Rett syndrome: From bed to bench

Pediatrics and Neonatology

Volumn 52, Issue 6, 2011, Pages 309-316

  Weng, Shih Ming ^a,b,c   Bailey, Mark E S ^b   Cobb, Stuart R ^a  

^a UNIVERSITY OF GLASGOW   (United Kingdom)

^b UNIVERSITY OF GLASGOW   (United Kingdom)

^c TAIPEI MEDICAL UNIVERSITY   (Taiwan)

Author keywords

animal model; MECP2; Rett Syndrome

Indexed keywords

1,4 BENZODIOXAN 6 CARBOXYLIC ACID PIPERIDIDE; ACETYLCHOLINE; BRAIN DERIVED NEUROTROPHIC FACTOR; DESIPRAMINE; DOPAMINE; GENTAMICIN; GLUTAMIC ACID; LENTIVIRUS VECTOR; MEMANTINE; METHYL CPG BINDING PROTEIN 2; NERVE GROWTH FACTOR; RECOMBINANT SOMATOMEDIN C; SEROTONIN; SOMATOMEDIN BINDING PROTEIN 3; SOMATOMEDIN C; SUBSTANCE P;

ALLELE; APRAXIA; ATAXIA; BALANCE DISORDER; BRAIN CORTEX; BRAIN WEIGHT; CEREBELLUM; CHROMOSOME XQ; CONSTIPATION; DENTATE GYRUS; DISEASE COURSE; DISEASE SEVERITY; ELECTROENCEPHALOGRAM; GENE CASSETTE; GENE INSERTION; GENE LOCUS; GENE MUTATION; GENE THERAPY; GENETIC MODEL; GRANULE CELL; GROWTH DISORDER; HIPPOCAMPAL CA3 REGION; HUMAN; INCIDENCE; INTRACTABLE EPILEPSY; MEMORY DISORDER; MENTAL DETERIORATION; MICROCEPHALY; MOTOR COORDINATION; MUSCLE HYPOTONIA; NERVE CELL PLASTICITY; NONHUMAN; PATHOGENESIS; PYRAMIDAL NERVE CELL; QT INTERVAL; RETT SYNDROME; REVIEW; SCOLIOSIS; SEIZURE; SIGNAL TRANSDUCTION; SPATIAL MEMORY; STEREOTYPY; STOP CODON; SUDDEN DEATH; VIRAL GENE DELIVERY SYSTEM;

ANIMALS; BRAIN; DISEASE MODELS, ANIMAL; ELECTROENCEPHALOGRAPHY; GENETIC LINKAGE; GENETIC THERAPY; HUMANS; MALE; METHYL-CPG-BINDING PROTEIN 2; MICE; MICE, KNOCKOUT; NEURONAL PLASTICITY; ORGAN SIZE; RETT SYNDROME;

EID: 84355162888     PISSN: 18759572     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.pedneo.2011.08.002     Document Type: Review

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