Loss of polycystin-1 in human cyst-lining epithelia leads to ciliary dysfunction

Journal of the American Society of Nephrology

Volumn 17, Issue 4, 2006, Pages 1015-1025

  Nauli, Surya M ^a   Rossetti, Sandro ^b   Kolb, Robert J ^a   Alenghat, Francis J ^a   Consugar, Mark B ^b   Harris, Peter C ^b   Ingber, Donald E ^a   Loghman Adham, Mahmoud ^c   Zhou, Jing ^a,d  

^a HARVARD MEDICAL SCHOOL   (United States)

^b Mayo Clinic   (United States)

^c SAINT LOUIS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^d HARVARD INSTITUTES OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CALCIUM; POLYCYSTIN 1; POLYCYSTIN 2;

ANIMAL CELL; ARTICLE; AUTOSOMAL DOMINANT DISORDER; CALCIUM CELL LEVEL; CALCIUM TRANSPORT; CELL CULTURE; CELL IMMORTALIZATION; CELL STIMULATION; CILIARY DYSKINESIA; CONTROLLED STUDY; EPITHELIUM CELL; FLOW; FLUID FLOW; GENE; GENE MUTATION; GERM LINE; HUMAN; HUMAN CELL; KIDNEY CYST; KIDNEY EPITHELIUM; KIDNEY POLYCYSTIC DISEASE; KIDNEY TUBULE; MECHANICAL STIMULATION; MECHANOSENSATION; MOUSE; NONHUMAN; NULL ALLELE; PKD1 GENE; PRIORITY JOURNAL; PROTEIN DEPLETION; PROTEIN EXPRESSION; PROTEIN FUNCTION; SENSATION; SHEAR STRESS; SOMATIC MUTATION;

EID: 33645463316     PISSN: 10466673     EISSN: None     Source Type: Journal    
DOI: 10.1681/ASN.2005080830     Document Type: Article

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