Impaired mitochondrial oxidative phosphorylation in skeletal muscle of the dystrophin-deficient mdx mouse

Molecular and Cellular Biochemistry

Volumn 183, Issue 1-2, 1998, Pages 87-96

  Kuznetsov, Andrey V ^a   Winkler, Kirstin ^a   Wiedemann, Falk R ^a   Von Bossanyi, Peter ^b   Dietzmann, Knut ^b   Kunz, Wolfram S ^a,b  

^a Klinik fur Neurologie   (Germany)

^b OTTO VON GUERICKE UNIVERSITY   (Germany)

Author keywords

Dystrophin deficiency; Mdx mice; Mitochondria; Oxidative phosphorylation; Skeletal and cardiac muscles; Skinned fibers

Indexed keywords

DYSTROPHIN; HEMOPROTEIN; MITOCHONDRIAL ENZYME;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DUCHENNE MUSCULAR DYSTROPHY; ENZYME ACTIVITY; FEMALE; METABOLIC RATE; MITOCHONDRIAL MEMBRANE; MITOCHONDRIAL RESPIRATION; MOUSE; MUSCLE BIOPSY; NONHUMAN; OXIDATIVE PHOSPHORYLATION; RESPIRATORY CHAIN; SKELETAL MUSCLE;

ADOLESCENT; ANIMALS; CHILD; CHILD, PRESCHOOL; DISEASE MODELS, ANIMAL; DYSTROPHIN; FEMALE; HUMANS; INFANT; MALE; MICE; MICE, INBRED C57BL; MICE, INBRED MDX; MITOCHONDRIA, MUSCLE; MUSCULAR DYSTROPHY, ANIMAL; OXIDATIVE PHOSPHORYLATION;

ANIMALIA; MUSCULUS;

EID: 0031800369     PISSN: 03008177     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1006868130002     Document Type: Article

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