Peroxisomes, peroxisomal diseases, and the hepatotoxicity induced by peroxisomal metabolites

Current Drug Metabolism

Volumn 13, Issue 10, 2012, Pages 1401-1411

  Wanders, Ronald J A ^a   Ferdinandusse, Sacha ^a  

^a UNIVERSITY OF AMSTERDAM   (Netherlands)

Author keywords

Fatty acid metabolism; Fatty acids; Hepatoxicity; Peroxisomes

Indexed keywords

2,6,10,14 TETRAMETHYLPENTADECANOIC ACID; BILE ACID; DIHYDROXYCHOLANOIC ACID; TETRACOSAHEXAENOIC ACID; TRIHYDROXYCHOLESTANOIC ACID; UNCLASSIFIED DRUG; VERY LONG CHAIN FATTY ACID;

2 METHYL ACYL COA RACEMASE DEFICIENCY; ACYL COA OXIDASE 1 DEFICIENCY; ADRENOLEUKODYSTROPHY; ARTICLE; BILE ACID SYNTHESIS; CELL FUNCTION; CHONDRODYSPLASIA PUNCTATA; D BIFUNCTIONAL PROTEIN DEFICIENCY; DISORDERS OF ETHERPHOSPHOLIPID BIOSYNTHESIS; DISORDERS OF FATTY ACID ALPHA OXIDATION; DISORDERS OF PEROXISOMAL FUNCTIONS; ENZYME DEFECT; FATTY ACID OXIDATION; HUMAN; LIVER TOXICITY; METABOLITE; MITOCHONDRIAL RESPIRATION; NONHUMAN; OXALOSIS 1; OXIDATIVE PHOSPHORYLATION; PEROXISOME; PEROXISOME BIOGENESIS DISORDER; REFSUM DISEASE; RHIZOMELIC CHONDRODYSPLASIA PUNCTATA TYPE 2; RHIZOMELIC CHONDRODYSPLASIA PUNCTATA TYPE 3; SINGLE PEROXISOMAL ENZYME DEFICIENCY; STEROL CARRIER PROTEIN X DEFICIENCY; ZELLWEGER SPECTRUM DISORDER; ZELLWEGER SYNDROME;

ANIMALS; BILE ACIDS AND SALTS; FATTY ACIDS; HUMANS; LIVER DISEASES; PEROXISOMAL DISORDERS; PEROXISOMES;

EID: 84870473233     PISSN: 13892002     EISSN: 18755453     Source Type: Journal    
DOI: 10.2174/138920012803762747     Document Type: Article

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