Targeted disruption of mouse long-chain acyl-CoA dehydrogenase gene reveals crucial roles for fatty acid oxidation

Proceedings of the National Academy of Sciences of the United States of America

Volumn 95, Issue 26, 1998, Pages 15592-15597

  Kurtz, David M ^a   Rinaldo, Piero ^b   Rhead, William J ^c   Tian, Liqun ^a   Millington, David S ^d   Vockley, Jerry ^e   Hamm, Doug A ^a   Brix, Amy E ^a   Lindsey, J Russell ^a   Pinkert, Carl A ^a   O'Brien, William E ^f   Wood, Philip A ^a  

^a UNIVERSITY OF ALABAMA SCHOOL OF MEDICINE   (United States)

^b YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^c UNIVERSITY OF IOWA   (United States)

^d DUKE CHILDREN S HOSPITAL   (United States)

^e MAYO CLINIC   (United States)

^f BAYLOR COLLEGE OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CARNITINE; DICARBOXYLIC ACID; FATTY ACID; LONG CHAIN FATTY ACID COENZYME A DEHYDROGENASE; OXIDOREDUCTASE; RNA; UNCLASSIFIED DRUG;

ACIDURIA; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CARDIOMYOPATHY; CONTROLLED STUDY; EMBRYO; ENZYME ACTIVITY; ENZYME DEFICIENCY; FATTY ACID BLOOD LEVEL; FATTY ACID OXIDATION; FEMALE; FETUS WASTAGE; GENE DISRUPTION; HYPOGLYCEMIA; LIPIDOSIS; LIVER MITOCHONDRION; MALE; MOUSE; NONHUMAN; PRIORITY JOURNAL; SUDDEN DEATH;

ACYL-COA DEHYDROGENASE, LONG-CHAIN; ANIMALS; DISEASE MODELS, ANIMAL; FATTY ACIDS, NONESTERIFIED; HUMANS; LIPID METABOLISM, INBORN ERRORS; LIVER; MICE; MICE, KNOCKOUT; MITOCHONDRIA, LIVER; MUSCLE, SKELETAL; SUBSTRATE SPECIFICITY;

EID: 13044277575     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.95.26.15592     Document Type: Article

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