Bile acid profiles in a peroxisomal D-3-Hydroxyacyl-CoA Dehydratase/D-3-Hydroxyacyl-CoA dehydrogenase bifunctional protein deficiency

Journal of Biochemistry

Volumn 122, Issue 3, 1997, Pages 655-658

  Une, Mizuho ^a   Konishi, Masaki ^a   Suzuki, Yasuyuki ^b   Akaboshi, Shinjiro ^c   Yoshii, Michiko ^a   Kuramoto, Taiju ^a   Fujimura, Kingo ^a  

^a HIROSHIMA UNIV SCHOOL OF MEDICINE   (Japan)

^b GIFU UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^c TOTTORI UNIVERSITY   (Japan)

Author keywords

Bile acid; Bile acid intermediates; D bifunctional protein; Peroxisomal disorder; oxidation

Indexed keywords

3 HYDROXYACYL COENZYME A DEHYDROGENASE; ACETYL COENZYME A ACETYLTRANSFERASE; ACYL COENZYME A OXIDASE; BILE ACID; ENOYL COENZYME A HYDRATASE;

ADRENOLEUKODYSTROPHY; ARTICLE; BILE; BILE ACID SYNTHESIS; CASE REPORT; ENZYME DEFICIENCY; FEMALE; GAS LIQUID CHROMATOGRAPHY; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HUMAN; INFANT; MASS SPECTROMETRY; PEROXISOME; REFSUM DISEASE; SERUM; URINE; ZELLWEGER SYNDROME;

EID: 0030860855     PISSN: 0021924X     EISSN: None     Source Type: Journal    
DOI: 10.1093/oxfordjournals.jbchem.a021803     Document Type: Article

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