Mouse models for peroxisome biogenesis defects and β-oxidation enzyme deficiencies

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1822, Issue 9, 2012, Pages 1489-1500

  Baes, Myriam ^a   Van Veldhoven, Paul P ^a  

^a UNIVERSITY OF LEUVEN   (Belgium)

Author keywords

Bile acids; Conditional knockout; Neurodegeneration; Peroxisome; PPARalpha; VLCFA

Indexed keywords

ACETYL COENZYME A ACETYLTRANSFERASE; ACYL COENZYME A OXIDASE; ACYL COENZYME A OXIDASE 1; ACYL COENZYME A OXIDASE 2; ACYL COENZYME A OXIDASE 3; BILE ACID; CHOLESTEROL; DICARBOXYLIC ACID; ENZYME; ESTRADIOL 17BETA DEHYDROGENASE; ESTRADIOL 17BETA DEHYDROGENASE TYPE IV; FATTY ACID; ICOSANOID; LIPID; MATRIX PROTEIN; MEMBRANE PROTEIN; NICOTINAMIDE ADENINE DINUCLEOTIDE; PERIPHERAL MYELIN PROTEIN 22; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR ALPHA; PEX PROTEIN; PHYTANIC ACID; PHYTOL; POLYUNSATURATED FATTY ACID; RACEMASE; STEROL CARRIER PROTEIN; STEROL CARRIER PROTEIN X; TRIACYLGLYCEROL; UNCLASSIFIED DRUG; UNINDEXED DRUG; VERY LONG CHAIN FATTY ACID; XENOBIOTIC AGENT;

ACCURACY; ADULTHOOD; BIOGENESIS; BLOOD CHEMISTRY; BRAIN CELL; CELL DAMAGE; CELL TYPE; DEREGULATION; DIET SUPPLEMENTATION; DRUG MEGADOSE; ENDOPLASMIC RETICULUM; ENZYME DEFICIENCY; ENZYME METABOLISM; FATTY ACID OXIDATION; GENE DELETION; GENE EXPRESSION; HISTOPATHOLOGY; HYPOLIPEMIA; LIPID ANALYSIS; LIVER; LIVER CELL; LOW DRUG DOSE; MOUSE; NONHUMAN; PEROXISOME; PRIORITY JOURNAL; PROTEIN FUNCTION; PROTEIN SYNTHESIS; RECEPTOR UPREGULATION; REVIEW; SERTOLI CELL; STEATORRHEA;

ACYL-COA OXIDASE; ACYLTRANSFERASES; ANIMALS; BRAIN; CARRIER PROTEINS; DISEASE MODELS, ANIMAL; ENOYL-COA HYDRATASE; HUMANS; LIPID METABOLISM; LIVER; MICE; OXIDATION-REDUCTION; PEROXISOMAL DISORDERS; PEROXISOMES; RACEMASES AND EPIMERASES;

MUS;

EID: 84864046565     PISSN: 09254439     EISSN: 1879260X     Source Type: Journal    
DOI: 10.1016/j.bbadis.2012.03.003     Document Type: Review

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