Material and mechanical properties of bones deficient for fibrillin-1 or fibrillin-2 microfibrils

Matrix Biology

Volumn 30, Issue 3, 2011, Pages 188-194

  Arteaga Solis, Emilio ^a   Sui Arteaga, Lee ^a   Kim, Minwook ^b   Schaffler, Mitchell B ^a   Jepsen, Karl J ^a   Pleshko, Nancy ^c   Ramirez, Francesco ^a  

^a MOUNT SINAI SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

^c Temple University   (United States)

Author keywords

Bone material and mechanical properties; Congenital contractural arachnodactyly; Fibrillin; Marfan syndrome; TGF

Indexed keywords

FIBRILLIN 1; FIBRILLIN 2; TRANSFORMING GROWTH FACTOR BETA;

ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; BONE DEVELOPMENT; BONE STRENGTH; BONE STRUCTURE; FIBER; HISTOLOGY; INFRARED SPECTROSCOPY; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN ASSEMBLY; RAMAN SPECTROMETRY; SIGNAL TRANSDUCTION;

ANIMALS; BIOMECHANICS; BONE DENSITY; CARBONATES; FEMUR; HUMANS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MICROFIBRILS; MICROFILAMENT PROTEINS; PHOSPHATES; STRESS, MECHANICAL; TORSION, MECHANICAL;

MUS;

EID: 79955531352     PISSN: 0945053X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.matbio.2011.03.004     Document Type: Article

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