The early-onset torsion dystonia-associated protein, torsinA, is a homeostatic regulator of endoplasmic reticulum stress response

Human Molecular Genetics

Volumn 19, Issue 18, 2010, Pages 3502-3515

  Chen, Pan ^a   Burdette, Alexander J ^a   Porter, J Christopher ^a   Ricketts, John C ^a   Fox, Stacey A ^a   Nery, Flavia C ^c   Hewett, Jeffrey W ^c   Berkowitz, Laura A ^a   Breakefield, Xandra O ^c   Caldwell, Kim A ^a,b   Caldwell, Guy A ^a,b  

^a UNIVERSITY OF ALABAMA   (United States)

^b UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

^c MASSACHUSETTS GENERAL HOSPITAL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE TRIPHOSPHATASE; PROTEIN; PROTEIN TORSIN A; UNCLASSIFIED DRUG;

ARTICLE; CAENORHABDITIS ELEGANS; CONTROLLED STUDY; ENDOPLASMIC RETICULUM STRESS; ENZYME ACTIVITY; GENE DELETION; GENE MUTATION; HOMEOSTASIS; IN VIVO STUDY; NEMATODE; NONHUMAN; PLASMID; PRIORITY JOURNAL; PROTEIN FOLDING; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; RNA INTERFERENCE; TORSION DYSTONIA; TRANSGENIC ORGANISM;

AGE OF ONSET; ANIMALS; ANIMALS, GENETICALLY MODIFIED; CAENORHABDITIS ELEGANS; CELLS, CULTURED; DISEASE MODELS, ANIMAL; DYSTONIA; ENDOPLASMIC RETICULUM; FIBROBLASTS; HOMEOSTASIS; HUMANS; MICE; MICE, KNOCKOUT; MOLECULAR CHAPERONES; PROTEIN TRANSPORT; STRESS, PHYSIOLOGICAL;

CAENORHABDITIS ELEGANS; MUS; NEMATODA;

EID: 77956113164     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddq266     Document Type: Article

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