Conditional mouse models for friedreich ataxia, a neurodegenerative disorder associating cardiomyopathy

Handbook of Experimental Pharmacology

Volumn 178, Issue , 2007, Pages 365-375

  Puccio, H ^a  

^a UNIVERSITÉ DE STRASBOURG   (France)

Author keywords

Ataxia; Cardiomyopathy; Frataxin; Iron; Iron sulfur cluster; Mitochondria; Neurodegeneration

Indexed keywords

ANIMAL; AUTOPHAGY; CARDIOMYOPATHY; DISEASE MODEL; FRIEDREICH ATAXIA; HUMAN; MITOCHONDRION; MOUSE; PATHOLOGY; REVIEW; ULTRASTRUCTURE;

ANIMALS; AUTOPHAGY; CARDIOMYOPATHIES; DISEASE MODELS, ANIMAL; FRIEDREICH ATAXIA; HUMANS; MICE; MITOCHONDRIA;

EID: 33846939794     PISSN: 01712004     EISSN: 18650325     Source Type: Book Series    
DOI: 10.1007/978-3-540-35109-2_15     Document Type: Article

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