Proteostasis strategies for restoring α1-antitrypsin deficiency

Proceedings of the American Thoracic Society

Volumn 7, Issue 6, 2010, Pages 415-422

  Bouchecareilh, Marion ^a   Conkright, Juliana J ^a,c   Balch, William E ^a,b  

^a Department of Cell Biology ^*  (United States)

^b SCRIPPS RESEARCH INSTITUTE   (United States)

^c Translational Research Institute   (United States)

Author keywords

Alpha 1 antitrypsin deficiency; COPD; Endoplasmic reticulum; Protein folding; Proteostasis

Indexed keywords

PROTEOME;

ALPHA 1 ANTITRYPSIN DEFICIENCY; ENDOPLASMIC RETICULUM; HUMAN; METABOLISM; PROTEIN FOLDING; PROTEOSTASIS DEFICIENCY; REVIEW;

ALPHA 1-ANTITRYPSIN DEFICIENCY; ENDOPLASMIC RETICULUM; HUMANS; PROTEIN FOLDING; PROTEOME; PROTEOSTASIS DEFICIENCIES;

EID: 79952264259     PISSN: 15463222     EISSN: 19435665     Source Type: Journal    
DOI: 10.1513/pats.201001-016AW     Document Type: Conference Paper

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