Phytanic acid and pristanic acid are oxidized by sequential peroxisomal and mitochondrial reactions in cultured fibroblasts

Journal of Lipid Research

Volumn 39, Issue 1, 1998, Pages 66-74

  Verhoeven, Nanda M ^a   Roe, Diane S ^b   Kok, Robert M ^a   Wanders, Ronald J A ^c   Jakobs, Cornelis ^a   Roe, Charles R ^b  

^a VU UNIVERSITY MEDICAL CENTER   (Netherlands)

^b BAYLOR UNIVERSITY MEDICAL CENTER   (United States)

^c UNIVERSITY OF AMSTERDAM   (Netherlands)

Author keywords

Carnitine palmitoyltransferase; Mitochondrion; Peroxisome; Tandem mass spectrometry

Indexed keywords

CARNITINE ACYLTRANSFERASE; CARNITINE PALMITOYLTRANSFERASE; PHYTANIC ACID;

ARTICLE; ENZYME DEFICIENCY; FATTY ACID OXIDATION; FIBROBLAST; HUMAN; HUMAN CELL; MITOCHONDRIAL RESPIRATION; PATHOPHYSIOLOGY; PEROXISOME; PRIORITY JOURNAL; TANDEM MASS SPECTROMETRY; ZELLWEGER SYNDROME;

EID: 0031908208     PISSN: 00222275     EISSN: None     Source Type: Journal    
DOI: 10.1016/s0022-2275(20)34204-8     Document Type: Article

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