Targeted deletion of the PEX2 peroxisome assembly gene in mice provides a model for Zellweger syndrome, a human neuronal migration disorder

Journal of Cell Biology

Volumn 139, Issue 5, 1997, Pages 1293-1305

  Faust, Phyllis L ^a,b   Hatten, Mary E ^a  

^a ROCKEFELLER UNIVERSITY   (United States)

^b Och Spine at New York Presbyterian Hospitals   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

PLASMALOGEN; VERY LONG CHAIN FATTY ACID;

ADRENAL CORTEX; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL MIGRATION; CONTROLLED STUDY; EMBRYO; FEMALE; GENE DELETION; GENE DISRUPTION; GENE TARGETING; LAMELLAR BODY; LIPID STORAGE; MALE; MOUSE; NEUROLOGIC DISEASE; NEWBORN; NONHUMAN; PEROXISOME; PRIORITY JOURNAL; ZELLWEGER SYNDROME;

ADRENAL GLANDS; ANIMALS; BRAIN; CELL MOVEMENT; CEREBELLUM; CEREBRAL CORTEX; CLONING, MOLECULAR; DISEASE MODELS, ANIMAL; ERYTHROCYTES; FATTY ACIDS; LIVER; MEMBRANE PROTEINS; MICE; MICE, MUTANT STRAINS; MICROBODIES; MOLECULAR SEQUENCE DATA; MORPHOGENESIS; NEURONS; PLASMALOGENS; SKULL; ZELLWEGER SYNDROME;

ANIMALIA;

EID: 0030830906     PISSN: 00219525     EISSN: None     Source Type: Journal    
DOI: 10.1083/jcb.139.5.1293     Document Type: Article

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