMENT; ARTICLE; BIOENERGY; BRAIN DAMAGE; CONTROLLED STUDY; ENZYME ACTIVITY; MOUSE; MUSCLE HYPOTONIA; NONHUMAN; PRIORITY JOURNAL; RESPIRATORY CHAIN; SKELETAL MUSCLE; WILD TYPE;

AMINO ACID METABOLISM, INBORN ERRORS; ANIMALS; BRAIN; BRAIN DISEASES, METABOLIC; CREATINE KINASE; DISEASE MODELS, ANIMAL; ELECTRON TRANSPORT; GLUTARYL-COA DEHYDROGENASE; HEART; KETOGLUTARATE DEHYDROGENASE COMPLEX; LYSINE; MICE; MICE, KNOCKOUT; MUSCLE, SKELETAL; MYOCARDIUM; SODIUM-POTASSIUM-EXCHANGING ATPASE;

MUS;

EID: 84866148060     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2012.04.015     Document Type: Article

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