Plasma analysis of di- and trihydroxycholestanoic acid diastereoisomers in peroxisomal α-methylacyl-CoA racemase deficiency

Journal of Lipid Research

Volumn 42, Issue 1, 2001, Pages 137-141

  Ferdinandusse, Sacha ^a   Overmars, Henk ^a   Denis, Simone ^a   Waterham, Hans R ^a   Wanders, Ronald J A ^a   Vreken, Peter ^a  

^a UNIVERSITY OF AMSTERDAM   (Netherlands)

Author keywords

Bile acid intermediates; Peroxisomal oxidation; Stereochemistry

Indexed keywords

ACYL COENZYME A OXIDASE; BILE ACID; CHOLESTEROL;

ARTICLE; BILE ACID SYNTHESIS; CASE REPORT; CHOLESTASIS; DIASTEREOISOMER; HUMAN; LIQUID CHROMATOGRAPHY; LIVER DISEASE; LIVER METABOLISM; PEROXISOME; PRIORITY JOURNAL; STEREOCHEMISTRY; TANDEM MASS SPECTROMETRY; ZELLWEGER SYNDROME;

BILE ACIDS AND SALTS; CHILD, PRESCHOOL; CHOLESTANOLS; CHOLESTASIS, INTRAHEPATIC; DIAGNOSIS, DIFFERENTIAL; FEMALE; HUMANS; INFANT; MALE; OXIDATION-REDUCTION; PEROXISOMAL DISORDERS; PEROXISOMES; RACEMASES AND EPIMERASES; SPECTROMETRY, MASS, ELECTROSPRAY IONIZATION; STEREOISOMERISM; ZELLWEGER SYNDROME;

EID: 0035130658     PISSN: 00222275     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

References (28)

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