2,6-Dimethylheptanoyl-CoA is a specific substrate for long-chain acyl-CoA dehydrogenase (LCAD): Evidence for a major role of LCAD in branched-chain fatty acid oxidation

Biochimica et Biophysica Acta - Lipids and Lipid Metabolism

Volumn 1393, Issue 1, 1998, Pages 35-40

  Wanders, Ronald J a ^a   Denis, Simone ^a   Ruiter, Jos P n ^a   Ijlst, Lodewijk ^a   Dacremont, Georges ^b  

^a EMMA CHILDREN S HOSPITAL   (Netherlands)

^b GHENT UNIVERSITY   (Belgium)

Author keywords

Fatty acid; Inherited disease; Mitochondrial fatty acid oxidation; Oxidation

Indexed keywords

2,6 DIMETHYLHEPTANOYL COENZYME A; ACYL COENZYME A; ACYL COENZYME A DEHYDROGENASE; ISOENZYME; LONG CHAIN ACYL COENZYME A DEHYDROGENASE; PHYTANIC ACID; UNCLASSIFIED DRUG;

ARTICLE; CELL LINE; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME PURIFICATION; ENZYME SPECIFICITY; FATTY ACID OXIDATION; FIBROBLAST CULTURE; HUMAN; HUMAN CELL; IN VITRO STUDY; PRIORITY JOURNAL;

ACYL-COA DEHYDROGENASE, LONG-CHAIN; CELLS, CULTURED; COENZYME A; FATTY ACIDS; HUMANS; MITOCHONDRIA; OXIDATION-REDUCTION; OXIDOREDUCTASES; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS; SUBSTRATE SPECIFICITY;

EID: 0032584506     PISSN: 00052760     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0005-2760(98)00053-8     Document Type: Article

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