Combined deficiency of peroxisomal β-oxidation and ether lipid synthesis in mice causes only minor cortical neuronal migration defects but severe hypotonia

Molecular Genetics and Metabolism

Volumn 100, Issue 1, 2010, Pages 71-76

  Krysko, Olga ^a   Bottelbergs, Astrid ^a   Veldhoven, Paul Van ^b   Baes, Myriam ^a  

^a UNIVERSITY OF LEUVEN   (Belgium)

^b Department of Molecular Cell Biology   (Belgium)

Author keywords

Hypotonia; Mouse model; Neuronal migration; Peroxisome biogenesis disorders; Plasmalogens; Very long chain fatty acids

Indexed keywords

ETHER LIPID;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; BIOGENESIS; BRAIN CELL; BRAIN DEVELOPMENT; CELL MIGRATION; CONTROLLED STUDY; DISEASE SEVERITY; FATTY ACID OXIDATION; FEMALE; KNOCKOUT MOUSE; LIPOGENESIS; MALE; MOUSE; MUSCLE HYPOTONIA; NERVE CELL DIFFERENTIATION; NONHUMAN; PEROXISOME; PRIORITY JOURNAL;

17-HYDROXYSTEROID DEHYDROGENASES; ACYLTRANSFERASES; ANIMALS; CELL MOVEMENT; CEREBELLUM; CEREBRAL CORTEX; ENOYL-COA HYDRATASE; MICE; MICE, KNOCKOUT; MULTIENZYME COMPLEXES; MUSCLE HYPOTONIA; PEROXISOMES;

MUS;

EID: 77950517530     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2010.02.003     Document Type: Article

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