Long glutamine tracts cause nuclear localization of a novel form of huntingtin in medium spiny striatal neurons in Hdh(Q92) and Hdh(Q111) knock-in mice

Human Molecular Genetics

Volumn 9, Issue 4, 2000, Pages 503-513

  Wheeler, Vanessa C ^a   White, Jacqueline K ^a,e   Gutekunst, Claire Anne ^b   Vrbanac, Vladimir ^a   Weaver, Meredith ^a   Li, Xiao Jiang ^b   Li, Shi Hua ^b   Yi, Hong ^b   Vonsattel, Jean Paul ^c   Gusella, James F ^a   Hersch, Steven ^b   Auerbach, Wojtek ^d   Joyner, Alexandra L ^d   MacDonald, Marcy E ^a  

^a Molecular Neurogenetics Unit   (United States)

^b EMORY UNIVERSITY SCHOOL OF MEDICINE   (United States)

^c Lab Molec Neuropathology M   (United States)

^d NEW YORK UNIVERSITY SCHOOL OF MEDICINE   (United States)

^e WELLCOME TRUST SANGER INSTITUTE   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

HUNTINGTIN; NERVE PROTEIN; POLYGLUTAMINE;

AMINO TERMINAL SEQUENCE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL NUCLEUS; CORPUS STRIATUM; DOMINANT INHERITANCE; HUNTINGTON CHOREA; MOUSE; NERVE; NONHUMAN; PRIORITY JOURNAL; PROTEIN LOCALIZATION;

ANIMALIA; SPINY;

EID: 0034163497     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/9.4.503     Document Type: Article

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