Metabolic dysfunction and altered mitochondrial dynamics in the utrophin-Dystrophin deficient mouse model of duchenne muscular dystrophy

PLoS ONE

Volumn 10, Issue 4, 2015, Pages

  Pant, Meghna ^a   Sopariwala, Danesh H ^a   Bal, Naresh C ^a   Lowe, Jeovanna ^b   Delfín, Dawn A ^b,c   Rafael Fortney, Jill ^b   Periasamy, Muthu ^a  

^a OHIO STATE UNIVERSITY   (United States)

^b THE OHIO STATE UNIVERSITY COLLEGE OF MEDICINE   (United States)

^c UNIVERSITY OF NEW MEXICO   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CITRATE SYNTHASE; DYNAMIN RELATED PROTEIN 1; DYSTROPHIN; GLYCERALDEHYDE 3 PHOSPHATE DEHYDROGENASE; HEXOKINASE; HEXOKINASE 1; HEXOKINASE 2; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE KINASE; LACTATE DEHYDROGENASE; MEMBRANE PROTEIN; MITOCHONDRIAL TRANSCRIPTION FACTOR A; MITOFUSIN 2; OXYGEN; PYRUVATE KINASE; PYRUVIC ACID; UNCLASSIFIED DRUG; UTROPHIN; DNM1L PROTEIN, MOUSE; DYNAMIN; GLUCOSE; GUANOSINE TRIPHOSPHATASE; HK1 PROTEIN, MOUSE; MFN2 PROTEIN, MOUSE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BASAL METABOLIC RATE; CONTROLLED STUDY; DISEASE MODEL; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DUCHENNE MUSCULAR DYSTROPHY; ENERGY EXPENDITURE; EXTENSOR DIGITORUM LONGUS MUSCLE; GLYCOLYSIS; METABOLIC DISORDER; MITOCHONDRIAL DYNAMICS; MOUSE; MUSCLE METABOLISM; MUSCLE STRENGTH; NONHUMAN; OXYGEN CONSUMPTION; PROTEIN EXPRESSION; SLOW MUSCLE FIBER; UPREGULATION; ANIMAL; ANIMAL MUSCULAR DYSTROPHY; DEFICIENCY; ENERGY METABOLISM; GENETICS; KNOCKOUT MOUSE; MALE; METABOLISM; MUSCLE CONTRACTION; SKELETAL MUSCLE; ULTRASTRUCTURE;

ANIMALIA; MUS;

ANIMALS; DISEASE MODELS, ANIMAL; DYNAMINS; DYSTROPHIN; ENERGY METABOLISM; GLUCOSE; GTP PHOSPHOHYDROLASES; HEXOKINASE; MALE; MICE; MICE, KNOCKOUT; MITOCHONDRIAL DYNAMICS; MUSCLE CONTRACTION; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, ANIMAL; MUSCULAR DYSTROPHY, DUCHENNE; OXYGEN CONSUMPTION; PYRUVATE KINASE; PYRUVIC ACID; UTROPHIN;

EID: 84928889829     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0123875     Document Type: Article

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