A mouse model for α-methylacyl-CoA racemase deficiency: Adjustment of bile acid synthesis and intolerance to dietary methyl-branched lipids

Human Molecular Genetics

Volumn 13, Issue 9, 2004, Pages 955-965

  Savolainen, Kalle ^a   Kotti, Tiina J ^a   Schmitz, Werner ^b   Savolainen, Teuvo I ^c   Sormunen, Raija T ^a   Ilves, Mika ^a   Vainio, Seppo J ^a   Conzelmann, Ernst ^b   Hiltunen, J Kalervo ^a  

^a UNIVERSITY OF OULU   (Finland)

^b UNIVERSITY OF WÜRZBURG   (Germany)

^c PÄIJÄT HÄME CENTRAL HOSPITAL   (Finland)

Author keywords

[No Author keywords available]

Indexed keywords

2 METHYLACYL COENZYME A RACEMASE; ACYL COENZYME A; BILE ACID; CELL ENZYME; CHOLESTEROL; CYTOCHROME; CYTOCHROME P450 3A1; CYTOCHROME P450 46A1; FATTY ACID; LIPID; MESSENGER RNA; METHYL GROUP; PEROXISOME MULTIFUNCTIONAL ENZYME 1; PHYTOL; RACEMASE; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BILE ACID BLOOD LEVEL; BILE ACID SYNTHESIS; BILE LEVEL; CONTROLLED STUDY; DETOXIFICATION; DIET SUPPLEMENTATION; DISEASE COURSE; ENZYME DEFICIENCY; ENZYME INDUCTION; FAT INTAKE; GENE INACTIVATION; LIPID DEGRADATION; LIVER DISEASE; LIVER LEVEL; MOUSE; NONHUMAN; NUCLEOTIDE SEQUENCE; NUTRITIONAL INTOLERANCE; PATHOPHYSIOLOGY; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; QUANTITATIVE ANALYSIS; SURVIVAL; SYMPTOMATOLOGY;

EID: 2442529920     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/ddh107     Document Type: Article

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