Gestational, pathologic and biochemical differences between very long-chain acyl-CoA dehydrogenase deficiency and long-chain acyl-CoA dehydrogenase deficiency in the mouse

Human Molecular Genetics

Volumn 10, Issue 19, 2001, Pages 2069-2077

  Cox, Keith B ^a   Hamm, Doug A ^a   Millington, David S ^b   Matern, Dietrich ^c   Vockley, Jerry ^c   Rinaldo, Piero ^c   Pinkert, Carl A ^a   Rhead, William J ^d   Lindsey, J Russell ^a   Wood, Philip A ^a  

^a UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

^b DUKE UNIVERSITY   (United States)

^c MAYO CLINIC   (United States)

^d UNIVERSITY OF IOWA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

2,6 DIMETHYLHEPTANOYL COENZYME A; ACYL COENZYME A; ACYL COENZYME A DEHYDROGENASE; BRANCHED CHAIN AMINO ACID; LONG CHAIN FATTY ACID; OLEOYL COENZYME A; PALMITOYL COENZYME A; UNCLASSIFIED DRUG; VERY LONG CHAIN FATTY ACID;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BIOCHEMISTRY; CHEMICAL MODIFICATION; CONTROLLED STUDY; DEHYDROGENATION; DIET RESTRICTION; DISEASE SEVERITY; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME SUBSTRATE; FATTY ACID OXIDATION; GENE MUTATION; GENOTYPE; HEART; HETEROZYGOSITY; LIPID BILE LEVEL; LIPID BLOOD LEVEL; LIVER; LIVER FATTY DEGENERATION; LONG CHAIN FATTY ACID COENZYME A DEHYDROGENASE DEFICIENCY; METABOLIC DISORDER; MITOCHONDRION; MOUSE; NONHUMAN; PATHOGENESIS; PATHOLOGY; PHENOTYPE; PREGNANCY; PRIORITY JOURNAL; PROGENY; SKELETAL MUSCLE; VERY LONG CHAIN FATTY ACID COENZYME A DEHYDROGENASE DEFICIENCY;

ANIMALIA;

EID: 0034782503     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/10.19.2069     Document Type: Article

References (33)

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