Respiration and growth defects in transmitochondrial cell lines carrying the 11778 mutation associated with Leber's hereditary optic neuropathy

Journal of Biological Chemistry

Volumn 271, Issue 22, 1996, Pages 13155-13161

  Hofhaus, Götz ^a,d   Johns, Donald R ^b   Hurko, Orest ^c   Attardi, Giuseppe ^a   Chomyn, Anne ^a  

^a CALIFORNIA INSTITUTE OF TECHNOLOGY   (United States)

^b HARVARD MEDICAL SCHOOL   (United States)

^c JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^d HEINRICH HEINE UNIVERSITY   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

MITOCHONDRIAL DNA; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE;

ARTICLE; CELL GROWTH; CONTROLLED STUDY; ENZYME ACTIVITY; GENE MUTATION; HEREDITARY OPTIC ATROPHY; HUMAN; HUMAN CELL; MITOCHONDRIAL MEMBRANE; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL; RESPIRATORY CHAIN;

ADULT; CELL DIVISION; CELL LINE; CELL LINE, TRANSFORMED; DNA, MITOCHONDRIAL; ELECTRON TRANSPORT; HUMANS; MALE; MIDDLE AGED; MITOCHONDRIA; MUTATION; NAD(P)H DEHYDROGENASE (QUINONE); NADH DEHYDROGENASE; OPTIC ATROPHIES, HEREDITARY; OXIDATIVE PHOSPHORYLATION; OXYGEN;

EID: 15844414869     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.271.22.13155     Document Type: Article

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