Dorfin prevents cell death by reducing mitochondrial localizing mutant superoxide dismutase 1 in a neuronal cell model of familial amyotrophic lateral sclerosis

Journal of Neurochemistry

Volumn 89, Issue 1, 2004, Pages 64-72

  Takeuchi, Hideyuki ^a   Niwa, Jun Ichi ^a   Hishikawa, Nozomi ^a   Ishigaki, Shinsuke ^a   Tanaka, Fumiaki ^a   Doyu, Manabu ^a   Sobue, Gen ^a  

^a NAGOYA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

Amyotrophic lateral sclerosis; Dorfin; Mitochondria; Neuronal cell death; Superoxide dismutase 1; Ubiquitin ligase

Indexed keywords

CASPASE; COPPER ZINC SUPEROXIDE DISMUTASE; CYTOCHROME C; DORFIN; MUTANT PROTEIN; SUPEROXIDE DISMUTASE; UBIQUITIN PROTEIN LIGASE; UNCLASSIFIED DRUG;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANTIOXIDANT ACTIVITY; ARTICLE; CONTROLLED STUDY; ENZYME ACTIVATION; ENZYME DEGRADATION; ENZYME LOCALIZATION; ENZYME RELEASE; FAMILIAL DISEASE; HUMAN; MITOCHONDRION; MOUSE; NERVE CELL NECROSIS; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL; SIGNAL TRANSDUCTION;

ANIMALIA;

EID: 1842562857     PISSN: 00223042     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1471-4159.2003.02289.x     Document Type: Article

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