Defective electron transfer in complexes I and IV in patients with aceruloplasminemia

Journal of the Neurological Sciences

Volumn 182, Issue 1, 2000, Pages 57-60

  Kohno, Satoshi ^a   Miyajima, Hiroaki ^a   Takahashi, Yoshitomo ^a   Suzuki, Hitoshi ^a   Hishida, Akira ^a  

^a HAMAMATSU UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

Aceruloplasminemia; Ceruloplasmin; Complex I and IV; Iron metabolism; Lipid peroxidation; Mitochondria; Mn SOD

Indexed keywords

CERULOPLASMIN; CYTOCHROME C OXIDASE; MALONALDEHYDE; MANGANESE SUPEROXIDE DISMUTASE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE);

ADULT; AGED; ARTICLE; BRAIN CORTEX; CASE REPORT; ELECTRON TRANSPORT; ENERGY METABOLISM; FEMALE; GENE MUTATION; HUMAN; HUMAN CELL; IRON METABOLISM; LIPID PEROXIDATION; MALE; MITOCHONDRIAL RESPIRATION; PRIORITY JOURNAL; RESPIRATORY CHAIN; WESTERN BLOTTING;

AGED; CEREBRAL CORTEX; CERULOPLASMIN; ELECTRON TRANSPORT; ELECTRON TRANSPORT COMPLEX I; ELECTRON TRANSPORT COMPLEX IV; FATAL OUTCOME; FEMALE; HUMANS; IRON METABOLISM DISORDERS; LIPID PEROXIDATION; MALE; MIDDLE AGED; MITOCHONDRIA; NADH, NADPH OXIDOREDUCTASES; SUPEROXIDE DISMUTASE;

EID: 0034672736     PISSN: 0022510X     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0022-510X(00)00452-4     Document Type: Article

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