Arrhythmias and conduction defects as presenting symptoms of fatty acid oxidation disorders in children

Circulation

Volumn 100, Issue 22, 1999, Pages 2248-2253

  Bonnet, Damien ^a,c   Martin, Delphine ^a   De Lonlay, Pascale ^a   Villain, Elizabeth ^a   Jouvet, Philippe ^a   Rabier, Daniel ^a   Brivet, Michèle ^b   Saudubray, Jean Marie ^a  

^a HÔPITAL NECKER ENFANTS MALADES   (France)

^b BICÊTRE HOSPITAL   (France)

^c Service de Cardiologie Pediatrique   (France)

Author keywords

Arrhythmia; Fatty acids; Metabolism

Indexed keywords

ACYL COENZYME A DEHYDROGENASE; ACYLCARNITINE; CARBON 14; CARNITINE PALMITOYLTRANSFERASE; CARRIER PROTEIN; FATTY ACID;

ARTICLE; CARDIOVASCULAR DISEASE; CHILD; CHILDHOOD DISEASE; ELECTROCARDIOGRAPHY MONITORING; ENZYME DEFICIENCY; FATTY ACID METABOLISM; FEMALE; HEART ARRHYTHMIA; HEART BUNDLE BRANCH BLOCK; HEART MUSCLE CONDUCTION DISTURBANCE; HEART VENTRICLE TACHYCARDIA; HUMAN; INFANT; MAJOR CLINICAL STUDY; MALE; MITOCHONDRIAL MEMBRANE; NEWBORN; PRIORITY JOURNAL; SYMPTOMATOLOGY;

EID: 0032729717     PISSN: 00097322     EISSN: None     Source Type: Journal    
DOI: 10.1161/01.CIR.100.22.2248     Document Type: Article

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