Premature death and neurologic abnormalities in transgenic mice expressing a mutant huntingtin exon-2 fragment

Human Molecular Genetics

Volumn 20, Issue 8, 2011, Pages 1633-1642

  Tebbenkamp, Andrew T N ^a   Swing, Debbie ^b   Tessarollo, Lino ^b   Borchelt, David R ^a  

^a UNIVERSITY OF FLORIDA COLLEGE OF MEDICINE   (United States)

^b NATIONAL CANCER INSTITUTE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COMPLEMENTARY DNA; HUNTINGTIN; MUTANT PROTEIN;

AMINO TERMINAL SEQUENCE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DEATH; EXON; EXPRESSION VECTOR; FEMALE; GENE EXPRESSION; LIFE EXPECTANCY; MALE; MOUSE; NEUROLOGIC DISEASE; NEUROPATHOLOGY; NONHUMAN; NUCLEOTIDE SEQUENCE; PHENOTYPE; PRION; PRIORITY JOURNAL; PROMOTER REGION; TRANSGENIC MOUSE; WEIGHT REDUCTION;

ANIMALS; BEHAVIOR, ANIMAL; BODY WEIGHT; BRAIN; DISEASE MODELS, ANIMAL; EXONS; HUMANS; INCLUSION BODIES; LIFE EXPECTANCY; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; ORGAN SIZE; PEPTIDE FRAGMENTS; PHENOTYPE; RECOMBINANT FUSION PROTEINS; SKIN;

MUS; MUS MUSCULUS;

EID: 79953123196     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddr040     Document Type: Article

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