Amyotrophic lateral sclerosis mutant vesicle-associated membrane protein-associated protein-B transgenic mice develop TAR-DNA-binding protein-43 pathology

Neuroscience

Volumn 167, Issue 3, 2010, Pages 774-785

  Tudor, E L ^a   Galtrey, C M ^a   Perkinton, M S ^a   Lau, K F ^a,b   De Vos, K J ^a   Mitchell, J C ^a   Ackerley, S ^a   Hortobagyi T ^a   Vamos E ^a   Leigh, P N ^a   Klasen, C ^c   McLoughlin, D M ^a,d   Shaw, C E ^a   Miller, C C J ^a  

^a KING'S COLLEGE LONDON   (United Kingdom)

^b CHINESE UNIVERSITY OF HONG KONG   (Hong Kong)

^c EUROPEAN MOLECULAR BIOLOGY LABORATORY   (Germany)

^d ST PATRICK S HOSPITAL   (Ireland)

Author keywords

Motor neuron disease; TAR DNA binding protein 43; Ubiquitin; Vesicle associated membrane protein associated protein B

Indexed keywords

SYNAPTOBREVIN; TAR DNA BINDING PROTEIN; UNCLASSIFIED DRUG; VESICLE ASSOCIATED MEMBRANE PROTEIN ASSOCIATED PROTEIN B;

AGE DISTRIBUTION; AMINO ACID SUBSTITUTION; AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; CYTOPLASM; HUMAN; HUMAN TISSUE; MOUSE; NERVOUS SYSTEM; NEUROPATHOLOGY; NONHUMAN; PRIORITY JOURNAL; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN METABOLISM; SPINAL CORD MOTONEURON; SURVIVAL; TRANSGENIC MOUSE; WILD TYPE;

AMINO ACID SUBSTITUTION; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; DISEASE MODELS, ANIMAL; DNA-BINDING PROTEINS; GENETIC PREDISPOSITION TO DISEASE; INCLUSION BODIES; MEMBRANE PROTEINS; MICE; MICE, TRANSGENIC; MOTOR NEURONS; POINT MUTATION; PROTEIN TRANSPORT; SPINAL CORD;

EID: 77951298381     PISSN: 03064522     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.neuroscience.2010.02.035     Document Type: Article

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