Proteasome-mediated degradation of integral inner nuclear membrane protein emerin in fibroblasts lacking A-type lamins

Biochemical and Biophysical Research Communications

Volumn 351, Issue 4, 2006, Pages 1011-1017

  Muchir, Antoine ^a   Massart, Catherine ^b,c   van Engelen, Baziel G ^d   Lammens, Martin ^d   Bonne, Gisèle ^b,c,e   Worman, Howard J ^a  

^a Columbia University ^*  (United States)

^b INSERM   (France)

^c SORBONNE UNIVERSITÉ   (France)

^d RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^e PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

Author keywords

Emerin; Lamin; Muscular dystrophy; Nesprin; Nuclear envelope; Proteasome

Indexed keywords

CELL MEMBRANE PROTEIN; EMERIN; LAMIN A; NESPRIN 1ALPHA; PROTEASOME; UNCLASSIFIED DRUG;

ARTICLE; CELL NUCLEUS MEMBRANE; CELLULAR DISTRIBUTION; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; FETUS; HOMOZYGOSITY; HUMAN; HUMAN CELL; MALE; NONSENSE MUTATION; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; PROTEIN PHOSPHORYLATION; RNA TRANSLATION; SKIN FIBROBLAST; STEADY STATE;

CELLS, CULTURED; CHILD; ENDOPLASMIC RETICULUM; FIBROBLASTS; HOMOZYGOTE; HUMANS; LAMIN TYPE A; MALE; MEMBRANE PROTEINS; MUTATION; NUCLEAR ENVELOPE; NUCLEAR PROTEINS; PROTEASOME ENDOPEPTIDASE COMPLEX; RNA, MESSENGER; SKIN;

EID: 33751255699     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2006.10.147     Document Type: Article

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