Dysmyelination not demyelination causes neurological symptoms in preweaned mice in a murine model of Cockayne syndrome

Proceedings of the National Academy of Sciences of the United States of America

Volumn 109, Issue 12, 2012, Pages 4627-4632

  Revet, Ingrid ^a   Feeney, Luzviminda ^a   Tang, Amy A ^b   Huang, Eric J ^b   Cleaver, James E ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

H2Ax; Behavior; Rotenone; Transcription coupled repair

Indexed keywords

CSB PROTEIN; HYPOXIA INDUCIBLE FACTOR 1ALPHA; MYELIN; MYELIN BASIC PROTEIN; NUCLEAR PROTEIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ANTERIOR COMMISSURE; ARTICLE; ATAXIA; CELL PROLIFERATION; COCKAYNE SYNDROME; CORPUS CALLOSUM; DEMYELINATION; DNA DAMAGE; FAILURE TO THRIVE; MOUSE; MYELIN DEFICIENCY; MYELINATION; NERVE CELL DIFFERENTIATION; NERVE FIBER; NEUROLOGIC DISEASE; NONHUMAN; OLIGODENDROGLIA; PRIORITY JOURNAL; SENSORIMOTOR CORTEX; STRATUM RADIATUM; WASTING SYNDROME; WEANING;

ANIMALS; BEHAVIOR, ANIMAL; BODY WEIGHT; COCKAYNE SYNDROME; CROSSES, GENETIC; DISEASE MODELS, ANIMAL; HISTONE DEACETYLASES; HISTONES; MICE; MODELS, GENETIC; MUTATION; MYELIN SHEATH; OLIGODENDROGLIA; ORGAN SIZE; TRANSCRIPTION, GENETIC;

MURINAE; MUS;

EID: 84858649212     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.1202621109     Document Type: Article

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