Aceruloplasminemia: Retinal histopathologic manifestations and iron-mediated melanosome degradation

Archives of Ophthalmology

Volumn 129, Issue 11, 2011, Pages 1466-1474

  Wolkow, Natalie ^a   Song, Ying ^a   Wu, Ting Di ^b,c   Qian, Jiang ^d   Guerquin Kern, Jean Luc ^b,c   Dunaief, Joshua L ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b INSTITUT CURIE   (France)

^c INSERM   (France)

^d ALBANY MEDICAL COLLEGE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CERULOPLASMIN; IRON; LIPOFUSCIN;

ACERULOPLASMINEMIA; ADULT; ARTICLE; ATROPHY; AUTOSOMAL RECESSIVE DISORDER; CLINICAL FEATURE; COMPLEMENT DEPOSITION; DEGRADATION; ELECTRON MICROSCOPY; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; HYPERTROPHY; IMMUNOHISTOCHEMISTRY; MALE; MELANOSOME; MICROSCOPY; MUTATION; PIGMENT EPITHELIUM; PRIORITY JOURNAL; RETINA; RETINA MACULA AGE RELATED DEGENERATION; RETINA NEUROEPITHELIAL LAYER; STAINING;

AGED, 80 AND OVER; CERULOPLASMIN; COMPLEMENT MEMBRANE ATTACK COMPLEX; FEMALE; FERRITINS; HUMANS; IMMUNOENZYME TECHNIQUES; IRON METABOLISM DISORDERS; LIPOFUSCIN; MACULAR DEGENERATION; MALE; MELANOSOMES; MICROSCOPY, ELECTRON; MIDDLE AGED; NEURODEGENERATIVE DISEASES; RETINAL DISEASES; RETINAL PIGMENT EPITHELIUM; SPECTROMETRY, MASS, SECONDARY ION; STAINING AND LABELING; TRANSFERRIN; VITRONECTIN;

EID: 81355154095     PISSN: 00039950     EISSN: 15383601     Source Type: Journal    
DOI: 10.1001/archophthalmol.2011.309     Document Type: Article

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