MBTPS1/SKI-1/S1P proprotein convertase is required for ECM signaling and axial elongation during somitogenesis and vertebral development

Human Molecular Genetics

Volumn 24, Issue 10, 2015, Pages 2884-2898

  Achilleos, Annita ^a   Huffman, Nichole T ^b   Marcinkiewicyz, Edwidge ^c   Seidah, Nabil G ^c   Chen, Qian ^b   Dallas, Sarah L ^b   Trainor, Paul A ^a,d   Gorski, Jeff P ^b  

^a STOWERS INSTITUTE FOR MEDICAL RESEARCH   (United States)

^b UNIVERSITY OF MISSOURI KANSAS CITY SCHOOL OF DENTISTRY   (United States)

^c CLIN RESEARCH INSTITUTE OF MONTREAL   (Canada)

^d UNIVERSITY OF KANSAS SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CRE RECOMBINASE; FIBRILLIN 2; FIBRONECTIN; GLYCOSYLTRANSFERASE; LAMININ; MEMBRANE BOUND TRANSCRIPTION FACTOR PROTEASE; SERINE PROTEINASE; SITE 1 PROTEASE; SUBTILISIN KEXIN ISOZYME 1; TRANSCRIPTION FACTOR; UNCLASSIFIED DRUG; FGF8 PROTEIN, MOUSE; FIBROBLAST GROWTH FACTOR 8; LFNG PROTEIN, MOUSE; MEMBRANE-BOUND TRANSCRIPTION FACTOR PEPTIDASE, SITE 1;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BONE DEVELOPMENT; CAUDAL REGRESSION SYNDROME; CONTROLLED STUDY; DERMIS; EMBRYO; EMBRYO DEVELOPMENT; EXTRACELLULAR MATRIX; FEMALE; GENE DELETION; HINDLIMB; LIMB DEVELOPMENT; LOSS OF FUNCTION MUTATION; LUMBAR VERTEBRA; MALE; MESODERM; MOUSE; NONHUMAN; OSCILLATION; OSSIFICATION; PARASPINAL MUSCLE; PATHOGENESIS; PERIODICITY; PHENOTYPE; PRIORITY JOURNAL; PROMOTER REGION; PROTEIN DEGRADATION; SACRUM; SECOND CERVICAL VERTEBRA; SIGNAL TRANSDUCTION; SOMITE; TENDON; VERTEBRA; VERTEBRA MALFORMATION; ABNORMALITIES; ANAL CANAL; ANIMAL; EMBRYOLOGY; GENE INACTIVATION; GENETICS; KNOCKOUT MOUSE; MENINGOCELE; METABOLISM; MORPHOGENESIS; ORGANOGENESIS; RECTUM; SPINE; TERATOMA;

ANAL CANAL; ANIMALS; BODY PATTERNING; EXTRACELLULAR MATRIX; FEMALE; FIBROBLAST GROWTH FACTOR 8; GENE KNOCKOUT TECHNIQUES; GLYCOSYLTRANSFERASES; MALE; MENINGOCELE; MICE; MICE, KNOCKOUT; ORGANOGENESIS; PROPROTEIN CONVERTASES; RECTUM; SACRUM; SERINE ENDOPEPTIDASES; SIGNAL TRANSDUCTION; SOMITES; SPINE; TERATOMA;

EID: 84929833023     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddv050     Document Type: Article

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