A general introduction to the biochemistry of mitochondrial fatty acid β-oxidation

Journal of Inherited Metabolic Disease

Volumn 33, Issue 5, 2010, Pages 469-477

  Houten, Sander Michel ^a   Wanders, Ronald J A ^a  

^a UNIVERSITY OF AMSTERDAM   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

BUTYRYL COENZYME A DEHYDROGENASE; CARNITINE PALMITOYLTRANSFERASE; FATTY ACID TRANSPORTER; LONG CHAIN ACYL COENZYME A DEHYDROGENASE; MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE;

CELL MEMBRANE TRANSPORT; CONGESTIVE CARDIOMYOPATHY; ENERGY METABOLISM; FATTY ACID OXIDATION; GLUCONEOGENESIS; HEART ARRHYTHMIA; HUMAN; HYPERTROPHIC CARDIOMYOPATHY; HYPOGLYCEMIA; HYPOKETOTIC HYPOGLYCEMIA; MITOCHONDRIAL MEMBRANE; NEWBORN SCREENING; NONHUMAN; PATHOPHYSIOLOGY; REVIEW; RHABDOMYOLYSIS; TRANSCRIPTION REGULATION;

ANIMALS; DISEASE MODELS, ANIMAL; ENERGY METABOLISM; FATTY ACIDS; GENOTYPE; HOMEOSTASIS; HUMANS; LIPID METABOLISM, INBORN ERRORS; MICE; MITOCHONDRIA; MITOCHONDRIAL DISEASES; OXIDATION-REDUCTION; PHENOTYPE;

EID: 77957608608     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-010-9061-2     Document Type: Review

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