-
1
-
-
56349088740
-
Mutant SOD1 from spinal cord of G93A rats is destabilized and binds to inner mitochondrial membrane
-
Ahtoniemi T., Jaronen M., Keksa-Goldsteine V., Goldsteins G., Koistinaho J. Mutant SOD1 from spinal cord of G93A rats is destabilized and binds to inner mitochondrial membrane. Neurobiol. Dis. 2008, 32(3):479-485.
-
(2008)
Neurobiol. Dis.
, vol.32
, Issue.3
, pp. 479-485
-
-
Ahtoniemi, T.1
Jaronen, M.2
Keksa-Goldsteine, V.3
Goldsteins, G.4
Koistinaho, J.5
-
2
-
-
0002984853
-
Control of glutamate metabolism. The effect of pyruvate
-
Balazs R. Control of glutamate metabolism. The effect of pyruvate. J. Neurochem. 1965, 12:63-76.
-
(1965)
J. Neurochem.
, vol.12
, pp. 63-76
-
-
Balazs, R.1
-
3
-
-
75149155060
-
Oxidative stress in ALS: key role in motor neuron injury and therapeutic target
-
Barber S.C., Shaw P.J. Oxidative stress in ALS: key role in motor neuron injury and therapeutic target. Free Radic. Biol. Med. 2010, 48(5):629-641.
-
(2010)
Free Radic. Biol. Med.
, vol.48
, Issue.5
, pp. 629-641
-
-
Barber, S.C.1
Shaw, P.J.2
-
4
-
-
4043075622
-
Lessons from models of SOD1-linked familial ALS
-
Bendotti C., Carri M.T. Lessons from models of SOD1-linked familial ALS. Trends Mol. Med. 2004, 10(8):393-400.
-
(2004)
Trends Mol. Med.
, vol.10
, Issue.8
, pp. 393-400
-
-
Bendotti, C.1
Carri, M.T.2
-
5
-
-
0036929577
-
Mitochondrial oxidative metabolism in motor neuron degeneration (mnd) mouse central nervous system
-
Bertamini M., Marzani B., Guarneri R., Guarneri P., Bigini P., Mennini T., Curti D. Mitochondrial oxidative metabolism in motor neuron degeneration (mnd) mouse central nervous system. Eur. J. Neurosci. 2002, 16(12):2291-2296.
-
(2002)
Eur. J. Neurosci.
, vol.16
, Issue.12
, pp. 2291-2296
-
-
Bertamini, M.1
Marzani, B.2
Guarneri, R.3
Guarneri, P.4
Bigini, P.5
Mennini, T.6
Curti, D.7
-
6
-
-
68349157123
-
Hypermetabolism in ALS patients: an early and persistent phenomenon
-
Bouteloup C., Desport J.C., Clavelou P., Guy N., Derumeaux-Burel H., Ferrier A., Couratier P. Hypermetabolism in ALS patients: an early and persistent phenomenon. J. Neurol. 2009, 256(8):1236-1242.
-
(2009)
J. Neurol.
, vol.256
, Issue.8
, pp. 1236-1242
-
-
Bouteloup, C.1
Desport, J.C.2
Clavelou, P.3
Guy, N.4
Derumeaux-Burel, H.5
Ferrier, A.6
Couratier, P.7
-
7
-
-
0027359334
-
Superoxide dismutase activity, oxidative damage, and mitochondrial energy metabolism in familial and sporadic amyotrophic lateral sclerosis
-
Bowling A.C., Schulz J.B., Brown R.H., Beal M.F. Superoxide dismutase activity, oxidative damage, and mitochondrial energy metabolism in familial and sporadic amyotrophic lateral sclerosis. J. Neurochem. 1993, 61:2322-2325.
-
(1993)
J. Neurochem.
, vol.61
, pp. 2322-2325
-
-
Bowling, A.C.1
Schulz, J.B.2
Brown, R.H.3
Beal, M.F.4
-
8
-
-
0031865772
-
Metabolic dysfunction in familial, but not sporadic, amyotrophic lateral sclerosis
-
Browne S.E., Bowling A.C., Baik M.J., Gurney M., Brown R.H., Beal M.F. Metabolic dysfunction in familial, but not sporadic, amyotrophic lateral sclerosis. J. Neurochem. 1998, 71:281-287.
-
(1998)
J. Neurochem.
, vol.71
, pp. 281-287
-
-
Browne, S.E.1
Bowling, A.C.2
Baik, M.J.3
Gurney, M.4
Brown, R.H.5
Beal, M.F.6
-
9
-
-
3943102116
-
Unraveling the mechanisms involved in motor neuron degeneration in ALS
-
Bruijn L.I., Miller T.M., Cleveland D.W. Unraveling the mechanisms involved in motor neuron degeneration in ALS. Annu. Rev. Neurosci. 2004, 27:723-749.
-
(2004)
Annu. Rev. Neurosci.
, vol.27
, pp. 723-749
-
-
Bruijn, L.I.1
Miller, T.M.2
Cleveland, D.W.3
-
10
-
-
33645102302
-
Neural mitochondrial Ca capacity impairment precedes the onset of motor symptoms in G93A Cu/Zn-superoxide dismutase mutant mice
-
Damiano M., Starkov A.A., Petri S., Kipiani K., Kiaei M., Mattiazzi M., Beal F.M., Manfredi G. Neural mitochondrial Ca capacity impairment precedes the onset of motor symptoms in G93A Cu/Zn-superoxide dismutase mutant mice. J. Neurochem. 2006, 96:1349-1361.
-
(2006)
J. Neurochem.
, vol.96
, pp. 1349-1361
-
-
Damiano, M.1
Starkov, A.A.2
Petri, S.3
Kipiani, K.4
Kiaei, M.5
Mattiazzi, M.6
Beal, F.M.7
Manfredi, G.8
-
11
-
-
0043166646
-
Early mitochondrial dysfunction occurs in motor cortex and spinal cord at the onset of disease in the Wobbler mouse
-
Dave K.R., Bradley W.G., Perez-Pinzon M.A. Early mitochondrial dysfunction occurs in motor cortex and spinal cord at the onset of disease in the Wobbler mouse. Exp. Neurol. 2003, 182:412-420.
-
(2003)
Exp. Neurol.
, vol.182
, pp. 412-420
-
-
Dave, K.R.1
Bradley, W.G.2
Perez-Pinzon, M.A.3
-
12
-
-
0024590153
-
Evoked effects of cholesterol binding on integral proteins and lipid fluidity of dog brain synaptosomal plasma membranes
-
Deliconstantinos G., Kopeikina L., Villiotou V. Evoked effects of cholesterol binding on integral proteins and lipid fluidity of dog brain synaptosomal plasma membranes. Biochem. Cell. Biol. 1989, 67(1):16-24.
-
(1989)
Biochem. Cell. Biol.
, vol.67
, Issue.1
, pp. 16-24
-
-
Deliconstantinos, G.1
Kopeikina, L.2
Villiotou, V.3
-
13
-
-
33744816556
-
Hypermetabolism in ALS: correlations with clinical and paraclinical parameters
-
Desport J.C., Torny F., Lacoste M., Preux P.M., Couratier P. Hypermetabolism in ALS: correlations with clinical and paraclinical parameters. Neurodegener. Dis. 2005, 2(3-4):202-207.
-
(2005)
Neurodegener. Dis.
, vol.2
, Issue.3-4
, pp. 202-207
-
-
Desport, J.C.1
Torny, F.2
Lacoste, M.3
Preux, P.M.4
Couratier, P.5
-
14
-
-
1642440240
-
Cupric-amyloid beta peptide complex stimulates oxidation of ascorbate and generation of hydroxyl radical
-
Dikalov S.I., Vitek M.P., Mason R.P. Cupric-amyloid beta peptide complex stimulates oxidation of ascorbate and generation of hydroxyl radical. Free Radic. Biol. Med. 2004, 36(3):340-347.
-
(2004)
Free Radic. Biol. Med.
, vol.36
, Issue.3
, pp. 340-347
-
-
Dikalov, S.I.1
Vitek, M.P.2
Mason, R.P.3
-
15
-
-
21844454460
-
Mitochondria in amyotrophic lateral sclerosis: a trigger and a target
-
Dupuis L., Gonzalez de Aguilar J.L., Oudart H., de Tapia M., Barbeito L., Loeffler J.P. Mitochondria in amyotrophic lateral sclerosis: a trigger and a target. Neurodegener. Dis. 2004, 1(6):245-254.
-
(2004)
Neurodegener. Dis.
, vol.1
, Issue.6
, pp. 245-254
-
-
Dupuis, L.1
Gonzalez de Aguilar, J.L.2
Oudart, H.3
de Tapia, M.4
Barbeito, L.5
Loeffler, J.P.6
-
16
-
-
65549128133
-
Muscle mitochondrial uncoupling dismantles neuromuscular junction and triggers distal degeneration of motor neurons
-
Dupuis L., Gonzalez de Aguilar J.L., Echaniz-Laguna A., Eschbach J., Rene F., Oudart H., Halter B., Huze C., Schaeffer L., Bouillaud F., Loeffler J.P. Muscle mitochondrial uncoupling dismantles neuromuscular junction and triggers distal degeneration of motor neurons. PLoS One. 2009, 4(4):e5390.
-
(2009)
PLoS One.
, vol.4
, Issue.4
-
-
Dupuis, L.1
Gonzalez de Aguilar, J.L.2
Echaniz-Laguna, A.3
Eschbach, J.4
Rene, F.5
Oudart, H.6
Halter, B.7
Huze, C.8
Schaeffer, L.9
Bouillaud, F.10
Loeffler, J.P.11
-
17
-
-
63449092530
-
Loss of metal ions, disulfide reduction and mutations related to familial ALS promote formation of amyloid-like aggregates from superoxide dismutase
-
Durer Z.A.O., Cohlberg J.A., Dinh P., Padua S., Ehrenclou K., Downes S., Tan J.K., Nakano Y., Bowman C.J., Hoskins J.L., Kwon C., Mason A.Z., Rodriguez J.A., Doucette P.A., Shaw B.F., Valentine J.S. Loss of metal ions, disulfide reduction and mutations related to familial ALS promote formation of amyloid-like aggregates from superoxide dismutase. PLoS One. 2009, 4(3):e5004.
-
(2009)
PLoS One.
, vol.4
, Issue.3
-
-
Durer, Z.A.O.1
Cohlberg, J.A.2
Dinh, P.3
Padua, S.4
Ehrenclou, K.5
Downes, S.6
Tan, J.K.7
Nakano, Y.8
Bowman, C.J.9
Hoskins, J.L.10
Kwon, C.11
Mason, A.Z.12
Rodriguez, J.A.13
Doucette, P.A.14
Shaw, B.F.15
Valentine, J.S.16
-
18
-
-
32644434546
-
Muscular mitochondrial function in amyotrophic lateral sclerosis is progressively altered as the disease develops: a temporal study in man
-
Echaniz-Laguna A., Zoll E., Ponsot J., N'Guessan B., Tranchant C., Loeffler J.P., Lampert E. Muscular mitochondrial function in amyotrophic lateral sclerosis is progressively altered as the disease develops: a temporal study in man. Exp. Neurol. 2006, 198(1):25-30.
-
(2006)
Exp. Neurol.
, vol.198
, Issue.1
, pp. 25-30
-
-
Echaniz-Laguna, A.1
Zoll, E.2
Ponsot, J.3
N'Guessan, B.4
Tranchant, C.5
Loeffler, J.P.6
Lampert, E.7
-
19
-
-
33748795566
-
Familial ALS-superoxide dismutases associate with mitochondria and shift their redox potentials
-
Ferri A., Cozzolino M., Crosio C., Nencini M., Casciati A., Gralla E.B., Rotilio G., Valentine J.C., Carri M.T. Familial ALS-superoxide dismutases associate with mitochondria and shift their redox potentials. Proc. Natl. Acad. Sci. U. S. A. 2006, 103(37):13860-13865.
-
(2006)
Proc. Natl. Acad. Sci. U. S. A.
, vol.103
, Issue.37
, pp. 13860-13865
-
-
Ferri, A.1
Cozzolino, M.2
Crosio, C.3
Nencini, M.4
Casciati, A.5
Gralla, E.B.6
Rotilio, G.7
Valentine, J.C.8
Carri, M.T.9
-
20
-
-
0041344579
-
Factors controlling the uptake of yeast copper/zinc superoxide dismutase into mitochondria
-
Field L.S., Furukawa Y., O'Halloran T.V., Culotta V.C. Factors controlling the uptake of yeast copper/zinc superoxide dismutase into mitochondria. J. Biol. Chem. 2003, 278(30):28052-28059.
-
(2003)
J. Biol. Chem.
, vol.278
, Issue.30
, pp. 28052-28059
-
-
Field, L.S.1
Furukawa, Y.2
O'Halloran, T.V.3
Culotta, V.C.4
-
21
-
-
78650681173
-
SOD1 targeted to the mitochondrial intermembrane space prevents motor neuropathy in the Sod1 knockout mouse
-
Fischer L.R., Igoudjil A., Magrané J., Li Y., Hansen J.M., Manfredi G., Glass J.D. SOD1 targeted to the mitochondrial intermembrane space prevents motor neuropathy in the Sod1 knockout mouse. Brain 2011, 134(1):196-209.
-
(2011)
Brain
, vol.134
, Issue.1
, pp. 196-209
-
-
Fischer, L.R.1
Igoudjil, A.2
Magrané, J.3
Li, Y.4
Hansen, J.M.5
Manfredi, G.6
Glass, J.D.7
-
22
-
-
33745821631
-
Posttranslational modifications in Cu, Zn-superoxide dismutase and mutations associated with amyotrophic lateral sclerosis
-
Furukawa Y., O'Halloran T.V. Posttranslational modifications in Cu, Zn-superoxide dismutase and mutations associated with amyotrophic lateral sclerosis. Antioxid. Redox. Signal. 2006, 8(5-6):847-867.
-
(2006)
Antioxid. Redox. Signal.
, vol.8
, Issue.5-6
, pp. 847-867
-
-
Furukawa, Y.1
O'Halloran, T.V.2
-
23
-
-
67650103911
-
Mitochondrial bioenergetics as a major motive force of speciation
-
Gershoni M., Templeton A.R., Mishmar D. Mitochondrial bioenergetics as a major motive force of speciation. Bioessays 2009, 31(6):642-650.
-
(2009)
Bioessays
, vol.31
, Issue.6
, pp. 642-650
-
-
Gershoni, M.1
Templeton, A.R.2
Mishmar, D.3
-
24
-
-
33751250197
-
Genetics of familial and sporadic amyotrophic lateral sclerosis
-
Gros-Louis F., Gaspar C., Rouleau G.A. Genetics of familial and sporadic amyotrophic lateral sclerosis. Biochim. Biophys. Acta. 2006, 1762(11-12):956-972.
-
(2006)
Biochim. Biophys. Acta.
, vol.1762
, Issue.11-12
, pp. 956-972
-
-
Gros-Louis, F.1
Gaspar, C.2
Rouleau, G.A.3
-
25
-
-
15844404722
-
A pore way to die
-
Halestrap A. A pore way to die. Nature 2005, 434:578-579.
-
(2005)
Nature
, vol.434
, pp. 578-579
-
-
Halestrap, A.1
-
26
-
-
0033956949
-
Mitochondria and cell death
-
Halestrap A.P., Doran E., Gillespie J.P., O'Toole A. Mitochondria and cell death. Biochem. Soc. Trans. 2000, 28(2):170-177.
-
(2000)
Biochem. Soc. Trans.
, vol.28
, Issue.2
, pp. 170-177
-
-
Halestrap, A.P.1
Doran, E.2
Gillespie, J.P.3
O'Toole, A.4
-
27
-
-
0036787803
-
Update on the glutamatergic neurotransmitter system and the role of excitotoxicity in amyotrophic lateral sclerosis
-
Heath P.R., Shaw P.J. Update on the glutamatergic neurotransmitter system and the role of excitotoxicity in amyotrophic lateral sclerosis. Muscle Nerve. 2002, 26:438-458.
-
(2002)
Muscle Nerve.
, vol.26
, pp. 438-458
-
-
Heath, P.R.1
Shaw, P.J.2
-
28
-
-
0037088793
-
Mutant Cu, Zn superoxide dismutase that causes motoneuron degeneration is present in mitochondria in the CNS
-
Higgins C.M., Jung C., Ding H., Xu Z. Mutant Cu, Zn superoxide dismutase that causes motoneuron degeneration is present in mitochondria in the CNS. J. Neurosci. 2002, 22:RC215.
-
(2002)
J. Neurosci.
, vol.22
-
-
Higgins, C.M.1
Jung, C.2
Ding, H.3
Xu, Z.4
-
29
-
-
0037022339
-
Focal loss of the glutamate transporter EAAT2 in a transgenic rat model of SOD1 mutant-mediated amyotrophic lateral sclerosis (ALS)
-
Howland D.S., Liu J., She Y., Goad B., Maragakis N.J., Kim B., Erickson J., Kulik J., DeVito L., Psaltis G., DeGennaro L.J., Cleveland D.W., Rothstein J.D. Focal loss of the glutamate transporter EAAT2 in a transgenic rat model of SOD1 mutant-mediated amyotrophic lateral sclerosis (ALS). Proc. Natl. Acad. Sci. U. S. A. 2002, 99:1604-1609.
-
(2002)
Proc. Natl. Acad. Sci. U. S. A.
, vol.99
, pp. 1604-1609
-
-
Howland, D.S.1
Liu, J.2
She, Y.3
Goad, B.4
Maragakis, N.J.5
Kim, B.6
Erickson, J.7
Kulik, J.8
DeVito, L.9
Psaltis, G.10
DeGennaro, L.J.11
Cleveland, D.W.12
Rothstein, J.D.13
-
30
-
-
77955961922
-
Misfolded mutant SOD1 directly inhibits VDAC1 conductance in a mouse model inherited ALS
-
Israelson A., Arbel N., Da Cruz S., Illeva H., Yamanaka K., Shoshan-Barmatz V., Cleveland D.W. Misfolded mutant SOD1 directly inhibits VDAC1 conductance in a mouse model inherited ALS. Neuron 2010, 67:575-587.
-
(2010)
Neuron
, vol.67
, pp. 575-587
-
-
Israelson, A.1
Arbel, N.2
Da Cruz, S.3
Illeva, H.4
Yamanaka, K.5
Shoshan-Barmatz, V.6
Cleveland, D.W.7
-
31
-
-
33646683358
-
Swelling and vacuolisation of mitochondria in transgenic SOD1-ALS mice: a consequence of supranormal SOD1 expression?
-
Jaarsma D. Swelling and vacuolisation of mitochondria in transgenic SOD1-ALS mice: a consequence of supranormal SOD1 expression?. Mitochondrion 2006, 6(1):48-49.
-
(2006)
Mitochondrion
, vol.6
, Issue.1
, pp. 48-49
-
-
Jaarsma, D.1
-
32
-
-
0034520591
-
Human Cu/Zn superoxide dismutase (SOD1) overexpression in mice causes mitochondrial vacuolization, axonal degeneration, and premature motoneuron death and accelerates motoneuron disease in mice expressing a familial amyotrophic lateral sclerosis mutant SOD1
-
Jaarsma D., Haasdijk E.D., Grashorn J.A., Hawkins R., van Duijn W., Verspaget H.W., London J., Holstege J.C. Human Cu/Zn superoxide dismutase (SOD1) overexpression in mice causes mitochondrial vacuolization, axonal degeneration, and premature motoneuron death and accelerates motoneuron disease in mice expressing a familial amyotrophic lateral sclerosis mutant SOD1. Neurobiol. Dis. 2000, 7(6 Pt B):623-643.
-
(2000)
Neurobiol. Dis.
, vol.7
, Issue.6 PART B
, pp. 623-643
-
-
Jaarsma, D.1
Haasdijk, E.D.2
Grashorn, J.A.3
Hawkins, R.4
van Duijn, W.5
Verspaget, H.W.6
London, J.7
Holstege, J.C.8
-
33
-
-
0037086851
-
A quantitative histochemical assay for activities of mitochondrial electron transport chain complexes in mouse spinal cord sections
-
Jung C., Higgins C.M.J., Xu Z. A quantitative histochemical assay for activities of mitochondrial electron transport chain complexes in mouse spinal cord sections. J. Neurosci. Methods. 2002, 114(2):165-172.
-
(2002)
J. Neurosci. Methods.
, vol.114
, Issue.2
, pp. 165-172
-
-
Jung, C.1
Higgins, C.M.J.2
Xu, Z.3
-
34
-
-
12144257165
-
Cytochrome c association with the inner mitochondrial membrane is impaired in the CNS of G93A-SOD1 mice
-
Kirkinezos I.G., Bacman S.R., Hernandez D., Oca-Cossio J., Arias L.J., Perez-Pinzon M.J., Bradley W.G., Moraes C.T. Cytochrome c association with the inner mitochondrial membrane is impaired in the CNS of G93A-SOD1 mice. J. Neurosci. 2005, 25:164-172.
-
(2005)
J. Neurosci.
, vol.25
, pp. 164-172
-
-
Kirkinezos, I.G.1
Bacman, S.R.2
Hernandez, D.3
Oca-Cossio, J.4
Arias, L.J.5
Perez-Pinzon, M.J.6
Bradley, W.G.7
Moraes, C.T.8
-
35
-
-
79955798781
-
Effect of malate on development of rotenone-induced brain changes in Wistar and OXYS rats: an MRI study
-
Kolosova N.G., Akulov A.E., Stefanova N.A., Moshkin M.P., Savelov A.A., Koptyug I.V., Panov A.V., Vavilin V.A. Effect of malate on development of rotenone-induced brain changes in Wistar and OXYS rats: an MRI study. Doklady Biol. Sci. 2011, 437:1-4.
-
(2011)
Doklady Biol. Sci.
, vol.437
, pp. 1-4
-
-
Kolosova, N.G.1
Akulov, A.E.2
Stefanova, N.A.3
Moshkin, M.P.4
Savelov, A.A.5
Koptyug, I.V.6
Panov, A.V.7
Vavilin, V.A.8
-
36
-
-
23444445882
-
Mitochondrial changes in skeletal muscle in amyotrophic lateral sclerosis and other neurogenic atrophies
-
Krasnianski A., Deschauer M., Neudecker S., Gellerich F.N., Muller T., Schoser B.G., Krasnianski M., Zierz S. Mitochondrial changes in skeletal muscle in amyotrophic lateral sclerosis and other neurogenic atrophies. Brain 2005, 128(8):1870-1876.
-
(2005)
Brain
, vol.128
, Issue.8
, pp. 1870-1876
-
-
Krasnianski, A.1
Deschauer, M.2
Neudecker, S.3
Gellerich, F.N.4
Muller, T.5
Schoser, B.G.6
Krasnianski, M.7
Zierz, S.8
-
37
-
-
2342650119
-
CO2 enhanced peroxidase activity of SOD1: the effects of pH
-
Liochev S.I., Fridovich I. CO2 enhanced peroxidase activity of SOD1: the effects of pH. Free Radic. Biol. Med. 2004, 36(11):1444-1447.
-
(2004)
Free Radic. Biol. Med.
, vol.36
, Issue.11
, pp. 1444-1447
-
-
Liochev, S.I.1
Fridovich, I.2
-
38
-
-
3242701496
-
Toxicity of familial ALS-linked SOD1 mutants from selective recruitment to spinal mitochondria
-
Liu J., Lillo C., Jonsson P.A., Vande Velde C., Ward C.M., Miller T.M., Subramaniam J.R., Rothstein J.D., Marklund S., Andersen P.M., Brannstrom T., Gredal O., Wong P.C., Williams D.S., Cleveland D.W. Toxicity of familial ALS-linked SOD1 mutants from selective recruitment to spinal mitochondria. Neuron 2004, 43:5-17.
-
(2004)
Neuron
, vol.43
, pp. 5-17
-
-
Liu, J.1
Lillo, C.2
Jonsson, P.A.3
Vande Velde, C.4
Ward, C.M.5
Miller, T.M.6
Subramaniam, J.R.7
Rothstein, J.D.8
Marklund, S.9
Andersen, P.M.10
Brannstrom, T.11
Gredal, O.12
Wong, P.C.13
Williams, D.S.14
Cleveland, D.W.15
-
39
-
-
66749104344
-
Mitochondrial function, morphology, and axonal transport in amyotrophic lateral sclerosis
-
Magrane J., Manfredi G. Mitochondrial function, morphology, and axonal transport in amyotrophic lateral sclerosis. Antiox. Redox Signal. 2009, 11(7):1615-1626.
-
(2009)
Antiox. Redox Signal.
, vol.11
, Issue.7
, pp. 1615-1626
-
-
Magrane, J.1
Manfredi, G.2
-
40
-
-
16844366080
-
Mitochondrial dysfunction and its role in motor neuron degeneration in ALS
-
Manfredi G., Xu Z. Mitochondrial dysfunction and its role in motor neuron degeneration in ALS. Mitochondrion 2005, 5(2):77-87.
-
(2005)
Mitochondrion
, vol.5
, Issue.2
, pp. 77-87
-
-
Manfredi, G.1
Xu, Z.2
-
41
-
-
33845361630
-
Motor neuron degeneration in amyotrophic lateral sclerosis mutant superoxide dismutase-1 transgenic mice: mechanisms of mitochondriopathy and cell death
-
Martin L.J., Liu Z., Chen K., Price A.C., Pan Y., Swaby J.W., Golden W.C. Motor neuron degeneration in amyotrophic lateral sclerosis mutant superoxide dismutase-1 transgenic mice: mechanisms of mitochondriopathy and cell death. J. Comp. Neurol. 2007, 500(1):20-46.
-
(2007)
J. Comp. Neurol.
, vol.500
, Issue.1
, pp. 20-46
-
-
Martin, L.J.1
Liu, Z.2
Chen, K.3
Price, A.C.4
Pan, Y.5
Swaby, J.W.6
Golden, W.C.7
-
42
-
-
67649811029
-
The mitochondrial permeability transition pore in motor neurons: involvement in the pathobiology of ALS mice
-
Martin L.J., Gertz B., Pan Y., Price A.C., Molkentin J.D., Chang Q. The mitochondrial permeability transition pore in motor neurons: involvement in the pathobiology of ALS mice. Exp. Neurol. 2009, 218(2):333-346.
-
(2009)
Exp. Neurol.
, vol.218
, Issue.2
, pp. 333-346
-
-
Martin, L.J.1
Gertz, B.2
Pan, Y.3
Price, A.C.4
Molkentin, J.D.5
Chang, Q.6
-
43
-
-
30344442440
-
Disease progression of human SOD1 (G93A) transgenic ALS model rats
-
Matsumoto A., Okada Y., Nakamichi M., Nakamura M., Toyama Y., Sobue G., Nagai M., Aoki M., Itoyama Y., Okano H. Disease progression of human SOD1 (G93A) transgenic ALS model rats. J. Neurosci. Res. 2006, 83(1):119-133.
-
(2006)
J. Neurosci. Res.
, vol.83
, Issue.1
, pp. 119-133
-
-
Matsumoto, A.1
Okada, Y.2
Nakamichi, M.3
Nakamura, M.4
Toyama, Y.5
Sobue, G.6
Nagai, M.7
Aoki, M.8
Itoyama, Y.9
Okano, H.10
-
44
-
-
0033912405
-
Mitochondrial oxidative stress. Physiologic consequences and potential for a role in aging
-
Melov S. Mitochondrial oxidative stress. Physiologic consequences and potential for a role in aging. Ann. N. Y. Acad. Sci. 2000, 908:219-225.
-
(2000)
Ann. N. Y. Acad. Sci.
, vol.908
, pp. 219-225
-
-
Melov, S.1
-
45
-
-
0036176613
-
Mitochondrial involvement in amyotrophic lateral sclerosis
-
Menzies F.M., Ince P.G., Shaw P.J. Mitochondrial involvement in amyotrophic lateral sclerosis. Neurochem. Intren. 2002, 40:543-551.
-
(2002)
Neurochem. Intren.
, vol.40
, pp. 543-551
-
-
Menzies, F.M.1
Ince, P.G.2
Shaw, P.J.3
-
46
-
-
36248984867
-
Spinal cord mitochondria display lower calcium retention capacity compared with brain mitochondria without inherent differences in sensitivity to cyclophilin D inhibition
-
Morota S., Hansson M.J., Ishii N., Kudo Y., Elmer E., Uchino H. Spinal cord mitochondria display lower calcium retention capacity compared with brain mitochondria without inherent differences in sensitivity to cyclophilin D inhibition. J. Neurochem. 2007, 103(5):2066-2076.
-
(2007)
J. Neurochem.
, vol.103
, Issue.5
, pp. 2066-2076
-
-
Morota, S.1
Hansson, M.J.2
Ishii, N.3
Kudo, Y.4
Elmer, E.5
Uchino, H.6
-
47
-
-
34548413597
-
Denervation-induced skeletal muscle atrophy is associated with increased mitochondrial ROS production
-
Muller F.L., Song W., Jang Y.C., Liu Y., Sabia M., Richardson A., Van Remmen H. Denervation-induced skeletal muscle atrophy is associated with increased mitochondrial ROS production. Am. J. Physiol. Regul. Integr. Comp. Physiol. 2007, 293(3):R1159-R1168.
-
(2007)
Am. J. Physiol. Regul. Integr. Comp. Physiol.
, vol.293
, Issue.3
-
-
Muller, F.L.1
Song, W.2
Jang, Y.C.3
Liu, Y.4
Sabia, M.5
Richardson, A.6
Van Remmen, H.7
-
48
-
-
38749087624
-
High rates of superoxide production in skeletal-muscle mitochondria respiring on both complex I- and complex II-linked substrates
-
Muller F.L., Liu Y., Abdul-Ghani M.A., Lustgarten M.S., Bhattacharya A., Jang Y.C., Van Remmen H. High rates of superoxide production in skeletal-muscle mitochondria respiring on both complex I- and complex II-linked substrates. Biochem. J. 2008, 409(2):491-499.
-
(2008)
Biochem. J.
, vol.409
, Issue.2
, pp. 491-499
-
-
Muller, F.L.1
Liu, Y.2
Abdul-Ghani, M.A.3
Lustgarten, M.S.4
Bhattacharya, A.5
Jang, Y.C.6
Van Remmen, H.7
-
49
-
-
0023270442
-
Hepatic ultrastructural changes and liver dysfunction in amyotrophic lateral sclerosis
-
Nakano Y., Hirayama K., Terao K. Hepatic ultrastructural changes and liver dysfunction in amyotrophic lateral sclerosis. Arch. Neurol. 1987, 44(1):103-106.
-
(1987)
Arch. Neurol.
, vol.44
, Issue.1
, pp. 103-106
-
-
Nakano, Y.1
Hirayama, K.2
Terao, K.3
-
50
-
-
0030034832
-
Independent modulation of the activity of ?-ketoglutarate dehydrogenase complex by Ca2+ and Mg2+
-
Panov A., Scarpa A. Independent modulation of the activity of ?-ketoglutarate dehydrogenase complex by Ca2+ and Mg2+. Biochemistry (US) 1996, 35:427-432.
-
(1996)
Biochemistry (US)
, vol.35
, pp. 427-432
-
-
Panov, A.1
Scarpa, A.2
-
51
-
-
1542268971
-
Quantitative evaluation of the effects of mitochondrial permeability transition pore modifiers on accumulation of calcium phosphate: two modes of action of mPTP modifiers
-
Panov A., Andreeva L., Greenamyre J.T. Quantitative evaluation of the effects of mitochondrial permeability transition pore modifiers on accumulation of calcium phosphate: two modes of action of mPTP modifiers. Arch. Biochem. Biophys. 2004, 424:44-52.
-
(2004)
Arch. Biochem. Biophys.
, vol.424
, pp. 44-52
-
-
Panov, A.1
Andreeva, L.2
Greenamyre, J.T.3
-
52
-
-
33847041066
-
Species and tissue specific relationships between mitochondrial permeability transition and generation of ROS in brain and liver mitochondria of rats and mice
-
Panov A., Dikalov S., Shalbuyeva N., Hemendinger R., Greenamyre J.T., Rosenfeld J. Species and tissue specific relationships between mitochondrial permeability transition and generation of ROS in brain and liver mitochondria of rats and mice. Am. J. Physiol. Cell. Physiol. 2007, 292(2):C708-C718.
-
(2007)
Am. J. Physiol. Cell. Physiol.
, vol.292
, Issue.2
-
-
Panov, A.1
Dikalov, S.2
Shalbuyeva, N.3
Hemendinger, R.4
Greenamyre, J.T.5
Rosenfeld, J.6
-
53
-
-
67649743314
-
The neuromediator glutamate, through specific substrate interactions, enhances mitochondrial ATP production and reactive oxygen species generation in nonsynaptic brain mitochondria
-
Panov A., Schonfeld P., Dikalov S., Hemendinger R., Bonkovsky H.L., Brooks B.R. The neuromediator glutamate, through specific substrate interactions, enhances mitochondrial ATP production and reactive oxygen species generation in nonsynaptic brain mitochondria. J. Biol. Chem. 2009, 284(21):14448-14456.
-
(2009)
J. Biol. Chem.
, vol.284
, Issue.21
, pp. 14448-14456
-
-
Panov, A.1
Schonfeld, P.2
Dikalov, S.3
Hemendinger, R.4
Bonkovsky, H.L.5
Brooks, B.R.6
-
54
-
-
77956183145
-
Effects of defatted bovine serum albumin on respiratory activities of brain and liver mitochondria from C57Bl/6G mice and Sprague Dawley rats
-
Panov A.V., Vavilin V.A., Lyalkhovich V.V., Brooks B.R., Bonkovsky H.L. Effects of defatted bovine serum albumin on respiratory activities of brain and liver mitochondria from C57Bl/6G mice and Sprague Dawley rats. Bull. Exp. Biol. Med. 2010, 149(2):187-190.
-
(2010)
Bull. Exp. Biol. Med.
, vol.149
, Issue.2
, pp. 187-190
-
-
Panov, A.V.1
Vavilin, V.A.2
Lyalkhovich, V.V.3
Brooks, B.R.4
Bonkovsky, H.L.5
-
55
-
-
78649960521
-
In vitro effects of cholesterol ?-d-glucoside, cholesterol and cycad phytosterol glucosides on respiration and reactive oxygen species generation in brain mitochondria
-
Panov A., Kubalik N., Brooks B.R., Shaw C.A. In vitro effects of cholesterol ?-d-glucoside, cholesterol and cycad phytosterol glucosides on respiration and reactive oxygen species generation in brain mitochondria. J. Membr. Biol. 2010, 237:71-77.
-
(2010)
J. Membr. Biol.
, vol.237
, pp. 71-77
-
-
Panov, A.1
Kubalik, N.2
Brooks, B.R.3
Shaw, C.A.4
-
56
-
-
79954528757
-
Metabolic and functional differences between brain and spinal cord mitochondria underlie different predisposition to pathology
-
Panov A.V., Kubalik N., Zinchenko N., Hemendinger R., Brooks B.R., Bonkovsky H.L. Metabolic and functional differences between brain and spinal cord mitochondria underlie different predisposition to pathology. Am. J. Physiol. Regul. Integr. 2011, 300(4):R844-R854.
-
(2011)
Am. J. Physiol. Regul. Integr.
, vol.300
, Issue.4
-
-
Panov, A.V.1
Kubalik, N.2
Zinchenko, N.3
Hemendinger, R.4
Brooks, B.R.5
Bonkovsky, H.L.6
-
57
-
-
77955934441
-
ALS-linked mutant SOD1 damages mitochondria by promoting conformational changes in Bcl-2
-
Pedrini S., Sau D., Guareschi S., Bogush M., Brown R.H., Naniche N., Kia A., Trotti D., Pasinelli P. ALS-linked mutant SOD1 damages mitochondria by promoting conformational changes in Bcl-2. Hum. Mol. Genet. 2010, 19(15):2974-2986.
-
(2010)
Hum. Mol. Genet.
, vol.19
, Issue.15
, pp. 2974-2986
-
-
Pedrini, S.1
Sau, D.2
Guareschi, S.3
Bogush, M.4
Brown, R.H.5
Naniche, N.6
Kia, A.7
Trotti, D.8
Pasinelli, P.9
-
58
-
-
0942287085
-
Programmed cell death in amyotrophic lateral sclerosis: a mechanism of pathogenic and therapeutic importance
-
Przedborski S. Programmed cell death in amyotrophic lateral sclerosis: a mechanism of pathogenic and therapeutic importance. Neurologist 2004, 10:1-7.
-
(2004)
Neurologist
, vol.10
, pp. 1-7
-
-
Przedborski, S.1
-
59
-
-
58249088828
-
Cu, Zn-superoxide dismutase-driven free radical modifications: copper- and carbonate radical anion-initiated protein radical chemistry
-
Ramirez D.C., Gomez-Mejiba S.E., Corbett J.T., Deterding L.J., Tomer K.B., Mason R.P. Cu, Zn-superoxide dismutase-driven free radical modifications: copper- and carbonate radical anion-initiated protein radical chemistry. Biochem. J. 2009, 417(1):341-353.
-
(2009)
Biochem. J.
, vol.417
, Issue.1
, pp. 341-353
-
-
Ramirez, D.C.1
Gomez-Mejiba, S.E.2
Corbett, J.T.3
Deterding, L.J.4
Tomer, K.B.5
Mason, R.P.6
-
60
-
-
0035978743
-
Amyotrophic lateral sclerosis
-
Rowland L.P., Shneider N.A. Amyotrophic lateral sclerosis. N. Engl. J. Med. 2001, 344(22):1688-1700.
-
(2001)
N. Engl. J. Med.
, vol.344
, Issue.22
, pp. 1688-1700
-
-
Rowland, L.P.1
Shneider, N.A.2
-
61
-
-
2342442179
-
Ultrastructural study of mitochondria in the spinal cord of transgenic mice with a G93A mutant SOD1 gene
-
Sasaki S., Warita H., Murakami T., Abe K., Iwata M. Ultrastructural study of mitochondria in the spinal cord of transgenic mice with a G93A mutant SOD1 gene. Acta Neuropathol. (Berl) 2004, 107:461-474.
-
(2004)
Acta Neuropathol. (Berl)
, vol.107
, pp. 461-474
-
-
Sasaki, S.1
Warita, H.2
Murakami, T.3
Abe, K.4
Iwata, M.5
-
62
-
-
60849106964
-
Racing against the clock: recognizing differentiating, diagnosing, and referring the amyotrophic lateral sclerosis patient
-
Shook S.J., Pioro E.P. Racing against the clock: recognizing differentiating, diagnosing, and referring the amyotrophic lateral sclerosis patient. Ann. Neurol. 2009, 65(suppl. 1):S10-S16.
-
(2009)
Ann. Neurol.
, vol.65
, Issue.SUPPL. 1
-
-
Shook, S.J.1
Pioro, E.P.2
-
63
-
-
0025471534
-
Rapid isolation of metabolically active mitochondria from rat brain and subregions using Percoll density gradient centrifugation
-
Sims N.R. Rapid isolation of metabolically active mitochondria from rat brain and subregions using Percoll density gradient centrifugation. J. Neurochem. 1990, 55:698-707.
-
(1990)
J. Neurochem.
, vol.55
, pp. 698-707
-
-
Sims, N.R.1
-
64
-
-
33847767167
-
Activities of mitochondrial complexes correlate with nNOS amount in muscle from ALS patients
-
Soraru G., Vergani L., Fedrizzi L., D'Ascenzo C., Polo A., Bernazzi B., Angelini C. Activities of mitochondrial complexes correlate with nNOS amount in muscle from ALS patients. Neuropathol. Appl. Neurobiol. 2007, 33(2):204-211.
-
(2007)
Neuropathol. Appl. Neurobiol.
, vol.33
, Issue.2
, pp. 204-211
-
-
Soraru, G.1
Vergani, L.2
Fedrizzi, L.3
D'Ascenzo, C.4
Polo, A.5
Bernazzi, B.6
Angelini, C.7
-
65
-
-
2642532860
-
Intrinsic differences in brain and spinal cord mitochondria: implication for therapeutic interventions
-
Sullivan P.G., Rabchevsky A.G., Keller J.Y.N., Lovell M., Sodhi A., Hart R.P., Scheffer S.W. Intrinsic differences in brain and spinal cord mitochondria: implication for therapeutic interventions. J. Comparative Neurol. 2004, 474:524-534.
-
(2004)
J. Comparative Neurol.
, vol.474
, pp. 524-534
-
-
Sullivan, P.G.1
Rabchevsky, A.G.2
Keller, J.Y.N.3
Lovell, M.4
Sodhi, A.5
Hart, R.P.6
Scheffer, S.W.7
-
66
-
-
5444222849
-
Calcium-permeable AMPA receptors promote misfolding of mutant SOD1 protein and development of amyotrophic lateral sclerosis in a transgenic mouse model
-
Tateno M., Sadakata H., Tanaka M., Itohara S., Shin R.M., Miura M., Masuda M., Aosaki T., Urushitani M., Misawa H., Takahashi R. Calcium-permeable AMPA receptors promote misfolding of mutant SOD1 protein and development of amyotrophic lateral sclerosis in a transgenic mouse model. Hum. Mol. Genet. 2004, 13:2183-2196.
-
(2004)
Hum. Mol. Genet.
, vol.13
, pp. 2183-2196
-
-
Tateno, M.1
Sadakata, H.2
Tanaka, M.3
Itohara, S.4
Shin, R.M.5
Miura, M.6
Masuda, M.7
Aosaki, T.8
Urushitani, M.9
Misawa, H.10
Takahashi, R.11
-
67
-
-
79551598971
-
Non-invasive diffusion tensor imaging detects white matter degeneration in the spinal cord of a mouse model of amyoptrophic lateral sclerosis
-
Underwood C.K., Kurniiawan N.D., Butler T.J., Cowin J., Wallace R.H. Non-invasive diffusion tensor imaging detects white matter degeneration in the spinal cord of a mouse model of amyoptrophic lateral sclerosis. NeuroImage 2010, 55(2):455-461.
-
(2010)
NeuroImage
, vol.55
, Issue.2
, pp. 455-461
-
-
Underwood, C.K.1
Kurniiawan, N.D.2
Butler, T.J.3
Cowin, J.4
Wallace, R.H.5
-
68
-
-
22244479388
-
Copper-zinc superoxide dismutase and amyotrophic lateral sclerosis
-
Valentine J.S., Doucette P.A., Potter S.Z. Copper-zinc superoxide dismutase and amyotrophic lateral sclerosis. Annu. Rev. Biochem. 2005, 74:563-593.
-
(2005)
Annu. Rev. Biochem.
, vol.74
, pp. 563-593
-
-
Valentine, J.S.1
Doucette, P.A.2
Potter, S.Z.3
-
69
-
-
41649086378
-
Selective association of misfolded ALS-linked mutant SOD1 with the cytoplasmic face of mitochondria
-
Vande Velde C., Miller T.M., Cashman N.R., Cleveland D.W. Selective association of misfolded ALS-linked mutant SOD1 with the cytoplasmic face of mitochondria. Proc. Natl. Acad. Sci. U. S. A. 2008, 105(10):4022-4027.
-
(2008)
Proc. Natl. Acad. Sci. U. S. A.
, vol.105
, Issue.10
, pp. 4022-4027
-
-
Vande Velde, C.1
Miller, T.M.2
Cashman, N.R.3
Cleveland, D.W.4
-
70
-
-
23944465642
-
Ca2+, mitochondria and selective motoneuron vulnerability: implications for ALS
-
Von Lewinski F., Keller B.U. Ca2+, mitochondria and selective motoneuron vulnerability: implications for ALS. Trends Neurosci. 2005, 28(9):494-500.
-
(2005)
Trends Neurosci.
, vol.28
, Issue.9
, pp. 494-500
-
-
Von Lewinski, F.1
Keller, B.U.2
-
71
-
-
0042329888
-
Behavioral and neurological correlates of ALS-parkinsonism dementia complex in adult mice fed washed cycad flour
-
Wilson J.M., Khabazian I., Wong M.C., Seyedalikhani A., Bains J.S., Pasqualotto B.A., Williams D.E., Andersen R.J., Simpson R.J., Smith R., Craig U.K., Kurland L.T., Shaw C.A. Behavioral and neurological correlates of ALS-parkinsonism dementia complex in adult mice fed washed cycad flour. Neuromolecular Med. 2002, 1(3):207-221.
-
(2002)
Neuromolecular Med.
, vol.1
, Issue.3
, pp. 207-221
-
-
Wilson, J.M.1
Khabazian, I.2
Wong, M.C.3
Seyedalikhani, A.4
Bains, J.S.5
Pasqualotto, B.A.6
Williams, D.E.7
Andersen, R.J.8
Simpson, R.J.9
Smith, R.10
Craig, U.K.11
Kurland, L.T.12
Shaw, C.A.13
-
72
-
-
0035896468
-
Dysfunctional mitochondrial respiration in the wobbler mouse brain
-
Xu G.-P., Dave K.R., Moraes C.T., Busto R., Sick T.J., Bradley W.G., Perez-Pinzon M.A. Dysfunctional mitochondrial respiration in the wobbler mouse brain. Neurosci. Lett. 2001, 300:141-144.
-
(2001)
Neurosci. Lett.
, vol.300
, pp. 141-144
-
-
Xu, G.-P.1
Dave, K.R.2
Moraes, C.T.3
Busto, R.4
Sick, T.J.5
Bradley, W.G.6
Perez-Pinzon, M.A.7
-
73
-
-
0028036798
-
Tricarboxylic acid cycle in rat brain synaptosomes. Fluxes and interactions with aspartate aminotransferase and malate/aspartate shuttle
-
Yudkoff M., Nelson D., Daikhin Y., Erecinska M. Tricarboxylic acid cycle in rat brain synaptosomes. Fluxes and interactions with aspartate aminotransferase and malate/aspartate shuttle. J. Biol. Chem. 1994, 269(44):27414-27420.
-
(1994)
J. Biol. Chem.
, vol.269
, Issue.44
, pp. 27414-27420
-
-
Yudkoff, M.1
Nelson, D.2
Daikhin, Y.3
Erecinska, M.4
|