The human mitochondrial replication fork in health and disease

Biochimica et Biophysica Acta - Bioenergetics

Volumn 1797, Issue 8, 2010, Pages 1378-1388

  Wanrooij, Sjoerd ^a   Falkenberg, Maria ^a,b  

^a UNIVERSITY OF GOTHENBURG   (Sweden)

^b MAX PLANCK INST FÜR BIOLOGIE   (Germany)

Author keywords

DNA replication; Mitochondria; Mitochondrial disease; MtDNA; POLRMT; Twinkle

Indexed keywords

DNA DIRECTED DNA POLYMERASE GAMMA; DOUBLE STRANDED DNA; GENE PRODUCT; MITOCHONDRIAL DNA; MITOCHONDRIAL RNA; PROTEIN TWINKLE; RNA POLYMERASE; SINGLE STRANDED DNA BINDING PROTEIN; UNCLASSIFIED DRUG;

AMINO TERMINAL SEQUENCE; CARBOXY TERMINAL SEQUENCE; CHRONIC PROGRESSIVE EXTERNAL OPHTHALMOPLEGIA; DISEASE MODEL; ENERGY YIELD; ENZYME ACTIVITY; GENE DELETION; GENE FUNCTION; GENE IDENTIFICATION; GENE OVEREXPRESSION; HOMOZYGOSITY; HUMAN; MITOCHONDRIAL DNA DEPLETION; MITOCHONDRIAL DNA REPLICATION; MUTATIONAL ANALYSIS; NEUROMUSCULAR DISEASE; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL; REVIEW;

ANIMALS; DNA HELICASES; DNA REPLICATION; DNA, MITOCHONDRIAL; DNA-DIRECTED DNA POLYMERASE; DNA-DIRECTED RNA POLYMERASES; HUMANS; MITOCHONDRIA; MUTATION;

MAMMALIA;

EID: 77953811054     PISSN: 00052728     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbabio.2010.04.015     Document Type: Review

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