Comparison of skeletal muscle pathology and motor function of dystrophin and utrophin deficient mouse strains

Neuromuscular Disorders

Volumn 22, Issue 5, 2012, Pages 406-417

  van Putten, Maaike ^a   Kumar, Darshan ^a   Hulsker, Margriet ^a   Hoogaars, Willem M H ^a   Plomp, Jaap J ^a   van Opstal, Annemarieke ^a   van Iterson, Maarten ^a   Admiraal, Peter ^a   van Ommen, Gert Jan B ^a   't Hoen, Peter A C ^a   Aartsma Rus, Annemieke ^a  

^a LEIDEN UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

Biomarkers; Duchenne muscular dystrophy; Dystrophin; Functional tests; Histopathology; Utrophin

Indexed keywords

BIOLOGICAL MARKER; CREATINE KINASE; DYSTROPHIN; UTROPHIN;

ALLELE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL REGENERATION; CELL STRUCTURE; CONTROLLED STUDY; CREATINE KINASE BLOOD LEVEL; DISEASE COURSE; DISEASE SEVERITY; DUCHENNE MUSCULAR DYSTROPHY; FIBROSIS; GENE EXPRESSION; GENETIC DISORDER; HISTOLOGY; MALE; MOTOR PERFORMANCE; MOUSE; MOUSE STRAIN; MUSCLE FUNCTION; NECROSIS; NEUROMUSCULAR SYNAPSE; NONHUMAN; ONSET AGE; PRIORITY JOURNAL; PROTEIN DEFICIENCY; ROTAROD TEST; SKELETAL MUSCLE; WILD TYPE;

ANIMALS; DISEASE MODELS, ANIMAL; DYSTROPHIN; MICE; MICE, INBRED MDX; MICE, KNOCKOUT; MOTOR ACTIVITY; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, ANIMAL; MUSCULAR DYSTROPHY, DUCHENNE; SURVIVAL ANALYSIS; UTROPHIN;

EID: 84857125347     PISSN: 09608966     EISSN: 18732364     Source Type: Journal    
DOI: 10.1016/j.nmd.2011.10.011     Document Type: Article

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