Lamins, laminopathies and disease mechanisms: Possible role for proteasomal degradation of key regulatory proteins

Journal of Biosciences

Volumn 36, Issue 3, 2011, Pages 471-479

  Parnaik, Veena K ^a   Chaturvedi, Pankaj ^a   Muralikrishna, Bh ^a  

^a CENTRE FOR CELLULAR AND MOLECULAR BIOLOGY   (India)

Author keywords

DNA repair; heterochromatin; lamin; nuclear envelope; proteasome; ubiquitin ligases

Indexed keywords

LAMIN; LAMIN A; LAMIN B1; LAMIN B2; LAMIN B3; LAMIN C; LAMIN C2; REGULATOR PROTEIN; UBIQUITIN; UNCLASSIFIED DRUG;

DISEASE INCIDENCE; DNA; GENETIC ANALYSIS; MUTATION; PATHOGENICITY; PROTEIN;

ADIPOSE TISSUE; ARTICLE; DEGENERATIVE DISEASE; FAMILIAL PARTIAL LIPODYSTROPHY; GENE; GENE MUTATION; GENETIC DISORDER; HEREDITARY MOTOR SENSORY NEUROPATHY; HUMAN; LAMINOPATHY; LMNA GENE; LMNB1 GENE; LMNB2 GENE; MUSCLE; NONHUMAN; PATHOGENESIS; PROGERIA; PROTEIN BINDING; PROTEIN DEGRADATION; PROTEIN FUNCTION; SIGNAL TRANSDUCTION;

GENETIC DISEASES, INBORN; HUMANS; LAMINS; MUTATION, MISSENSE; NUCLEAR LAMINA; PROTEASOME ENDOPEPTIDASE COMPLEX; SIGNAL TRANSDUCTION;

EID: 80054817543     PISSN: 02505991     EISSN: 09737138     Source Type: Journal    
DOI: 10.1007/s12038-011-9085-2     Document Type: Article

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