Direct interaction with filamins modulates the stability and plasma membrane expression of CFTR

Journal of Clinical Investigation

Volumn 117, Issue 2, 2007, Pages 364-374

  Thelin, William R ^a   Chen, Yun ^a   Gentzsch, Martina ^a   Kreda, Silvia M ^b   Sallee, Jennifer L ^a   Scarlett, Cameron O ^b   Borchers, Christoph H ^b   Jacobson, Ken ^a   Stutts, M Jackson ^b   Milgram, Sharon L ^a  

^a UNIVERSITY OF NORTH CAROLINA   (United States)

^b UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ACTIN; FILAMIN; PHENYLALANINE; SERINE; TRANSMEMBRANE CONDUCTANCE REGULATOR;

AMINO TERMINAL SEQUENCE; ARTICLE; BIOACCUMULATION; CELL MEMBRANE; CELL SURFACE; CONTROLLED STUDY; EMBRYO; FEMALE; GENE DISRUPTION; HUMAN; HUMAN CELL; LYSOSOME; METABOLIC REGULATION; MISSENSE MUTATION; MODULATION; MOLECULAR DYNAMICS; NONHUMAN; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN BINDING; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN PROTEIN INTERACTION; PROTEIN TRANSPORT;

AMINO ACID SEQUENCE; AMINO ACID SUBSTITUTION; ANIMALS; BINDING SITES; CELL LINE; CELL MEMBRANE; CONTRACTILE PROTEINS; CRICETINAE; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; DRUG STABILITY; HELA CELLS; HUMANS; KINETICS; MICROFILAMENT PROTEINS; MODELS, MOLECULAR; MOLECULAR SEQUENCE DATA; MUTATION, MISSENSE; PROTEIN BINDING; PROTEIN CONFORMATION; PROTEOMICS; RECOMBINANT PROTEINS; SEQUENCE HOMOLOGY, AMINO ACID;

EID: 33846834167     PISSN: 00219738     EISSN: 15588238     Source Type: Journal    
DOI: 10.1172/JCI30376     Document Type: Article

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