-
1
-
-
0344021409
-
Prions and the Immune System: A Journey Through Gut, Spleen, and Nerves
-
DOI 10.1016/S0065-2776(03)81004-0
-
A Aguzzi 2003 Prions and the immune system: a journey through gut, spleen, and nerves Adv Immunol 81 123 171 1:CAS:528:DC%2BD2cXhvFaqsrs%3D 14711055 10.1016/S0065-2776(03)81004-0 (Pubitemid 38009043)
-
(2003)
Advances in Immunology
, vol.81
, pp. 123-171
-
-
Aguzzi, A.1
-
3
-
-
53749085861
-
The epidemiology of kuru: Monitoring the epidemic from its peak to its end
-
18849286 10.1098/rstb.2008.0071
-
MP Alpers 2008 The epidemiology of kuru: monitoring the epidemic from its peak to its end Philos Trans R Soc Lond B Biol Sci 363 3707 3713 18849286 10.1098/rstb.2008.0071
-
(2008)
Philos Trans R Soc Lond B Biol Sci
, vol.363
, pp. 3707-3713
-
-
Alpers, M.P.1
-
4
-
-
70350141829
-
Risk of Creutzfeldt-Jakob disease transmission by ocular surgery and tissue transplantation
-
1:STN:280:DC%2BD1MnovFykuw%3D%3D 19136921 10.1038/eye.2008.381
-
WJ Armitage AB Tullo JW Ironside 2009 Risk of Creutzfeldt-Jakob disease transmission by ocular surgery and tissue transplantation Eye 23 1926 1930 1:STN:280:DC%2BD1MnovFykuw%3D%3D 19136921 10.1038/eye.2008.381
-
(2009)
Eye
, vol.23
, pp. 1926-1930
-
-
Armitage, W.J.1
Tullo, A.B.2
Ironside, J.W.3
-
5
-
-
32644461629
-
vCJD prion acquires altered virulence through trans-species infection
-
DOI 10.1016/j.bbrc.2006.01.149, PII S0006291X06002312
-
M Asano S Mohri JW Ironside M Ito N Tamaoki T Kitamoto 2006 vCJD prion acquires altered virulence through trans-species infection Biochem Biophys Res Commun 342 293 299 1:CAS:528:DC%2BD28Xhs1Wlsr4%3D 16480953 10.1016/j.bbrc.2006. 01.149 (Pubitemid 43247390)
-
(2006)
Biochemical and Biophysical Research Communications
, vol.342
, Issue.1
, pp. 293-299
-
-
Asano, M.1
Mohri, S.2
Ironside, J.W.3
Ito, M.4
Tamaoki, N.5
Kitamoto, T.6
-
6
-
-
18744362997
-
BSE prions propagate as either variant CJD-like or sporadic CJD-like prion strains in transgenic mice expressing human prion protein
-
DOI 10.1093/emboj/cdf653
-
E Asante J Linehan M Desbruslais, et al. 2002 BSE prions propagate as either variant CJD-like or sporadic CJD-like prion strains in transgenic mice expressing human prion protein EMBO J 21 6358 6366 1:CAS:528: DC%2BD38XpsFChtbc%3D 12456643 10.1093/emboj/cdf653 (Pubitemid 35448414)
-
(2002)
EMBO Journal
, vol.21
, Issue.23
, pp. 6358-6366
-
-
Asante, E.A.1
Linehan, J.M.2
Desbruslais, M.3
Joiner, S.4
Gowland, I.5
Wood, A.L.6
Welch, J.7
Hill, A.F.8
Lloyd, S.E.9
Wadsworth, J.D.F.10
Collinge, J.11
-
7
-
-
33746057444
-
Dissociation of pathological and molecular phenotype of variant Creutzfeldt-Jakob disease in transgenic human prion protein 129 heterozygous mice
-
DOI 10.1073/pnas.0604292103
-
E Asante J Linehan I Gowland, et al. 2006 Dissociation of pathological and molecular phenotype of variant Creutzfeldt-Jakob disease in transgenic human prion protein 129 heterozygous mice Proc Natl Acad Sci USA 103 10759 10764 1:CAS:528:DC%2BD28XntFWmsbk%3D 16809423 10.1073/pnas.0604292103 (Pubitemid 44078049)
-
(2006)
Proceedings of the National Academy of Sciences of the United States of America
, vol.103
, Issue.28
, pp. 10759-10764
-
-
Asante, E.A.1
Linehan, J.M.2
Gowland, I.3
Joiner, S.4
Fox, K.5
Cooper, S.6
Osiguwa, O.7
Gorry, M.8
Welch, J.9
Houghton, R.10
Desbruslais, M.11
Brandner, S.12
Wadsworth, J.D.F.13
Collinge, J.14
-
8
-
-
34447123223
-
Atypical transmissible spongiform encephalopathies (TSEs) in ruminants
-
17126958 10.1016/j.vaccine.2006.10.058 1:CAS:528:DC%2BD2sXnslWns74%3D
-
T Baron AG Biacabe JN Arsac S Benestad MH Groschup 2006 Atypical transmissible spongiform encephalopathies (TSEs) in ruminants Vaccine 25 5625 5630 17126958 10.1016/j.vaccine.2006.10.058 1:CAS:528:DC%2BD2sXnslWns74%3D
-
(2006)
Vaccine
, vol.25
, pp. 5625-5630
-
-
Baron, T.1
Biacabe, A.G.2
Arsac, J.N.3
Benestad, S.4
Groschup, M.H.5
-
9
-
-
37249001722
-
Sc in vivo
-
DOI 10.1074/jbc.M704329200
-
RM Barron SL Campbell D King, et al. 2007 High titres of TSE infectivity associated with extremely low levels of PrPSc in vivo J Biol Chem 282 35878 35886 1:CAS:528:DC%2BD2sXhtlKrsbrO 17923484 10.1074/jbc.M704329200 (Pubitemid 350277109)
-
(2007)
Journal of Biological Chemistry
, vol.282
, Issue.49
, pp. 35878-35886
-
-
Barron, R.M.1
Campbell, S.L.2
King, D.3
Bellon, A.4
Chapman, K.E.5
Williamson, R.A.6
Manson, J.C.7
-
10
-
-
50049104145
-
Atypical/Nor98 scrapie: Properties of the agent, genetics, and epidemiology
-
18187032 10.1051/vetres:2007056 1:CAS:528:DC%2BD1cXhtFKisb%2FP
-
SL Benestad JN Arsac W Goldmann M Noremark 2008 Atypical/Nor98 scrapie: properties of the agent, genetics, and epidemiology Vet Res 39 19 18187032 10.1051/vetres:2007056 1:CAS:528:DC%2BD1cXhtFKisb%2FP
-
(2008)
Vet Res
, vol.39
, pp. 19
-
-
Benestad, S.L.1
Arsac, J.N.2
Goldmann, W.3
Noremark, M.4
-
11
-
-
38949108662
-
Prominent and persistent extraneural infection in human PrP transgenic mice infected with variant CJD
-
DOI 10.1371/journal.pone.0001419
-
V Beringue A Le Dur P Tixador, et al. 2008 Prominent and persistent extraneural infection in human PrP transgenic mice infected with variant CJD PLoS One 3 e1419 18183299 10.1371/journal.pone.0001419 1:CAS:528: DC%2BD1cXhtVSms7s%3D (Pubitemid 351223230)
-
(2008)
PLoS ONE
, vol.3
, Issue.1
-
-
Beringue, V.1
Le Dur, A.2
Tixador, P.3
Reine, F.4
Lepourry, L.5
Perret-Llaudet, A.6
Haik, S.7
Vilotte, J.-L.8
Fontes, M.9
Laude, H.10
-
12
-
-
50049099543
-
Prion agents diversity and species barrier
-
18519020 10.1051/vetres:2008024 1:CAS:528:DC%2BD1cXhtFKisb7K
-
V Beringue JL Vilotte H Laude 2008 Prion agents diversity and species barrier Vet Res 39 47 18519020 10.1051/vetres:2008024 1:CAS:528: DC%2BD1cXhtFKisb7K
-
(2008)
Vet Res
, vol.39
, pp. 47
-
-
Beringue, V.1
Vilotte, J.L.2
Laude, H.3
-
13
-
-
33646059507
-
Predicting susceptibility and incubation time of human-to-human transmission of vCJD
-
1:STN:280:DC%2BD283isFWjsA%3D%3D 16632309 10.1016/S1474-4422(06)70413-6
-
MT Bishop P Hart L Aitchison, et al. 2006 Predicting susceptibility and incubation time of human-to-human transmission of vCJD Lancet Neurol 5 393 398 1:STN:280:DC%2BD283isFWjsA%3D%3D 16632309 10.1016/S1474-4422(06)70413-6
-
(2006)
Lancet Neurol
, vol.5
, pp. 393-398
-
-
Bishop, M.T.1
Hart, P.2
Aitchison, L.3
-
14
-
-
27144451227
-
Prion generation in vitro: Amyloid of Ure2p is infectious
-
DOI 10.1038/sj.emboj.7600772, PII 7600772
-
A Brachmann U Baxa RB Wickner 2005 Prion generation in vitro: amyloid of Ure2p is infectious EMBO J 24 3082 3092 1:CAS:528:DC%2BD2MXpsleksr8%3D 16096644 10.1038/sj.emboj.7600772 (Pubitemid 41486344)
-
(2005)
EMBO Journal
, vol.24
, Issue.17
, pp. 3082-3092
-
-
Brachmann, A.1
Baxa, U.2
Wickner, R.B.3
-
15
-
-
53749101923
-
Central and peripheral pathology of kuru: Pathological analysis of a recent case and comparison with other forms of human prion disease
-
18849292 10.1098/rstb.2008.0091
-
S Brandner J Whitfield K Boone, et al. 2008 Central and peripheral pathology of kuru: pathological analysis of a recent case and comparison with other forms of human prion disease Philos Trans R Soc Lond B Biol Sci 363 3755 3763 18849292 10.1098/rstb.2008.0091
-
(2008)
Philos Trans R Soc Lond B Biol Sci
, vol.363
, pp. 3755-3763
-
-
Brandner, S.1
Whitfield, J.2
Boone, K.3
-
16
-
-
0023243707
-
The epidemiology of Creutzfeldt-Jakob disease: Conclusion of a 15-year investigation in France and review of the world literature
-
1:STN:280:DyaL2s3ivFGntg%3D%3D 3295589
-
P Brown F Cathala RF Raubertas DC Gajdusek P Castaigne 1987 The epidemiology of Creutzfeldt-Jakob disease: conclusion of a 15-year investigation in France and review of the world literature Neurology 37 895 904 1:STN:280:DyaL2s3ivFGntg%3D%3D 3295589
-
(1987)
Neurology
, vol.37
, pp. 895-904
-
-
Brown, P.1
Cathala, F.2
Raubertas, R.F.3
Gajdusek, D.C.4
Castaigne, P.5
-
17
-
-
0034711176
-
Iatrogenic Creutzfeldt-Jakob disease at the millennium
-
1:STN:280:DC%2BD3crht12rsg%3D%3D 11071481
-
P Brown M Preece JP Brandel, et al. 2000 Iatrogenic Creutzfeldt-Jakob disease at the millennium Neurology 55 1075 1081 1:STN:280: DC%2BD3crht12rsg%3D%3D 11071481
-
(2000)
Neurology
, vol.55
, pp. 1075-1081
-
-
Brown, P.1
Preece, M.2
Brandel, J.P.3
-
18
-
-
0026667331
-
"Friendly fire" in medicine: Hormones, homografts, and Creutzfeldt-Jakob disease
-
1:STN:280:DyaK38zgtFWrug%3D%3D 1351607 10.1016/0140-6736(92)92431-E
-
P Brown MA Preece RG Will 1992 "Friendly fire" in medicine: hormones, homografts, and Creutzfeldt-Jakob disease Lancet 340 24 27 1:STN:280:DyaK38zgtFWrug%3D%3D 1351607 10.1016/0140-6736(92)92431-E
-
(1992)
Lancet
, vol.340
, pp. 24-27
-
-
Brown, P.1
Preece, M.A.2
Will, R.G.3
-
19
-
-
0141849861
-
Neuropathology of prion diseases
-
DOI 10.1093/bmb/66.1.121
-
H Budka 2003 Neuropathology of prion diseases Br Med Bull 66 121 130 1:CAS:528:DC%2BD3sXnvVeqsbw%3D 14522854 10.1093/bmb/66.1.121 (Pubitemid 37173497)
-
(2003)
British Medical Bulletin
, vol.66
, pp. 121-130
-
-
Budka, H.1
-
20
-
-
0028876473
-
Neuropathological diagnostic criteria for Creutzfeldt-Jakob disease (CJD) and other human spongiform encephalopathies (Prion diseases)
-
1:STN:280:DyaK28vgtFOrtg%3D%3D 8974629 10.1111/j.1750-3639.1995.tb00625.x
-
H Budka A Aguzzi P Brown, et al. 1995 Neuropathological diagnostic criteria for Creutzfeldt-Jakob disease (CJD) and other human spongiform encephalopathies (Prion diseases) Brain Pathol 5 459 466 1:STN:280: DyaK28vgtFOrtg%3D%3D 8974629 10.1111/j.1750-3639.1995.tb00625.x
-
(1995)
Brain Pathol
, vol.5
, pp. 459-466
-
-
Budka, H.1
Aguzzi, A.2
Brown, P.3
-
21
-
-
33749254251
-
Classification of sporadic Creutzfeldt-Jakob disease revisited
-
DOI 10.1093/brain/awl224
-
I Cali R Castellani J Yuan, et al. 2006 Classification of sporadic Creutzfeldt-Jakob disease revisited Brain 129 2266 2277 16923954 10.1093/brain/awl224 (Pubitemid 44522113)
-
(2006)
Brain
, vol.129
, Issue.9
, pp. 2266-2277
-
-
Cali, I.1
Castellani, R.2
Yuan, J.3
Al-Shekhlee, A.4
Cohen, M.L.5
Xiao, X.6
Moleres, F.J.7
Parchi, P.8
Zou, W.-Q.9
Gambetti, P.10
-
22
-
-
33750310849
-
Prions and their partners in crime
-
DOI 10.1038/nature05294, PII NATURE05294
-
B Caughey GS Baron 2006 Prions and their partners in crime Nature 443 803 810 1:CAS:528:DC%2BD28XhtVyktbbI 17051207 10.1038/nature05294 (Pubitemid 44622685)
-
(2006)
Nature
, vol.443
, Issue.7113
, pp. 803-810
-
-
Caughey, B.1
Baron, G.S.2
-
23
-
-
0030768832
-
Allelic origin of the abnormal prion protein isoform in familial prion diseases
-
DOI 10.1038/nm0997-1009
-
SG Chen P Parchi P Brown, et al. 1997 Allelic origin of the abnormal prion protein isoform in familial prion diseases Nat Med 3 1009 1015 1:CAS:528:DyaK2sXlvVylsrY%3D 9288728 10.1038/nm0997-1009 (Pubitemid 27391956)
-
(1997)
Nature Medicine
, vol.3
, Issue.9
, pp. 1009-1015
-
-
Chen, S.G.1
Parchi, P.2
Brown, P.3
Capellari, S.4
Zou, W.5
Cochran, E.J.6
Vnencak-Jones, C.L.7
Julien, J.8
Vital, C.9
Mikol, J.10
Lugaresi, E.11
Autilio-Gambetti, L.12
Gambetti, P.13
-
24
-
-
67650078963
-
Prevalence of disease related prion protein in anonymous tonsil specimens in Britain: Cross sectional opportunistic survey
-
19460798 10.1136/bmj.b1442
-
JP Clewley CM Kelly N Andrews, et al. 2009 Prevalence of disease related prion protein in anonymous tonsil specimens in Britain: cross sectional opportunistic survey BMJ 338 b1442 19460798 10.1136/bmj.b1442
-
(2009)
BMJ
, vol.338
, pp. 1442
-
-
Clewley, J.P.1
Kelly, C.M.2
Andrews, N.3
-
25
-
-
0025859996
-
Genetic predisposition to iatrogenic Creutzfeldt-Jakob disease
-
1:STN:280:DyaK3M3mtVWqsw%3D%3D 1675319 10.1016/0140-6736(91)93128-V
-
J Collinge MS Palmer AJ Dryden 1991 Genetic predisposition to iatrogenic Creutzfeldt-Jakob disease Lancet 337 1441 1442 1:STN:280:DyaK3M3mtVWqsw%3D%3D 1675319 10.1016/0140-6736(91)93128-V
-
(1991)
Lancet
, vol.337
, pp. 1441-1442
-
-
Collinge, J.1
Palmer, M.S.2
Dryden, A.J.3
-
26
-
-
0033600407
-
Variant Creutzfeldt-Jakob disease
-
DOI 10.1016/S0140-6736(99)05128-4
-
J Collinge 1999 Variant Creutzfeldt-Jakob disease Lancet 354 317 323 1:STN:280:DyaK1Mzms12gtA%3D%3D 10440324 10.1016/S0140-6736(99)05128-4 (Pubitemid 29348751)
-
(1999)
Lancet
, vol.354
, Issue.9175
, pp. 317-323
-
-
Collinge, J.1
-
27
-
-
0034916581
-
Prion diseases of humans and animals: Their causes and molecular basis
-
DOI 10.1146/annurev.neuro.24.1.519
-
J Collinge 2001 Prion diseases of humans and animals: their causes and molecular basis Annu Rev Neurosci 24 519 550 1:CAS:528:DC%2BD3MXls1Shs7s%3D 11283320 10.1146/annurev.neuro.24.1.519 (Pubitemid 32695238)
-
(2001)
Annual Review of Neuroscience
, vol.24
, pp. 519-550
-
-
Collinge, J.1
-
28
-
-
21344445937
-
Molecular neurology of prion disease
-
DOI 10.1136/jnnp.2004.048660
-
J Collinge 2005 Molecular neurology of prion disease J Neurol Neurosurg Psychiatry 76 906 919 1:STN:280:DC%2BD2Mzhs1Clsw%3D%3D 15965195 10.1136/jnnp.2004.048660 (Pubitemid 40909547)
-
(2005)
Journal of Neurology, Neurosurgery and Psychiatry
, vol.76
, Issue.7
, pp. 906-919
-
-
Collinge, J.1
-
29
-
-
0026650443
-
Inherited prion disease with 144 base pair gene insertion: II: Clinical and pathological features
-
1352725 10.1093/brain/115.3.687
-
J Collinge J Brown J Hardy, et al. 1992 Inherited prion disease with 144 base pair gene insertion: II: Clinical and pathological features Brain 115 687 710 1352725 10.1093/brain/115.3.687
-
(1992)
Brain
, vol.115
, pp. 687-710
-
-
Collinge, J.1
Brown, J.2
Hardy, J.3
-
30
-
-
36049020231
-
A general model of prion strains and their pathogenicity
-
DOI 10.1126/science.1138718
-
J Collinge A Clarke 2007 A general model of prion strains and their pathogenicity Science 318 930 936 1:CAS:528:DC%2BD2sXht1KhsLrF 17991853 10.1126/science.1138718 (Pubitemid 350098981)
-
(2007)
Science
, vol.318
, Issue.5852
, pp. 930-936
-
-
Collinge, J.1
Clarke, A.R.2
-
31
-
-
0024474822
-
Diagnosis of Gerstmann-Straussler syndrome in familial dementia with prion protein gene analysis
-
1:STN:280:DyaL1M3psVOksg%3D%3D 2567794 10.1016/S0140-6736(89)90256-0
-
J Collinge AE Harding F Owen, et al. 1989 Diagnosis of Gerstmann-Straussler syndrome in familial dementia with prion protein gene analysis Lancet 2 15 17 1:STN:280:DyaL1M3psVOksg%3D%3D 2567794 10.1016/S0140-6736(89)90256-0
-
(1989)
Lancet
, vol.2
, pp. 15-17
-
-
Collinge, J.1
Harding, A.E.2
Owen, F.3
-
32
-
-
0025330687
-
Prion dementia without characteristic pathology
-
DOI 10.1016/0140-6736(90)91518-F
-
J Collinge F Owen M Poulter, et al. 1990 Prion dementia without characteristic pathology Lancet 336 7 9 1:STN:280:DyaK3czgvFGisQ%3D%3D 1973256 10.1016/0140-6736(90)91518-F (Pubitemid 20207867)
-
(1990)
Lancet
, vol.336
, Issue.8706
, pp. 7-9
-
-
Collinge, J.1
Owen, F.2
Poulter, M.3
Leach, M.4
Crow, T.J.5
Rossor, M.N.6
Hardy, J.7
Mullan, M.J.8
Janota, I.9
Lantos, P.L.10
-
33
-
-
13344293718
-
Unaltered susceptibility to BSE in transgenic mice expressing human prion protein
-
1:CAS:528:DyaK28XltFSr 8524411 10.1038/378779a0
-
J Collinge MS Palmer KCL Sidle, et al. 1995 Unaltered susceptibility to BSE in transgenic mice expressing human prion protein Nature 378 779 783 1:CAS:528:DyaK28XltFSr 8524411 10.1038/378779a0
-
(1995)
Nature
, vol.378
, pp. 779-783
-
-
Collinge, J.1
Palmer, M.S.2
Sidle, K.C.L.3
-
34
-
-
0029831213
-
Molecular analysis of prion strain variation and the aetiology of 'new variant' CJD
-
DOI 10.1038/383685a0
-
J Collinge KC Sidle J Meads J Ironside AF Hill 1996 Molecular analysis of prion strain variation and the aetiology of 'new variant' CJD Nature 383 685 690 1:CAS:528:DyaK28XmsVGgu7Y%3D 8878476 10.1038/383685a0 (Pubitemid 26360638)
-
(1996)
Nature
, vol.383
, Issue.6602
, pp. 685-690
-
-
Collinge, J.1
Sidle, K.C.L.2
Meads, J.3
Ironside, J.4
Hill, A.F.5
-
35
-
-
33745440706
-
Kuru in the 21st century-an acquired human prion disease with very long incubation periods
-
DOI 10.1016/S0140-6736(06)68930-7, PII S0140673606689307
-
J Collinge J Whitfield E McKintosh, et al. 2006 Kuru in the 21st century-an acquired human prion disease with very long incubation periods Lancet 367 2068 2074 16798390 10.1016/S0140-6736(06)68930-7 (Pubitemid 43949290)
-
(2006)
Lancet
, vol.367
, Issue.9528
, pp. 2068-2074
-
-
Collinge, J.1
Whitfield, J.2
McKintosh, E.3
Beck, J.4
Mead, S.5
Thomas, D.J.6
Alpers, M.P.7
-
36
-
-
53749107527
-
A clinical study of kuru patients with long incubation periods at the end of the epidemic in Papua New Guinea
-
18849289 10.1098/rstb.2008.0068
-
J Collinge J Whitfield E McKintosh, et al. 2008 A clinical study of kuru patients with long incubation periods at the end of the epidemic in Papua New Guinea Philos Trans R Soc Lond B Biol Sci 363 3725 3739 18849289 10.1098/rstb.2008.0068
-
(2008)
Philos Trans R Soc Lond B Biol Sci
, vol.363
, pp. 3725-3739
-
-
Collinge, J.1
Whitfield, J.2
McKintosh, E.3
-
37
-
-
0033608367
-
Surgical treatment and risk of sporadic Creutzfeldt-Jakob disease: A case-control study
-
DOI 10.1016/S0140-6736(98)08138-0
-
S Collins MG Law A Fletcher A Boyd J Kaldor CL Masters 1999 Surgical treatment and risk of sporadic Creutzfeldt-Jakob disease: a case-control study Lancet 353 693 697 1:STN:280:DyaK1M7ntFGiug%3D%3D 10073510 10.1016/S0140- 6736(98)08138-0 (Pubitemid 29103801)
-
(1999)
Lancet
, vol.353
, Issue.9154
, pp. 693-697
-
-
Collins, S.1
Law, M.G.2
Fletcher, A.3
Boyd, A.4
Kaldor, J.5
Masters, C.L.6
-
38
-
-
33749236229
-
Determinants of diagnostic investigation sensitivities across the clinical spectrum of sporadic Creutzfeldt-Jakob disease
-
DOI 10.1093/brain/awl159
-
SJ Collins P Sanchez-Juan CL Masters, et al. 2006 Determinants of diagnostic investigation sensitivities across the clinical spectrum of sporadic Creutzfeldt-Jakob disease Brain 129 2278 2287 1:STN:280:DC%2BD28vpvVOksQ%3D%3D 16816392 10.1093/brain/awl159 (Pubitemid 44522114)
-
(2006)
Brain
, vol.129
, Issue.9
, pp. 2278-2287
-
-
Collins, S.J.1
Sanchez-Juan, P.2
Masters, C.L.3
Klug, G.M.4
Van Duijn, C.5
Poleggi, A.6
Pocchiari, M.7
Almonti, S.8
Cuadrado-Corrales, N.9
De Pedro-Cuesta, J.10
Budka, H.11
Gelpi, E.12
Glatzel, M.13
Tolnay, M.14
Hewer, E.15
Zerr, I.16
Heinemann, U.17
Kretszchmar, H.A.18
Jansen, G.H.19
Olsen, E.20
Mitrova, E.21
Alperovitch, A.22
Brandel, J.-P.23
Mackenzie, J.24
Murray, K.25
Will, R.G.26
more..
-
39
-
-
58149280203
-
Detection and characterization of proteinase K-sensitive disease-related prion protein with thermolysin
-
1:CAS:528:DC%2BD1cXhtlGls7fK 18684106 10.1042/BJ20081235
-
S Cronier N Gros MH Tattum, et al. 2008 Detection and characterization of proteinase K-sensitive disease-related prion protein with thermolysin Biochem J 416 297 305 1:CAS:528:DC%2BD1cXhtlGls7fK 18684106 10.1042/BJ20081235
-
(2008)
Biochem J
, vol.416
, pp. 297-305
-
-
Cronier, S.1
Gros, N.2
Tattum, M.H.3
-
40
-
-
0033619758
-
New insight into abnormal prion protein using monoclonal antibodies
-
1:CAS:528:DyaK1MXnvFaqtLY%3D 10600476 10.1006/bbrc.1999.1730
-
S Demart JG Fournier C Creminon, et al. 1999 New insight into abnormal prion protein using monoclonal antibodies Biochem Biophys Res Commun 265 652 657 1:CAS:528:DyaK1MXnvFaqtLY%3D 10600476 10.1006/bbrc.1999.1730
-
(1999)
Biochem Biophys Res Commun
, vol.265
, pp. 652-657
-
-
Demart, S.1
Fournier, J.G.2
Creminon, C.3
-
42
-
-
4744338847
-
Analysis of 2000 consecutive UK tonsillectomy specimens for disease-related prion protein
-
DOI 10.1016/S0140-6736(04)17143-2, PII S0140673604171432
-
A Frosh LC Smith CJ Jackson, et al. 2004 Analysis of 2000 consecutive UK tonsillectomy specimens for disease-related prion protein Lancet 364 1260 1262 15464187 10.1016/S0140-6736(04)17143-2 (Pubitemid 39311347)
-
(2004)
Lancet
, vol.364
, Issue.9441
, pp. 1260-1262
-
-
Frosh, A.1
Smith, L.C.2
Jackson, C.J.3
Linehan, J.M.4
Brandner, S.5
Wadsworth, J.D.F.6
Collinge, J.7
-
43
-
-
0030069023
-
Insoluble wild-type and protease-resistant mutant prion protein in brains of patients with inherited prion disease
-
DOI 10.1038/nm0196-59
-
R Gabizon G Telling Z Meiner M Halimi I Kahana SB Prusiner 1996 Insoluble wild-type and protease-resistant mutant prion protein in brains of patients with inherited prion disease Nat Med 2 59 64 1:CAS:528:DyaK28XivVSmsg%3D%3D 8564843 10.1038/nm0196-59 (Pubitemid 26028074)
-
(1996)
Nature Medicine
, vol.2
, Issue.1
, pp. 59-64
-
-
Gabizon, R.1
Telling, G.2
Meiner, Z.3
Halimi, M.4
Kahana, I.5
Prusiner, S.B.6
-
44
-
-
46749121818
-
A novel human disease with abnormal prion protein sensitive to protease
-
DOI 10.1002/ana.21420
-
P Gambetti Z Dong J Yuan, et al. 2008 A novel human disease with abnormal prion protein sensitive to protease Ann Neurol 63 697 708 1:CAS:528: DC%2BD1cXptFegurw%3D 18571782 10.1002/ana.21420 (Pubitemid 351945529)
-
(2008)
Annals of Neurology
, vol.63
, Issue.6
, pp. 697-708
-
-
Gambetti, P.1
Dong, Z.2
Yuan, J.3
Xiao, X.4
Zheng, M.5
Alshekhlee, A.6
Castellani, R.7
Cohen, M.8
Barria, M.A.9
Gonzalez-Romero, D.10
Belay, E.D.11
Schonberger, L.B.12
Marder, K.13
Harris, C.14
Burke, J.R.15
Montine, T.16
Wisniewski, T.17
Dickson, D.W.18
Soto, C.19
Hulette, C.M.20
Mastrianni, J.A.21
Kong, Q.22
Zou, W.-Q.23
more..
-
45
-
-
0141514771
-
Sporadic and familial CJD: Classification and characterisation
-
DOI 10.1093/bmb/66.1.213
-
P Gambetti Q Kong W Zou P Parchi SG Chen 2003 Sporadic and familial CJD: classification and characterisation Br Med Bull 66 213 239 1:CAS:528: DC%2BD3sXnvVeqtrk%3D 14522861 10.1093/bmb/66.1.213 (Pubitemid 37173504)
-
(2003)
British Medical Bulletin
, vol.66
, pp. 213-239
-
-
Gambetti, P.1
Kong, Q.2
Zou, W.3
Parchi, P.4
Chen, S.G.5
-
46
-
-
0242361687
-
Extraneural Pathologic Prion Protein in Sporadic Creutzfeldt-Jakob Disease
-
DOI 10.1056/NEJMoa030351
-
M Glatzel E Abela M Maissen A Aguzzi 2003 Extraneural pathologic prion protein in sporadic Creutzfeldt-Jakob disease N Engl J Med 349 1812 1820 1:CAS:528:DC%2BD3sXosl2gur8%3D 14602879 10.1056/NEJMoa030351 (Pubitemid 37362957)
-
(2003)
New England Journal of Medicine
, vol.349
, Issue.19
, pp. 1812-1820
-
-
Glatzel, M.1
Abela, E.2
Maissen, M.3
Aguzzi, A.4
-
47
-
-
0014190760
-
Self replication and scrapie
-
1:STN:280:DyaF1c%2Fht1amtw%3D%3D 4964084 10.1038/2151043a0
-
JS Griffith 1967 Self replication and scrapie Nature 215 1043 1044 1:STN:280:DyaF1c%2Fht1amtw%3D%3D 4964084 10.1038/2151043a0
-
(1967)
Nature
, vol.215
, pp. 1043-1044
-
-
Griffith, J.S.1
-
48
-
-
0028990981
-
The original Gerstmann-Straussler-Scheinker family of Austria: Divergent clinicopathological phenotypes but constant PrP genotype
-
1:STN:280:DyaK28%2FkvVWmsg%3D%3D 8520719 10.1111/j.1750-3639.1995. tb00596.x
-
JA Hainfellner S Brantner-Inthaler L Cervenáková, et al. 1995 The original Gerstmann-Straussler-Scheinker family of Austria: divergent clinicopathological phenotypes but constant PrP genotype Brain Pathol 5 201 211 1:STN:280:DyaK28%2FkvVWmsg%3D%3D 8520719 10.1111/j.1750-3639.1995.tb00596.x
-
(1995)
Brain Pathol
, vol.5
, pp. 201-211
-
-
Hainfellner, J.A.1
Brantner-Inthaler, S.2
Cervenáková, L.3
-
49
-
-
2542618458
-
Prion protein heterogeneity in sporadic but not variant Creutzfeldt-Jakob disease: U.K. cases 1991-2002
-
DOI 10.1002/ana.20127
-
MW Head TJ Bunn MT Bishop, et al. 2004 Prion protein heterogeneity in sporadic but not variant Creutzfeldt-Jakob disease: U.K. cases 1991-2002 Ann Neurol 55 851 859 1:CAS:528:DC%2BD2cXlsVCkurs%3D 15174020 10.1002/ana.20127 (Pubitemid 38702581)
-
(2004)
Annals of Neurology
, vol.55
, Issue.6
, pp. 851-859
-
-
Head, M.W.1
Bunn, T.J.R.2
Bishop, M.T.3
McLoughlin, V.4
Lowrie, S.5
McKimmie, C.S.6
Williams, M.C.7
McCardle, L.8
MacKenzie, J.9
Knight, R.10
Will, R.G.11
Ironside, J.W.12
-
50
-
-
33749242953
-
Sporadic Creutzfeldt-Jakob disease: Further twists and turns in a convoluted protein
-
DOI 10.1093/brain/awl225
-
MW Head JW Ironside 2006 Sporadic Creutzfeldt-Jakob disease: further twists and turns in a convoluted protein Brain 129 2238 2240 16923953 10.1093/brain/awl225 (Pubitemid 44522111)
-
(2006)
Brain
, vol.129
, Issue.9
, pp. 2238-2240
-
-
Head, M.W.1
Ironside, J.W.2
-
51
-
-
1142267004
-
Peripheral tissue involvement in sporadic, iatrogenic, and variant Creutzfeldt-Jakob disease: An immunohistochemical, quantitative, and biochemical study
-
1:CAS:528:DC%2BD2cXlsVCgtw%3D%3D 14695328
-
MW Head D Ritchie N Smith, et al. 2004 Peripheral tissue involvement in sporadic, iatrogenic, and variant Creutzfeldt-Jakob disease: an immunohistochemical, quantitative, and biochemical study Am J Pathol 164 143 153 1:CAS:528:DC%2BD2cXlsVCgtw%3D%3D 14695328
-
(2004)
Am J Pathol
, vol.164
, pp. 143-153
-
-
Head, M.W.1
Ritchie, D.2
Smith, N.3
-
52
-
-
0033573778
-
Investigation of variant Creutzfeldt-Jakob disease and other human prion diseases with tonsil biopsy samples
-
DOI 10.1016/S0140-6736(98)12075-5
-
AF Hill RJ Butterworth S Joiner, et al. 1999 Investigation of variant Creutzfeldt-Jakob disease and other human prion diseases with tonsil biopsy samples Lancet 353 183 189 1:STN:280:DyaK1M7itVOnug%3D%3D 9923873 10.1016/S0140-6736(98)12075-5 (Pubitemid 29088029)
-
(1999)
Lancet
, vol.353
, Issue.9148
, pp. 183-189
-
-
Hill, A.F.1
Butterworth, R.J.2
Joiner, S.3
Jackson, G.4
Rossor, M.N.5
Thomas, D.J.6
Frosh, A.7
Tolley, N.8
Bell, J.E.9
Spencer, M.10
King, A.11
Al-Sarraj, S.12
Ironside, J.W.13
Lantos, P.L.14
Collinge, J.15
-
53
-
-
33244468109
-
Distinct glycoform ratios of protease resistant prion protein associated with PRNP point mutations
-
DOI 10.1093/brain/awl013
-
AF Hill S Joiner J Beck, et al. 2006 Distinct glycoform ratios of protease resistant prion protein associated with PRNP point mutations Brain 129 676 685 16415305 10.1093/brain/awl013 (Pubitemid 43278229)
-
(2006)
Brain
, vol.129
, Issue.3
, pp. 676-685
-
-
Hill, A.F.1
Joiner, S.2
Beck, J.A.3
Campbell, T.A.4
Dickinson, A.5
Poulter, M.6
Wadsworth, J.D.F.7
Collinge, J.8
-
54
-
-
0037677595
-
Molecular classification of sporadic Creutzfeldt-Jakob disease
-
DOI 10.1093/brain/awg125
-
AF Hill S Joiner JD Wadsworth, et al. 2003 Molecular classification of sporadic Creutzfeldt-Jakob disease Brain 126 1333 1346 12764055 10.1093/brain/awg125 (Pubitemid 36644379)
-
(2003)
Brain
, vol.126
, Issue.6
, pp. 1333-1346
-
-
Hill, A.F.1
Joiner, S.2
Wadsworth, J.D.F.3
Sidle, K.C.L.4
Bell, J.E.5
Budka, H.6
Ironside, J.W.7
Collinge, J.8
-
55
-
-
0031015906
-
Diagnosis of new variant Creutzfeldt-Jakob disease by tonsil biopsy
-
DOI 10.1016/S0140-6736(97)24002-X
-
AF Hill M Zeidler J Ironside J Collinge 1997 Diagnosis of new variant Creutzfeldt-Jakob disease by tonsil biopsy Lancet 349 99 100 1:STN:280:DyaK2s7kvFKitA%3D%3D 8996424 10.1016/S0140-6736(97)24002-X (Pubitemid 27023429)
-
(1997)
Lancet
, vol.349
, Issue.9045
, pp. 99-100
-
-
Hill, A.F.1
Zeidler, M.2
Ironside, J.3
Collinge, J.4
-
56
-
-
3242716876
-
Prevalence of lymphoreticular prion protein accumulation in UK tissue samples
-
DOI 10.1002/path.1580
-
DA Hilton AC Ghani L Conyers, et al. 2004 Prevalence of lymphoreticular prion protein accumulation in UK tissue samples J Pathol 203 733 739 1:CAS:528:DC%2BD2cXmtFSmt7o%3D 15221931 10.1002/path.1580 (Pubitemid 38961558)
-
(2004)
Journal of Pathology
, vol.203
, Issue.3
, pp. 733-739
-
-
Hilton, D.A.1
Ghani, A.C.2
Conyers, L.3
Edwards, P.4
McCardle, L.5
Ritchie, D.6
Penney, M.7
Hegazy, D.8
Ironside, J.W.9
-
57
-
-
12144289549
-
Specificity of lymphoreticular accumulation of prion protein for variant Creutzfeldt-Jakob disease
-
DOI 10.1136/jcp.2003.012278
-
DA Hilton J Sutak ME Smith, et al. 2004 Specificity of lymphoreticular accumulation of prion protein for variant Creutzfeldt-Jakob disease J Clin Pathol 57 300 302 1:CAS:528:DC%2BD2cXntVagu70%3D 14990604 10.1136/jcp.2003. 012278 (Pubitemid 38338845)
-
(2004)
Journal of Clinical Pathology
, vol.57
, Issue.3
, pp. 300-302
-
-
Hilton, D.A.1
Sutak, J.2
Smith, M.E.F.3
Penney, M.4
Conyers, L.5
Edwards, P.6
McCardle, L.7
Ritchie, D.8
Head, M.W.9
Wiley, C.A.10
Ironside, J.W.11
-
58
-
-
63649142297
-
Human prion protein (PrP) 219 K is converted to PrPSc but shows heterozygous inhibition in variant Creutzfeldt-Jakob disease infection
-
1:CAS:528:DC%2BD1MXht1OrtLk%3D 19074151 10.1074/jbc.M809254200
-
M Hizume A Kobayashi K Teruya, et al. 2009 Human prion protein (PrP) 219 K is converted to PrPSc but shows heterozygous inhibition in variant Creutzfeldt-Jakob disease infection J Biol Chem 284 3603 3609 1:CAS:528:DC%2BD1MXht1OrtLk%3D 19074151 10.1074/jbc.M809254200
-
(2009)
J Biol Chem
, vol.284
, pp. 3603-3609
-
-
Hizume, M.1
Kobayashi, A.2
Teruya, K.3
-
59
-
-
1642416427
-
Neuropathology and molecular biology of variant Creutzfeldt-Jakob disease
-
1:CAS:528:DC%2BD2cXlvFSiurs%3D 15148991
-
JW Ironside MW Head 2004 Neuropathology and molecular biology of variant Creutzfeldt-Jakob disease Curr Top Microbiol Immunol 284 133 159 1:CAS:528:DC%2BD2cXlvFSiurs%3D 15148991
-
(2004)
Curr Top Microbiol Immunol
, vol.284
, pp. 133-159
-
-
Ironside, J.W.1
Head, M.W.2
-
60
-
-
0033930868
-
Laboratory diagnosis of variant Creutzfeldt-Jakob disease
-
DOI 10.1046/j.1365-2559.2000.00946.x
-
JW Ironside MW Head JE Bell L McCardle RG Will 2000 Laboratory diagnosis of variant Creutzfeldt-Jakob disease Histopathology 37 1 9 1:STN:280: DC%2BD3cvgsVWrsA%3D%3D 10931212 10.1046/j.1365-2559.2000.00946.x (Pubitemid 30496729)
-
(2000)
Histopathology
, vol.37
, Issue.1
, pp. 1-9
-
-
Ironside, J.W.1
Head, M.W.2
Bell, J.E.3
McCardle, L.4
Will, R.G.5
-
61
-
-
25444525438
-
High levels of disease related prion protein in the ileum in variant Creutzfeldt-Jakob disease [9]
-
DOI 10.1136/gut.2005.072447
-
S Joiner J Linehan S Brandner JD Wadsworth J Collinge 2005 High levels of disease related prion protein in the ileum in variant Creutzfeldt-Jakob disease Gut 54 1506 1508 1:STN:280:DC%2BD2Mvpt1Shsg%3D%3D 16162963 10.1136/gut.2005. 072447 (Pubitemid 41375217)
-
(2005)
Gut
, vol.54
, Issue.10
, pp. 1506-1508
-
-
Joiner, S.1
Linehan, J.M.2
Brandner, S.3
Wadsworth, J.D.F.4
Collinge, J.5
-
62
-
-
1642617641
-
Protein-only transmission of three yeast prion strains
-
DOI 10.1038/nature02391
-
CY King R Diaz-Avalos 2004 Protein-only transmission of three yeast prion strains Nature 428 319 323 1:CAS:528:DC%2BD2cXitFCnuro%3D 15029195 10.1038/nature02391 (Pubitemid 38418802)
-
(2004)
Nature
, vol.428
, Issue.6980
, pp. 319-323
-
-
King, C.-Y.1
Diaz-Avalos, R.2
-
63
-
-
24344492256
-
Chronic wasting disease of elk: Transmissibility to humans examined by transgenic mouse models
-
DOI 10.1523/JNEUROSCI.2467-05.2005
-
Q Kong S Huang W Zou, et al. 2005 Chronic wasting disease of elk: transmissibility to humans examined by transgenic mouse models J Neurosci 25 7944 7949 1:CAS:528:DC%2BD2MXhtVaktrfO 16135751 10.1523/JNEUROSCI.2467-05.2005 (Pubitemid 41254397)
-
(2005)
Journal of Neuroscience
, vol.25
, Issue.35
, pp. 7944-7949
-
-
Kong, Q.1
Huang, S.2
Zou, W.3
Vanegas, D.4
Wang, M.5
Wu, D.6
Yuan, J.7
Zheng, M.8
Bai, H.9
Deng, H.10
Chen, K.11
Jenny, A.L.12
O'Rourke, K.13
Belay, E.D.14
Schonberger, L.B.15
Petersen, R.B.16
Sy, M.-S.17
Chen, S.G.18
Gambetti, P.19
-
64
-
-
0037447071
-
Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene
-
DOI 10.1073/pnas.2627989100
-
C Korth K Kaneko D Groth, et al. 2003 Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene Proc Natl Acad Sci USA 100 4784 4789 1:CAS:528:DC%2BD3sXjt12nsbw%3D 12684540 10.1073/pnas.2627989100 (Pubitemid 36457806)
-
(2003)
Proceedings of the National Academy of Sciences of the United States of America
, vol.100
, Issue.8
, pp. 4784-4789
-
-
Korth, C.1
Kaneko, K.2
Groth, D.3
Heye, N.4
Telling, G.5
Mastrianni, J.6
Parchi, P.7
Gambetti, P.8
Will, R.9
Ironside, J.10
Heinrich, C.11
Tremblay, P.12
DeArmond, S.J.13
Prusiner, S.B.14
-
66
-
-
20444474976
-
Structural insights into a yeast prion illuminate nucleation and strain diversity
-
DOI 10.1038/nature03679
-
R Krishnan SL Lindquist 2005 Structural insights into a yeast prion illuminate nucleation and strain diversity Nature 435 765 772 1:CAS:528:DC%2BD2MXkvVGgsLk%3D 15944694 10.1038/nature03679 (Pubitemid 40839721)
-
(2005)
Nature
, vol.435
, Issue.7043
, pp. 765-772
-
-
Krishnan, R.1
Lindquist, S.L.2
-
67
-
-
0035957401
-
Adaptation of the bovine spongiform encephalopathy agent to primates and comparison with Creutzfeldt-Jakob Disease: Implications for human health
-
DOI 10.1073/pnas.041490898
-
CI Lasmezas JG Fournier V Nouvel, et al. 2001 Adaptation of the bovine spongiform encephalopathy agent to primates and comparison with Creutzfeldt-Jakob disease: implications for human health Proc Natl Acad Sci USA 98 4142 4147 1:CAS:528:DC%2BD3MXis1KhtL0%3D 11259641 10.1073/pnas.041490898 (Pubitemid 32249912)
-
(2001)
Proceedings of the National Academy of Sciences of the United States of America
, vol.98
, Issue.7
, pp. 4142-4147
-
-
Lasmezas, C.I.1
Fournier, J.-G.2
Nouvel, V.3
Boe, H.4
Marce, D.5
Lamoury, F.6
Kopp, N.7
Hauw, J.-J.8
Ironside, J.9
Bruce, M.10
Dormont, D.11
Deslys, J.-P.12
-
68
-
-
0035863452
-
Increased susceptibility to kuru of carriers of the PRNP 129 methionine/methionine genotype
-
DOI 10.1086/317935
-
HS Lee P Brown L Cervenáková, et al. 2001 Increased susceptibility to kuru of carriers of the PRNP 129 methionine/methionine genotype J Infect Dis 183 192 196 1:CAS:528:DC%2BD3MXmsFGktA%3D%3D 11120925 10.1086/317935 (Pubitemid 32066018)
-
(2001)
Journal of Infectious Diseases
, vol.183
, Issue.2
, pp. 192-196
-
-
Lee, H.-S.1
Brown, P.2
Cervenakova, L.3
Garruto, R.M.4
Alpers, M.P.5
Gajdusek, D.C.6
Goldfarb, L.G.7
-
69
-
-
22044441644
-
Australian sporadic CJD analysis supports endogenous determinants of molecular-clinical profiles
-
DOI 10.1212/01.wnl.0000167188.65787.a0
-
V Lewis AF Hill GM Klug A Boyd CL Masters SJ Collins 2005 Australian sporadic CJD analysis supports endogenous determinants of molecular-clinical profiles Neurology 65 113 118 1:STN:280:DC%2BD2Mzls1ertQ%3D%3D 16009895 10.1212/01.wnl.0000167188.65787.a0 (Pubitemid 40967785)
-
(2005)
Neurology
, vol.65
, Issue.1
, pp. 113-118
-
-
Lewis, V.1
Hill, A.F.2
Klug, G.M.3
Boyd, A.4
Masters, C.L.5
Collins, S.J.6
-
70
-
-
76749109480
-
Darwinian evolution of prions in cell culture
-
1:CAS:528:DC%2BC3cXhslWis78%3D 20044542 10.1126/science.1183218
-
J Li S Browning SP Mahal AM Oelschlegel C Weissmann 2010 Darwinian evolution of prions in cell culture Science 327 869 872 1:CAS:528: DC%2BC3cXhslWis78%3D 20044542 10.1126/science.1183218
-
(2010)
Science
, vol.327
, pp. 869-872
-
-
Li, J.1
Browning, S.2
Mahal, S.P.3
Oelschlegel, A.M.4
Weissmann, C.5
-
71
-
-
1142273431
-
Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion
-
DOI 10.1016/S0140-6736(04)15486-X
-
CA Llewelyn PE Hewitt RS Knight, et al. 2004 Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion Lancet 363 417 421 1:STN:280:DC%2BD2c%2FnsVWhuw%3D%3D 14962520 10.1016/S0140-6736(04)15486-X (Pubitemid 38210057)
-
(2004)
Lancet
, vol.363
, Issue.9407
, pp. 417-421
-
-
Llewelyn, C.A.1
Hewitt, P.E.2
Knight, R.S.G.3
Amar, K.4
Cousens, S.5
MacKenzie, J.6
Will, R.G.7
-
72
-
-
15544390665
-
Genetic susceptibility to prion diseases in humans and mice
-
DOI 10.2174/1389202053202166
-
S Lloyd J Collinge 2005 Genetic susceptibility to prion diseases in humans and mice Current Genomics 6 1 11 1:CAS:528:DC%2BD2MXisVWgt7w%3D 10.2174/1389202053202166 (Pubitemid 40403363)
-
(2005)
Current Genomics
, vol.6
, Issue.1
, pp. 1-11
-
-
Lloyd, S.E.1
Collinge, J.2
-
73
-
-
0035932993
-
Identification of multiple quantitative trait loci linked to prion disease incubation period in mice
-
DOI 10.1073/pnas.101130398
-
S Lloyd ON Onwuazor J Beck, et al. 2001 Identification of multiple quantitative trait loci linked to prion disease incubation period in mice Proc Natl Acad Sci USA 98 6279 6283 1:CAS:528:DC%2BD3MXktVWksLk%3D 11353827 10.1073/pnas.101130398 (Pubitemid 32488230)
-
(2001)
Proceedings of the National Academy of Sciences of the United States of America
, vol.98
, Issue.11
, pp. 6279-6283
-
-
Lloyd, S.E.1
Onwuazor, O.N.2
Beck, J.A.3
Mallinson, G.4
Farrall, M.5
Targonski, P.6
Collinge, J.7
Fisher, E.M.C.8
-
74
-
-
61449198575
-
HECTD2 is associated with susceptibility to mouse and human prion disease
-
19214206 10.1371/journal.pgen.1000383 1:CAS:528:DC%2BD1MXisFygt7g%3D
-
SE Lloyd EG Maytham H Pota, et al. 2009 HECTD2 is associated with susceptibility to mouse and human prion disease PLoS Genet 5 e1000383 19214206 10.1371/journal.pgen.1000383 1:CAS:528:DC%2BD1MXisFygt7g%3D
-
(2009)
PLoS Genet
, vol.5
, pp. 1000383
-
-
Lloyd, S.E.1
Maytham, E.G.2
Pota, H.3
-
75
-
-
53249101908
-
Surgery and risk of sporadic Creutzfeldt-Jakob disease in Denmark and Sweden: Registry-based case-control studies
-
18843192 10.1159/000163097
-
I Mahillo-Fernandez J Pedro-Cuesta MJ Bleda, et al. 2008 Surgery and risk of sporadic Creutzfeldt-Jakob disease in Denmark and Sweden: registry-based case-control studies Neuroepidemiology 31 229 240 18843192 10.1159/000163097
-
(2008)
Neuroepidemiology
, vol.31
, pp. 229-240
-
-
Mahillo-Fernandez, I.1
Pedro-Cuesta, J.2
Bleda, M.J.3
-
76
-
-
77950558353
-
Live cell FRET predicts an altered molecular association of heterologous PrP-Sc with PrP-C
-
1:CAS:528:DC%2BC3cXjtFShtr8%3D 20086009 10.1074/jbc.M109.058107
-
S Mallik W Yang EM Norstrom JA Mastrianni 2010 Live cell FRET predicts an altered molecular association of heterologous PrP-Sc with PrP-C J Biol Chem 285 8967 8975 1:CAS:528:DC%2BC3cXjtFShtr8%3D 20086009 10.1074/jbc.M109.058107
-
(2010)
J Biol Chem
, vol.285
, pp. 8967-8975
-
-
Mallik, S.1
Yang, W.2
Norstrom, E.M.3
Mastrianni, J.A.4
-
77
-
-
33749248163
-
Inherited prion disease with six octapeptide repeat insertional mutation - Molecular analysis of phenotypic heterogeneity
-
DOI 10.1093/brain/awl226
-
S Mead M Poulter J Beck, et al. 2006 Inherited prion disease with six octapeptide repeat insertional mutation-molecular analysis of phenotypic heterogeneity Brain 129 2297 2317 16923955 10.1093/brain/awl226 (Pubitemid 44522116)
-
(2006)
Brain
, vol.129
, Issue.9
, pp. 2297-2317
-
-
Mead, S.1
Poulter, M.2
Beck, J.3
Webb, T.E.F.4
Campbell, T.A.5
Linehan, J.M.6
Desbruslais, M.7
Joiner, S.8
Wadsworth, J.D.F.9
King, A.10
Lantos, P.11
Collinge, J.12
-
78
-
-
34548137339
-
Inherited prion disease with 5-OPRI: Phenotype modification by repeat length and codon 129
-
DOI 10.1212/01.wnl.0000267642.41594.9d, PII 0000611420070821000005
-
S Mead TE Webb TA Campbell, et al. 2007 Inherited prion disease with 5-OPRI: phenotype modification by repeat length and codon 129 Neurology 69 730 738 1:CAS:528:DC%2BD2sXovFWju7g%3D 17709704 10.1212/01.wnl.0000267642.41594.9d (Pubitemid 47300929)
-
(2007)
Neurology
, vol.69
, Issue.8
, pp. 730-738
-
-
Mead, S.1
Webb, T.E.F.2
Campbell, T.A.3
Beck, J.4
Linehan, J.M.5
Rutherfoord, S.6
Joiner, S.7
Wadsworth, J.D.F.8
Heckmann, J.9
Wroe, S.10
Doey, L.11
King, A.12
Collinge, J.13
-
79
-
-
0242684410
-
Balancing selection at the prion protein gene consistent with prehistoric Kurulike epidemics
-
DOI 10.1126/science.1083320
-
S Mead MP Stumpf J Whitfield, et al. 2003 Balancing selection at the prion protein gene consistent with prehistoric kuru-like epidemics Science 300 640 643 1:CAS:528:DC%2BD3sXjtVymu7s%3D 12690204 10.1126/science.1083320 (Pubitemid 36520588)
-
(2003)
Science
, vol.300
, Issue.5619
, pp. 640-643
-
-
Mead, S.1
Stumpf, M.P.H.2
Whitfield, J.3
Beck, J.A.4
Poulter, M.5
Campbell, T.6
Uphill, J.B.7
Goldstein, D.8
Alpers, M.9
Fisher, E.M.C.10
Collinge, J.11
-
80
-
-
33645147707
-
Prion disease genetics
-
1:CAS:528:DC%2BD28Xhs1eqsbc%3D 16391566 10.1038/sj.ejhg.5201544
-
S Mead 2006 Prion disease genetics Eur J Hum Genet 14 273 281 1:CAS:528:DC%2BD28Xhs1eqsbc%3D 16391566 10.1038/sj.ejhg.5201544
-
(2006)
Eur J Hum Genet
, vol.14
, pp. 273-281
-
-
Mead, S.1
-
81
-
-
57249087392
-
Genetic risk factors for variant Creutzfeldt-Jakob disease: A genome-wide association study
-
19081515 10.1016/S1474-4422(08)70265-5
-
S Mead M Poulter J Uphill, et al. 2009 Genetic risk factors for variant Creutzfeldt-Jakob disease: a genome-wide association study Lancet Neurol 8 57 66 19081515 10.1016/S1474-4422(08)70265-5
-
(2009)
Lancet Neurol
, vol.8
, pp. 57-66
-
-
Mead, S.1
Poulter, M.2
Uphill, J.3
-
82
-
-
71549169557
-
Neurodegeneration. Could they all be prion diseases?
-
1:CAS:528:DC%2BD1MXhsFOhu7jK 19965731 10.1126/science.326.5958.1337
-
G Miller 2009 Neurodegeneration. Could they all be prion diseases? Science 326 1337 1339 1:CAS:528:DC%2BD1MXhsFOhu7jK 19965731 10.1126/science.326. 5958.1337
-
(2009)
Science
, vol.326
, pp. 1337-1339
-
-
Miller, G.1
-
83
-
-
22744448690
-
Immunodetection of disease-associated mutant PrP, which accelerates disease in GSS transgenic mice
-
DOI 10.1038/sj.emboj.7600717
-
KE Nazor F Kuhn T Seward, et al. 2005 Immunodetection of disease-associated mutant PrP, which accelerates disease in GSS transgenic mice EMBO J 24 2472 2480 1:CAS:528:DC%2BD2MXlvVWqtrg%3D 15962001 10.1038/sj.emboj. 7600717 (Pubitemid 41032597)
-
(2005)
EMBO Journal
, vol.24
, Issue.13
, pp. 2472-2480
-
-
Nazor, K.E.1
Kuhn, F.2
Seward, T.3
Green, M.4
Zwald, D.5
Purro, M.6
Schmid, J.7
Biffiger, K.8
Power, A.M.9
Oesch, B.10
Raeber, A.J.11
Telling, G.C.12
-
84
-
-
1942533390
-
Sc core generated by protease digestion: Implications for strain typing and molecular classification of CJD
-
DOI 10.1074/jbc.M313220200
-
S Notari S Capellari A Giese, et al. 2004 Effects of different experimental conditions on the PrPSc core generated by protease digestion: Implications for strain typing and molecular classification of CJD J Biol Chem 279 16797 16804 1:CAS:528:DC%2BD2cXjtVSjsr8%3D 14754888 10.1074/jbc.M313220200 (Pubitemid 38509382)
-
(2004)
Journal of Biological Chemistry
, vol.279
, Issue.16
, pp. 16797-16804
-
-
Notari, S.1
Capellari, S.2
Giese, A.3
Westner, I.4
Baruzzi, A.5
Ghetti, B.6
Gambetti, P.7
Kretzschmar, H.A.8
Parchi, P.9
-
85
-
-
69149088365
-
Is Parkinson's disease a prion disorder?
-
1:CAS:528:DC%2BD1MXhtVKrurnJ 19666621 10.1073/pnas.0906759106
-
CW Olanow SB Prusiner 2009 Is Parkinson's disease a prion disorder? Proc Natl Acad Sci USA 106 12571 12572 1:CAS:528:DC%2BD1MXhtVKrurnJ 19666621 10.1073/pnas.0906759106
-
(2009)
Proc Natl Acad Sci USA
, vol.106
, pp. 12571-12572
-
-
Olanow, C.W.1
Prusiner, S.B.2
-
86
-
-
0025820942
-
Homozygous prion protein genotype predisposes to sporadic Creutzfeldt-Jakob disease
-
1:CAS:528:DyaK3MXltFWrt7w%3D 1677164 10.1038/352340a0
-
MS Palmer AJ Dryden JT Hughes J Collinge 1991 Homozygous prion protein genotype predisposes to sporadic Creutzfeldt-Jakob disease Nature 352 340 342 1:CAS:528:DyaK3MXltFWrt7w%3D 1677164 10.1038/352340a0
-
(1991)
Nature
, vol.352
, pp. 340-342
-
-
Palmer, M.S.1
Dryden, A.J.2
Hughes, J.T.3
Collinge, J.4
-
87
-
-
0030953939
-
Typing prion isoforms [5]
-
DOI 10.1038/386232a0
-
P Parchi S Capellari SG Chen, et al. 1997 Typing prion isoforms Nature 386 232 233 1:CAS:528:DyaK2sXitVGktbc%3D 9069279 10.1038/386232a0 (Pubitemid 27142500)
-
(1997)
Nature
, vol.386
, Issue.6622
, pp. 232-234
-
-
Parchi, P.1
Capellari, S.2
Chen, S.G.3
Petersen, R.B.4
Gambetti, P.5
Kopp, N.6
Brown, P.7
Kitamoto, T.8
Tateishi, J.9
Giese, A.10
Kretzschmar, H.11
Collinge, J.12
Hill, A.F.13
Sidle, K.C.L.14
Ironside, J.15
-
88
-
-
8944259890
-
Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease
-
DOI 10.1002/ana.410390613
-
P Parchi R Castellani S Capellari, et al. 1996 Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease Ann Neurol 39 767 778 1:CAS:528:DyaK28Xkt1Omsb0%3D 8651649 10.1002/ana.410390613 (Pubitemid 26183813)
-
(1996)
Annals of Neurology
, vol.39
, Issue.6
, pp. 767-778
-
-
Parchi, P.1
Castellani, R.2
Capellari, S.3
Ghetti, B.4
Young, K.5
Chen, S.G.6
Farlow, M.7
Dickson, D.W.8
Sima, A.A.F.9
Trojanowski, J.Q.10
Petersen, R.B.11
Gambetti, P.12
-
89
-
-
0032493453
-
Different patterns of truncated prion protein fragments correlate with distinct phenotypes in P102L Gerstmann-Straussler-Scheinker disease
-
DOI 10.1073/pnas.95.14.8322
-
P Parchi SG Chen P Brown, et al. 1998 Different patterns of truncated prion protein fragments correlate with distinct phenotypes in P102L Gerstmann-Sträussler-Scheinker disease Proc Natl Acad Sci USA 95 8322 8327 1:CAS:528:DyaK1cXks1Sksbc%3D 9653185 10.1073/pnas.95.14.8322 (Pubitemid 28326111)
-
(1998)
Proceedings of the National Academy of Sciences of the United States of America
, vol.95
, Issue.14
, pp. 8322-8327
-
-
Parchi, P.1
Chen, S.G.2
Browns, P.3
Zou, W.4
Capellari, S.5
Budka, H.6
Hainfellner, J.7
Reyes, P.F.8
Golden, G.T.9
Hauw, J.J.10
Gajdusek, D.C.11
Gambetti, P.12
-
90
-
-
0032816292
-
Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects
-
DOI 10.1002/1531-8249(199908)46:2<224::AID-ANA12>3.0.CO;2-W
-
P Parchi A Giese S Capellari, et al. 1999 Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects Ann Neurol 46 224 233 1:STN:280:DyaK1MzntFCrug%3D%3D 10443888 10.1002/1531-8249(199908)46:2<224::AID-ANA12>3.0.CO;2-W (Pubitemid 29382879)
-
(1999)
Annals of Neurology
, vol.46
, Issue.2
, pp. 224-233
-
-
Parchi, P.1
Giese, A.2
Capellari, S.3
Brown, P.4
Schulz-Schaeffer, W.5
Windl, O.6
Zerr, I.7
Budka, H.8
Kopp, N.9
Piccardo, P.10
Poser, S.11
Rojiani, A.12
Streichemberger, N.13
Julien, J.14
Vital, C.15
Ghetti, B.16
Gambetti, P.17
Kretzschmar, H.18
-
91
-
-
66949127502
-
Inter-laboratory assessment of PrP(Sc) typing in Creutzfeldt-Jakob disease: A western blot study within the NeuroPrion consortium
-
18624793 10.1111/j.1750-3639.2008.00187.x 1:CAS:528:DC%2BD1MXos1Ojtrs%3D
-
P Parchi S Notari P Weber, et al. 2008 Inter-laboratory assessment of PrP(Sc) typing in Creutzfeldt-Jakob disease: a western blot study within the NeuroPrion consortium Brain Pathol 19 384 391 18624793 10.1111/j.1750-3639.2008. 00187.x 1:CAS:528:DC%2BD1MXos1Ojtrs%3D
-
(2008)
Brain Pathol
, vol.19
, pp. 384-391
-
-
Parchi, P.1
Notari, S.2
Weber, P.3
-
92
-
-
12944253111
-
Genetic influence on the structural variations of the abnormal prion protein
-
1:CAS:528:DC%2BD3cXmtlehtrg%3D 10963679 10.1073/pnas.97.18.10168
-
P Parchi WQ Zou W Wang, et al. 2000 Genetic influence on the structural variations of the abnormal prion protein Proc Natl Acad Sci USA 97 10168 10172 1:CAS:528:DC%2BD3cXmtlehtrg%3D 10963679 10.1073/pnas.97.18.10168
-
(2000)
Proc Natl Acad Sci USA
, vol.97
, pp. 10168-10172
-
-
Parchi, P.1
Zou, W.Q.2
Wang, W.3
-
93
-
-
4043157677
-
Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient
-
DOI 10.1016/S0140-6736(04)16811-6, PII S0140673604168116
-
AH Peden MW Head DL Ritchie JE Bell JW Ironside 2004 Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient Lancet 364 527 529 15302196 10.1016/S0140-6736(04)16811-6 (Pubitemid 39070413)
-
(2004)
Lancet
, vol.364
, Issue.9433
, pp. 527-529
-
-
Peden, A.H.1
Head, M.W.2
Ritchie, D.L.3
Bell, P.J.E.4
Ironside, P.J.W.5
-
94
-
-
33644651130
-
Sc in the skeletal muscle of patients with variant, iatrogenic, and sporadic forms of Creutzfeldt-Jakob disease
-
DOI 10.2353/ajpath.2006.050788
-
AH Peden DL Ritchie MW Head JW Ironside 2006 Detection and localization of PrPSc in the skeletal muscle of patients with variant, iatrogenic, and sporadic forms of Creutzfeldt-Jakob disease Am J Pathol 168 927 935 1:CAS:528:DC%2BD28XislGgur8%3D 16507908 10.2353/ajpath.2006.050788 (Pubitemid 43327745)
-
(2006)
American Journal of Pathology
, vol.168
, Issue.3
, pp. 927-935
-
-
Peden, A.H.1
Ritchie, D.L.2
Head, M.W.3
Ironside, J.W.4
-
95
-
-
78349283007
-
Nosocomial transmission of sporadic Creutzfeldt-Jakob disease: Results from a risk-based assessment of surgical interventions
-
(in press)
-
Pedro-Cuesta J, Mahillo-Fernandez I, Rabano A et al (2010) Nosocomial transmission of sporadic Creutzfeldt-Jakob disease: results from a risk-based assessment of surgical interventions. J Neurol Neurosurg Psychiatry (in press)
-
(2010)
J Neurol Neurosurg Psychiatry
-
-
Pedro-Cuesta, J.1
Mahillo-Fernandez, I.2
Rabano, A.3
-
96
-
-
0031754291
-
Phenotypic variability of Gerstmann-Straussler-Scheinker disease is associated with prion protein heterogeneity
-
1:STN:280:DyaK1M%2FgtVWrtQ%3D%3D 9786248 10.1097/00005072-199810000-00010
-
P Piccardo SR Dlouhy PMJ Lievens, et al. 1998 Phenotypic variability of Gerstmann-Straussler-Scheinker disease is associated with prion protein heterogeneity J Neuropathol Exp Neurol 57 979 988 1:STN:280: DyaK1M%2FgtVWrtQ%3D%3D 9786248 10.1097/00005072-199810000-00010
-
(1998)
J Neuropathol Exp Neurol
, vol.57
, pp. 979-988
-
-
Piccardo, P.1
Dlouhy, S.R.2
Lievens, P.M.J.3
-
97
-
-
0034974318
-
Prion proteins with different conformations accumulate in Gerstmann-Straussler-Scheinker disease caused by A117V and F198S mutations
-
1:CAS:528:DC%2BD3MXkvFyktrw%3D 11395398
-
P Piccardo JJ Liepnieks A William, et al. 2001 Prion proteins with different conformations accumulate in Gerstmann-Straussler-Scheinker disease caused by A117V and F198S mutations Am J Pathol 158 2201 2207 1:CAS:528:DC%2BD3MXkvFyktrw%3D 11395398
-
(2001)
Am J Pathol
, vol.158
, pp. 2201-2207
-
-
Piccardo, P.1
Liepnieks, J.J.2
William, A.3
-
98
-
-
27744459883
-
Sc types in individuals with Creutzfeldt-Jakob disease
-
DOI 10.1016/S1474-4422(05)70225-8, PII S1474442205702258
-
M Polymenidou K Stoeck M Glatzel M Vey A Bellon A Aguzzi 2005 Coexistence of multiple PrP(Sc) types in individuals with Creutzfeldt-Jakob disease Lancet Neurol 4 805 814 1:CAS:528:DC%2BD2MXhtlWmtrjI 16297838 10.1016/S1474-4422(05) 70225-8 (Pubitemid 41619435)
-
(2005)
Lancet Neurology
, vol.4
, Issue.12
, pp. 805-814
-
-
Polymenidou, M.1
Stoeck, K.2
Glatzel, M.3
Vey, M.4
Bellon, A.5
Aguzzi, A.6
-
99
-
-
0020321767
-
Novel proteinaceous infectious particles cause scrapie
-
1:CAS:528:DyaL38XhsFyqtro%3D 6801762 10.1126/science.6801762
-
SB Prusiner 1982 Novel proteinaceous infectious particles cause scrapie Science 216 136 144 1:CAS:528:DyaL38XhsFyqtro%3D 6801762 10.1126/science.6801762
-
(1982)
Science
, vol.216
, pp. 136-144
-
-
Prusiner, S.B.1
-
102
-
-
0141515202
-
Sc
-
DOI 10.1093/bmb/66.1.21
-
D Riesner 2003 Biochemistry and structure of PrP(C) and PrP(Sc) Br Med Bull 66 21 33 1:CAS:528:DC%2BD3sXnvVeqtr4%3D 14522846 10.1093/bmb/66.1.21 (Pubitemid 37173489)
-
(2003)
British Medical Bulletin
, vol.66
, pp. 21-33
-
-
Riesner, D.1
-
103
-
-
0031720905
-
Eight prion strains have PrP(Sc) molecules with different conformations
-
DOI 10.1038/2654
-
Sc molecules with different conformations Nat Med 4 1157 1165 1:CAS:528:DyaK1cXms1Ggt74%3D 9771749 10.1038/2654 (Pubitemid 28468829)
-
(1998)
Nature Medicine
, vol.4
, Issue.10
, pp. 1157-1165
-
-
Safar, J.1
Wille, H.2
Itri, V.3
Groth, D.4
Serban, H.5
Torchia, M.6
Cohen, F.E.7
Prusiner, S.B.8
-
104
-
-
20044383009
-
Diagnosis of human prion disease
-
DOI 10.1073/pnas.0409651102
-
JG Safar MD Geschwind C Deering, et al. 2005 Diagnosis of human prion disease Proc Natl Acad Sci USA 102 3501 3506 1:CAS:528:DC%2BD2MXitl2ksrs%3D 15741275 10.1073/pnas.0409651102 (Pubitemid 40328074)
-
(2005)
Proceedings of the National Academy of Sciences of the United States of America
, vol.102
, Issue.9
, pp. 3501-3506
-
-
Safar, J.G.1
Geschwind, M.D.2
Deering, C.3
Didorenko, S.4
Sattavat, M.5
Sanchez, H.6
Serban, A.7
Vey, M.8
Baron, H.9
Giles, K.10
Miller, B.L.11
DeArmond, S.J.12
Prusiner, S.B.13
-
105
-
-
33644845779
-
Analysis of prion strains by PrP(Sc) profiling in sporadic Creutzfeldt-Jakob disease
-
16354106 10.1371/journal.pmed.0030014 1:CAS:528:DC%2BD28XitlKiu74%3D
-
G Schoch H Seeger J Bogousslavsky, et al. 2005 Analysis of prion strains by PrP(Sc) profiling in sporadic Creutzfeldt-Jakob disease PLoS Med 3 e14 16354106 10.1371/journal.pmed.0030014 1:CAS:528:DC%2BD28XitlKiu74%3D
-
(2005)
PLoS Med
, vol.3
, pp. 14
-
-
Schoch, G.1
Seeger, H.2
Bogousslavsky, J.3
-
106
-
-
19544363062
-
Prions as adaptive conduits of memory and inheritance
-
DOI 10.1038/nrg1616
-
J Shorter S Lindquist 2005 Prions as adaptive conduits of memory and inheritance Nat Rev Genet 6 435 450 1:CAS:528:DC%2BD2MXkslSnu7s%3D 15931169 10.1038/nrg1616 (Pubitemid 40733889)
-
(2005)
Nature Reviews Genetics
, vol.6
, Issue.6
, pp. 435-450
-
-
Shorter, J.1
Lindquist, S.2
-
107
-
-
24644448839
-
The most infectious prion protein particles
-
DOI 10.1038/nature03989
-
JR Silveira GJ Raymond AG Hughson, et al. 2005 The most infectious prion protein particles Nature 437 257 261 1:CAS:528:DC%2BD2MXpsleku74%3D 16148934 10.1038/nature03989 (Pubitemid 41294488)
-
(2005)
Nature
, vol.437
, Issue.7056
, pp. 257-261
-
-
Silveira, J.R.1
Raymond, G.J.2
Hughson, A.G.3
Race, R.E.4
Sim, V.L.5
Hayes, S.F.6
Caughey, B.7
-
108
-
-
0030902421
-
Identification of the prion protein allotypes which accumulate in the brain of sporadic and familial Creutzfeldt-Jakob disease patients
-
1:CAS:528:DyaK2sXivFOms7w%3D 9142120 10.1038/nm0597-521
-
MC Silvestrini F Cardone B Maras, et al. 1997 Identification of the prion protein allotypes which accumulate in the brain of sporadic and familial Creutzfeldt-Jakob disease patients Nat Med 3 521 525 1:CAS:528: DyaK2sXivFOms7w%3D 9142120 10.1038/nm0597-521
-
(1997)
Nat Med
, vol.3
, pp. 521-525
-
-
Silvestrini, M.C.1
Cardone, F.2
Maras, B.3
-
109
-
-
0034306805
-
Quantitative trait loci affecting prion incubation time in mice
-
1:CAS:528:DC%2BD3cXmvFWlurw%3D 11013074 10.1006/geno.2000.6320
-
DA Stephenson K Chiotti C Ebeling, et al. 2000 Quantitative trait loci affecting prion incubation time in mice Genomics 69 47 53 1:CAS:528: DC%2BD3cXmvFWlurw%3D 11013074 10.1006/geno.2000.6320
-
(2000)
Genomics
, vol.69
, pp. 47-53
-
-
Stephenson, D.A.1
Chiotti, K.2
Ebeling, C.3
-
110
-
-
0035937094
-
A 7-kDa prion protein (PrP) fragment, an integral component of the PrP region required for infectivity, is the major amyloid protein in Gerstmann-Straussler-Scheinker disease A117V
-
1:CAS:528:DC%2BD3MXhs1Kmuro%3D 11087738 10.1074/jbc.M007062200
-
F Tagliavini PMJ Lievens C Tranchant, et al. 2001 A 7-kDa prion protein (PrP) fragment, an integral component of the PrP region required for infectivity, is the major amyloid protein in Gerstmann-Straussler-Scheinker disease A117V J Biol Chem 276 6009 6015 1:CAS:528:DC%2BD3MXhs1Kmuro%3D 11087738 10.1074/jbc.M007062200
-
(2001)
J Biol Chem
, vol.276
, pp. 6009-6015
-
-
Tagliavini, F.1
Lievens, P.M.J.2
Tranchant, C.3
-
111
-
-
1642633056
-
Conformational variations in an infectious protein determine prion strain differences
-
DOI 10.1038/nature02392
-
M Tanaka P Chien N Naber R Cooke JS Weissman 2004 Conformational variations in an infectious protein determine prion strain differences Nature 428 323 328 1:CAS:528:DC%2BD2cXitFCnurs%3D 15029196 10.1038/nature02392 (Pubitemid 38418803)
-
(2004)
Nature
, vol.428
, Issue.6980
, pp. 323-328
-
-
Tanaka, M.1
Chien, P.2
Naber, N.3
Cooke, R.4
Weissman, J.S.5
-
112
-
-
17044435107
-
Mechanism of cross-species prion transmission an infectious conformation compatible with two highly divergent yeast prion proteins
-
1:CAS:528:DC%2BD2MXjsVaks7k%3D 15820678 10.1016/j.cell.2005.03.008
-
M Tanaka P Chien K Yonekura JS Weissman 2005 Mechanism of cross-species prion transmission an infectious conformation compatible with two highly divergent yeast prion proteins Cell 121 49 62 1:CAS:528:DC%2BD2MXjsVaks7k%3D 15820678 10.1016/j.cell.2005.03.008
-
(2005)
Cell
, vol.121
, pp. 49-62
-
-
Tanaka, M.1
Chien, P.2
Yonekura, K.3
Weissman, J.S.4
-
113
-
-
12644272790
-
Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity
-
DOI 10.1126/science.274.5295.2079
-
GC Telling P Parchi SJ DeArmond, et al. 1996 Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity Science 274 2079 2082 1:CAS:528:DyaK2sXjtFeq 8953038 10.1126/science.274.5295.2079 (Pubitemid 27020700)
-
(1996)
Science
, vol.274
, Issue.5295
, pp. 2079-2082
-
-
Telling, G.C.1
Parchi, P.2
DeArmond, S.J.3
Cortelli, P.4
Montagna, P.5
Gabizon, R.6
Mastrianni, J.7
Lugaresi, E.8
Gambetti, P.9
Prusiner, S.B.10
-
114
-
-
0028882424
-
Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein
-
1:CAS:528:DyaK2MXosF2ku7g%3D 7553876 10.1016/0092-8674(95)90236-8
-
GC Telling M Scott J Mastrianni, et al. 1995 Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein Cell 83 79 90 1:CAS:528:DyaK2MXosF2ku7g%3D 7553876 10.1016/0092-8674(95)90236-8
-
(1995)
Cell
, vol.83
, pp. 79-90
-
-
Telling, G.C.1
Scott, M.2
Mastrianni, J.3
-
115
-
-
33846490771
-
Proteinase K-sensitive disease-associated ovine prion protein revealed by conformation-dependent immunoassay
-
DOI 10.1042/BJ20061264
-
AM Thackray L Hopkins R Bujdoso 2007 Proteinase K-sensitive disease-associated ovine prion protein revealed by conformation-dependent immunoassay Biochem J 401 475 483 1:CAS:528:DC%2BD2sXhtVahtQ%3D%3D 17018021 10.1042/BJ20061264 (Pubitemid 46166430)
-
(2007)
Biochemical Journal
, vol.401
, Issue.2
, pp. 475-483
-
-
Thackray, A.M.1
Hopkins, L.2
Bujdoso, R.3
-
116
-
-
0842304471
-
Sc Conformers Induced by a Synthetic Peptide and Several Prion Strains
-
DOI 10.1128/JVI.78.4.2088-2099.2004
-
P Tremblay HL Ball K Kaneko, et al. 2004 Mutant PrP(Sc) conformers induced by a synthetic peptide and several prion strains J Virol 78 2088 2099 1:CAS:528:DC%2BD2cXhtFKnsLo%3D 14747574 10.1128/JVI.78.4.2088-2099.2004 (Pubitemid 38176741)
-
(2004)
Journal of Virology
, vol.78
, Issue.4
, pp. 2088-2099
-
-
Tremblay, P.1
Ball, H.L.2
Kaneko, K.3
Groth, D.4
Hegde, R.S.5
Cohen, F.E.6
DeArmond, S.J.7
Prusiner, S.B.8
Safar, J.G.9
-
117
-
-
0037159185
-
Protease-sensitive scrapie prion protein in aggregates of heterogeneous sizes
-
DOI 10.1021/bi025958g
-
S Tzaban G Friedlander O Schonberger, et al. 2002 Protease-sensitive scrapie prion protein in aggregates of heterogeneous sizes Biochemistry 41 12868 12875 1:CAS:528:DC%2BD38Xntlaisbg%3D 12379130 10.1021/bi025958g (Pubitemid 35192516)
-
(2002)
Biochemistry
, vol.41
, Issue.42
, pp. 12868-12875
-
-
Tzaban, S.1
Friedlander, G.2
Schonberger, O.3
Horonchik, L.4
Yedidia, Y.5
Shaked, G.6
Gabizon, R.7
Taraboulos, A.8
-
118
-
-
42949128703
-
res type 1/type 2 dichotomy in Creutzfeldt-Jakob disease
-
DOI 10.1371/journal.ppat.1000029
-
E Uro-Coste H Cassard S Simon, et al. 2008 Beyond PrP type 1/type 2 dichotomy in Creutzfeldt-Jakob disease PLoS Pathog 4 e1000029 10.1371/journal.ppat.1000029 1:CAS:528:DC%2BD1cXksFelsbc%3D (Pubitemid 351631097)
-
(2008)
PLoS Pathogens
, vol.4
, Issue.3
-
-
Uro-Coste, E.1
Cassard, H.2
Simon, S.3
Lugan, S.4
Bilheude, J.-M.5
Perret-Liaudet, A.6
Ironside, J.W.7
Haik, S.8
Basset-Leobon, C.9
Lacroux, C.10
Peoch, K.11
Streichenberger, N.12
Langeveld, J.13
Head, M.W.14
Grassi, J.15
Hauw, J.-J.16
Schelcher, F.17
Delisle, M.B.18
Andreoletti, O.19
-
119
-
-
10044224475
-
Human prion protein with valine 129 prevents expression of variant CJD phenotype
-
DOI 10.1126/science.1103932
-
JD Wadsworth EA Asante M Desbruslais, et al. 2004 Human prion protein with valine 129 prevents expression of variant CJD phenotype Science 306 1793 1796 1:CAS:528:DC%2BD2cXhtVKitb%2FN 15539564 10.1126/science.1103932 (Pubitemid 39601400)
-
(2004)
Science
, vol.306
, Issue.5702
, pp. 1793-1796
-
-
Wadsworth, J.D.F.1
Asante, E.A.2
Desbruslais, M.3
Linehan, J.M.4
Joiner, S.5
Gowland, I.6
Welch, J.7
Stone, L.8
Lloyd, S.E.9
Hill, A.F.10
Brandner, S.11
Collinge, J.12
-
120
-
-
34249984739
-
Update on human prion disease
-
1:CAS:528:DC%2BD2sXmtlWjurw%3D 17408929
-
JD Wadsworth J Collinge 2007 Update on human prion disease Biochim Biophys Acta 1772 598 609 1:CAS:528:DC%2BD2sXmtlWjurw%3D 17408929
-
(2007)
Biochim Biophys Acta
, vol.1772
, pp. 598-609
-
-
Wadsworth, J.D.1
Collinge, J.2
-
121
-
-
0141849458
-
Molecular and clinical classification of human prion disease
-
DOI 10.1093/bmb/66.1.241
-
JD Wadsworth AF Hill JA Beck J Collinge 2003 Molecular and clinical classification of human prion disease Br Med Bull 66 241 254 1:CAS:528:DC%2BD3sXnvVeqtrY%3D 14522862 10.1093/bmb/66.1.241 (Pubitemid 37173505)
-
(2003)
British Medical Bulletin
, vol.66
, pp. 241-254
-
-
Wadsworth, J.D.F.1
Hill, A.F.2
Beck, J.A.3
Collinge, J.4
-
122
-
-
0033130083
-
Strain-specific prion-protein conformation determined by metal ions
-
1:CAS:528:DyaK1MXksVKitrg%3D 10559865 10.1038/9030
-
JD Wadsworth AF Hill S Joiner GS Jackson A Clarke J Collinge 1999 Strain-specific prion-protein conformation determined by metal ions Nat Cell Biol 1 55 59 1:CAS:528:DyaK1MXksVKitrg%3D 10559865 10.1038/9030
-
(1999)
Nat Cell Biol
, vol.1
, pp. 55-59
-
-
Wadsworth, J.D.1
Hill, A.F.2
Joiner, S.3
Jackson, G.S.4
Clarke, A.5
Collinge, J.6
-
123
-
-
33845979521
-
Prion infectivity in variant Creutzfeldt-Jakob disease rectum
-
DOI 10.1136/gut.2006.091637
-
JD Wadsworth S Joiner K Fox, et al. 2007 Prion infectivity in variant Creutzfeldt-Jakob disease rectum Gut 56 90 94 1:CAS:528:DC%2BD2sXhtF2qsLk%3D 16763054 10.1136/gut.2006.091637 (Pubitemid 46044893)
-
(2007)
Gut
, vol.56
, Issue.1
, pp. 90-94
-
-
Wadsworth, J.D.F.1
Joiner, S.2
Fox, K.3
Linehan, J.M.4
Desbruslais, M.5
Brandner, S.6
Asante, E.A.7
Collinge, J.8
-
124
-
-
0035928432
-
Tissue distribution of protease resistant prion protein in variant Creutzfeldt-Jakob disease using a highly sensitive immunoblotting assay
-
DOI 10.1016/S0140-6736(01)05403-4
-
JD Wadsworth S Joiner AF Hill, et al. 2001 Tissue distribution of protease resistant prion protein in variant CJD using a highly sensitive immuno-blotting assay Lancet 358 171 180 1:CAS:528:DC%2BD3MXltlymsr4%3D 11476832 10.1016/S0140-6736(01)05403-4 (Pubitemid 32718539)
-
(2001)
Lancet
, vol.358
, Issue.9277
, pp. 171-180
-
-
Wadsworth, J.D.F.1
Joiner, S.2
Hill, A.F.3
Campbell, T.A.4
Desbruslais, M.5
Luthert, P.J.6
Collinge, J.7
-
125
-
-
33745094097
-
Phenotypic heterogeneity in inherited prion disease (P102L) is associated with differential propagation of protease-resistant wild-type and mutant prion protein
-
DOI 10.1093/brain/awl076
-
JD Wadsworth S Joiner J Linehan, et al. 2006 Phenotypic heterogeneity in inherited prion disease (P102L) is associated with differential propagation of protease-resistant wild-type and mutant prion protein Brain 129 1557 1569 16597650 10.1093/brain/awl076 (Pubitemid 43999387)
-
(2006)
Brain
, vol.129
, Issue.6
, pp. 1557-1569
-
-
Wadsworth, J.D.F.1
Joiner, S.2
Linehan, J.M.3
Cooper, S.4
Powell, C.5
Mallinson, G.6
Buckell, J.7
Gowland, I.8
Asante, E.A.9
Budka, H.10
Brandner, S.11
Collinge, J.12
-
126
-
-
53749088994
-
Review. The origin of the prion agent of kuru: Molecular and biological strain typing
-
1:CAS:528:DC%2BD1cXhsVGgt7jJ 18849291 10.1098/rstb.2008.0069
-
JD Wadsworth S Joiner JM Linehan EA Asante S Brandner J Collinge 2008 Review. The origin of the prion agent of kuru: molecular and biological strain typing Philos Trans R Soc Lond B Biol Sci 363 3747 3753 1:CAS:528: DC%2BD1cXhsVGgt7jJ 18849291 10.1098/rstb.2008.0069
-
(2008)
Philos Trans R Soc Lond B Biol Sci
, vol.363
, pp. 3747-3753
-
-
Wadsworth, J.D.1
Joiner, S.2
Linehan, J.M.3
Asante, E.A.4
Brandner, S.5
Collinge, J.6
-
127
-
-
41649086573
-
Kuru prions and sporadic Creutzfeldt-Jakob disease prions have equivalent transmission properties in transgenic and wild-type mice
-
DOI 10.1073/pnas.0800190105
-
JD Wadsworth S Joiner JM Linehan, et al. 2008 Kuru prions and sporadic Creutzfeldt-Jakob disease prions have equivalent transmission properties in transgenic and wild-type mice Proc Natl Acad Sci USA 105 3885 3890 1:CAS:528:DC%2BD1cXjs1Ohs7w%3D 18316717 10.1073/pnas.0800190105 (Pubitemid 351723494)
-
(2008)
Proceedings of the National Academy of Sciences of the United States of America
, vol.105
, Issue.10
, pp. 3885-3890
-
-
Wadsworth, J.D.F.1
Joiner, S.2
Linehan, J.M.3
Desbruslais, M.4
Fox, K.5
Cooper, S.6
Cronier, S.7
Asante, E.A.8
Mead, S.9
Brandner, S.10
Hill, A.F.11
Collinge, J.12
-
128
-
-
84934437264
-
Molecular diagnosis of human prion disease
-
1:CAS:528:DC%2BD1cXosVSqtLg%3D 18576157 10.1007/978-1-59745-234-2-14
-
JD Wadsworth C Powell JA Beck, et al. 2008 Molecular diagnosis of human prion disease Methods Mol Biol 459 197 227 1:CAS:528:DC%2BD1cXosVSqtLg%3D 18576157 10.1007/978-1-59745-234-2-14
-
(2008)
Methods Mol Biol
, vol.459
, pp. 197-227
-
-
Wadsworth, J.D.1
Powell, C.2
Beck, J.A.3
-
129
-
-
9444267651
-
The state of the prion
-
DOI 10.1038/nrmicro1025
-
C Weissmann 2004 The state of the prion Nat Rev Microbiol 2 861 871 1:CAS:528:DC%2BD2cXos1Kqu78%3D 15494743 10.1038/nrmicro1025 (Pubitemid 39561804)
-
(2004)
Nature Reviews Microbiology
, vol.2
, Issue.11
, pp. 861-871
-
-
Weissmann, C.1
-
130
-
-
73549086979
-
Similarities between forms of sheep scrapie and Creutzfeldt-Jakob disease are encoded by distinct prion types
-
1:CAS:528:DC%2BC3cXkt12kuw%3D%3D 19850886 10.2353/ajpath.2009.090623
-
WM Wemheuer SL Benestad A Wrede, et al. 2009 Similarities between forms of sheep scrapie and Creutzfeldt-Jakob disease are encoded by distinct prion types Am J Pathol 175 2566 2573 1:CAS:528:DC%2BC3cXkt12kuw%3D%3D 19850886 10.2353/ajpath.2009.090623
-
(2009)
Am J Pathol
, vol.175
, pp. 2566-2573
-
-
Wemheuer, W.M.1
Benestad, S.L.2
Wrede, A.3
-
132
-
-
34447530804
-
Prions of fungi: Inherited structures and biological roles
-
DOI 10.1038/nrmicro1708, PII NRMICRO1708
-
RB Wickner HK Edskes F Shewmaker T Nakayashiki 2007 Prions of fungi: inherited structures and biological roles Nat Rev Microbiol 5 611 618 1:CAS:528:DC%2BD2sXns12hurw%3D 17632572 10.1038/nrmicro1708 (Pubitemid 47074116)
-
(2007)
Nature Reviews Microbiology
, vol.5
, Issue.8
, pp. 611-618
-
-
Wickner, R.B.1
Edskes, H.K.2
Shewmaker, F.3
Nakayashiki, T.4
-
133
-
-
0141849457
-
Acquired prion disease: Iatrogenic CJD, variant CJD, kuru
-
DOI 10.1093/bmb/66.1.255
-
RG Will 2003 Acquired prion disease: iatrogenic CJD, variant CJD, kuru Br Med Bull 66 255 265 1:CAS:528:DC%2BD3sXnvVeqtrc%3D 14522863 10.1093/bmb/66.1.255 (Pubitemid 37173506)
-
(2003)
British Medical Bulletin
, vol.66
, pp. 255-265
-
-
Will, R.G.1
-
134
-
-
0342951746
-
A new variant of Creutzfeldt-Jakob disease in the UK
-
1:STN:280:DyaK287nvVKruw%3D%3D 8598754 10.1016/S0140-6736(96)91412-9
-
RG Will JW Ironside M Zeidler, et al. 1996 A new variant of Creutzfeldt-Jakob disease in the UK Lancet 347 921 925 1:STN:280: DyaK287nvVKruw%3D%3D 8598754 10.1016/S0140-6736(96)91412-9
-
(1996)
Lancet
, vol.347
, pp. 921-925
-
-
Will, R.G.1
Ironside, J.W.2
Zeidler, M.3
-
135
-
-
2442735162
-
Genetic basis of Creutzfeldt-Jakob disease in the United Kingdom: A systematic analysis of predisposing mutations and allelic variation in the PRNP gene
-
DOI 10.1007/s004390050204
-
O Windl M Dempster JP Estibeiro, et al. 1996 Genetic basis of Creutzfeldt-Jakob disease in the United Kingdom: a systematic analysis of predisposing mutations and allelic variation in the PRNP gene Hum Genet 98 259 264 1:CAS:528:DyaK28Xls1Chu7w%3D 8707291 10.1007/s004390050204 (Pubitemid 26258371)
-
(1996)
Human Genetics
, vol.98
, Issue.3
, pp. 259-264
-
-
Windl, O.1
Dempster, M.2
Estibeiro, J.P.3
Lathe, R.4
De Silva, R.5
Esmonde, T.6
Will, R.7
Springbett, A.8
Campbell, T.A.9
Sidle, K.C.L.10
Palmer, M.S.11
Collinge, J.12
-
136
-
-
33845227845
-
Clinical presentation and pre-mortem diagnosis of variant Creutzfeldt-Jakob disease associated with blood transfusion: A case report
-
DOI 10.1016/S0140-6736(06)69835-8, PII S0140673606698358
-
SJ Wroe S Pal D Siddique, et al. 2006 Clinical presentation and pre-mortem diagnosis of variant Creutzfeldt-Jakob disease associated with blood transfusion: a case report Lancet 368 2061 2067 17161728 10.1016/S0140-6736(06) 69835-8 (Pubitemid 44855106)
-
(2006)
Lancet
, vol.368
, Issue.9552
, pp. 2061-2067
-
-
Wroe, S.J.1
Pal, S.2
Siddique, D.3
Hyare, H.4
Macfarlane, R.5
Joiner, S.6
Linehan, J.M.7
Brandner, S.8
Wadsworth, J.D.9
Hewitt, P.10
Collinge, J.11
-
137
-
-
30344438495
-
Detection of type 1 prion protein in variant Creutzfeldt-Jakob disease
-
DOI 10.2353/ajpath.2006.050766
-
HM Yull DL Ritchie JP Langeveld, et al. 2006 Detection of type 1 prion protein in variant Creutzfeldt-Jakob disease Am J Pathol 168 151 157 1:CAS:528:DC%2BD28XhtVKksb0%3D 16400018 10.2353/ajpath.2006.050766 (Pubitemid 43062568)
-
(2006)
American Journal of Pathology
, vol.168
, Issue.1
, pp. 151-157
-
-
Yull, H.M.1
Ritchie, D.L.2
Langeveld, J.P.M.3
Van Zijderveld, F.G.4
Bruce, M.E.5
Ironside, J.W.6
Head, M.W.7
-
138
-
-
0035798669
-
PH-dependent prion protein conformation in classical Creutzfeldt-Jakob disease
-
1:CAS:528:DC%2BD3MXosVKhsbY%3D 11682490 10.1074/jbc.C100458200
-
G Zanusso A Farinazzo M Fiorini, et al. 2001 pH-dependent prion protein conformation in classical Creutzfeldt-Jakob disease J Biol Chem 276 40377 40380 1:CAS:528:DC%2BD3MXosVKhsbY%3D 11682490 10.1074/jbc.C100458200
-
(2001)
J Biol Chem
, vol.276
, pp. 40377-40380
-
-
Zanusso, G.1
Farinazzo, A.2
Fiorini, M.3
-
139
-
-
4644259154
-
Identification of distinct N-terminal truncated forms of prion protein in different Creutzfeldt-Jakob disease subtypes
-
DOI 10.1074/jbc.M405468200
-
G Zanusso A Farinazzo F Prelli, et al. 2004 Identification of distinct N-terminal truncated forms of prion protein in different Creutzfeldt-Jakob disease subtypes J Biol Chem 279 38936 38942 1:CAS:528:DC%2BD2cXnt1yjsL0%3D 15247220 10.1074/jbc.M405468200 (Pubitemid 39296054)
-
(2004)
Journal of Biological Chemistry
, vol.279
, Issue.37
, pp. 38936-38942
-
-
Zanusso, G.1
Farinazzo, A.2
Prelli, F.3
Fiorini, M.4
Gelati, M.5
Ferrari, S.6
Righetti, P.G.7
Rizzuto, N.8
Frangiones, B.9
Monaco, S.10
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