Dorfin ameliorates phenotypes in a transgenic mouse model of amyotrophic lateral sclerosis

Journal of Neuroscience Research

Volumn 88, Issue 1, 2010, Pages 123-135

  Sone, Jun ^a   Niwa, Jun Ichi ^a,b   Kawai, Kaori ^a   Ishigaki, Shinsuke ^a   Yamada, Shin Ichi ^a   Adachi, Hiroaki ^a   Katsuno, Masahisa ^a   Tanaka, Fumiaki ^a   Doyu, Manabu ^a,b   Sobue, Gen ^a  

^a NAGOYA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^b AICHI MEDICAL UNIVERSITY   (Japan)

Author keywords

ALS; Dorfin; G93A mutant SOD1; Neurodegeneration; Ubiquitin ligase

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; DORFIN PROTEIN; MUTANT PROTEIN; UBIQUITIN PROTEIN LIGASE E3; UNCLASSIFIED DRUG;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; GENE OVEREXPRESSION; MOTONEURON; MOUSE; NERVE CELL DEGENERATION; NEUROLOGY; NONHUMAN; NUCLEOTIDE SEQUENCE; PHENOTYPE; PRIORITY JOURNAL; SPINAL CORD; TRANSGENIC MOUSE; VENTRAL ROOT;

AMYOTROPHIC LATERAL SCLEROSIS; ANALYSIS OF VARIANCE; ANIMALS; ASTROCYTES; BLOTTING, WESTERN; DISEASE MODELS, ANIMAL; GENE DOSAGE; IMMUNOHISTOCHEMISTRY; IMMUNOPRECIPITATION; KAPLAN-MEIERS ESTIMATE; MICE; MICE, TRANSGENIC; MOTOR SKILLS; NERVE DEGENERATION; NEURONS; PHENOTYPE; ROTAROD PERFORMANCE TEST; SPINAL CORD; SPINAL NERVE ROOTS; SUPEROXIDE DISMUTASE; UBIQUITIN-PROTEIN LIGASES;

EID: 73949087427     PISSN: 03604012     EISSN: 10974547     Source Type: Journal    
DOI: 10.1002/jnr.22175     Document Type: Article

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