Removal of multiple arginine-framed trafficking signals overcomes misprocessing of ΔF508 CFTR present in most patients with cystic fibrosis

Molecular Cell

Volumn 4, Issue 1, 1999, Pages 137-142

  Chang, Xiu bao ^a   Cui, Liying ^a   Hou, Yue xian ^a   Jensen, Timothy J ^a   Aleksandrov, Andrei A ^a   Mengos, April ^a   Riordan, John R ^a  

^a MAYO CLINIC   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

TRANSMEMBRANE CONDUCTANCE REGULATOR;

AMINO ACID SEQUENCE; AMINO ACID SUBSTITUTION; ARTICLE; CYSTIC FIBROSIS; HUMAN; PROTEIN ANALYSIS; PROTEIN LOCALIZATION; PROTEIN PROCESSING; PROTEIN STRUCTURE; SIGNAL TRANSDUCTION; STRUCTURE ANALYSIS;

EID: 0033166350     PISSN: 10972765     EISSN: None     Source Type: Journal    
DOI: 10.1016/S1097-2765(00)80196-3     Document Type: Article

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