-
2
-
-
0034278759
-
Aggresomes and Russell bodies. Symptoms of cellular indigestion?
-
Kopito R.R., and Sitia R. Aggresomes and Russell bodies. Symptoms of cellular indigestion?. EMBO Rep 1 (2000) 225-231
-
(2000)
EMBO Rep
, vol.1
, pp. 225-231
-
-
Kopito, R.R.1
Sitia, R.2
-
3
-
-
67649246879
-
alpha1-Antitrypsin deficiency, chronic obstructive pulmonary disease and the serpinopathies
-
Ekeowa U.I., Gooptu B., Belorgey D., Hagglof P., Karlsson-Li S., Miranda E., et al. alpha1-Antitrypsin deficiency, chronic obstructive pulmonary disease and the serpinopathies. Clin Sci (Lond) 116 (2009) 837-850
-
(2009)
Clin Sci (Lond)
, vol.116
, pp. 837-850
-
-
Ekeowa, U.I.1
Gooptu, B.2
Belorgey, D.3
Hagglof, P.4
Karlsson-Li, S.5
Miranda, E.6
-
4
-
-
63149175877
-
Endoplasmic reticulum protein quality control in neurodegenerative disease: the good, the bad and the therapy
-
Scheper W., and Hoozemans J.J. Endoplasmic reticulum protein quality control in neurodegenerative disease: the good, the bad and the therapy. Curr Med Chem 16 (2009) 615-626
-
(2009)
Curr Med Chem
, vol.16
, pp. 615-626
-
-
Scheper, W.1
Hoozemans, J.J.2
-
5
-
-
8744302265
-
Catalysis of disulphide bond formation in the endoplasmic reticulum
-
Ellgaard L. Catalysis of disulphide bond formation in the endoplasmic reticulum. Biochem Soc Trans 32 Pt 5 (2004 Nov) 663-667
-
(2004)
Biochem Soc Trans
, vol.32
, Issue.PART 5
, pp. 663-667
-
-
Ellgaard, L.1
-
6
-
-
0346096508
-
Quality control in the endoplasmic reticulum protein factory
-
Sitia R., and Braakman I. Quality control in the endoplasmic reticulum protein factory. Nature 426 (2003) 891-894
-
(2003)
Nature
, vol.426
, pp. 891-894
-
-
Sitia, R.1
Braakman, I.2
-
7
-
-
0026059137
-
Peptide-binding specificity of the molecular chaperone BiP
-
Flynn G.C., Pohl J., Flocco M.T., and Rothman J.E. Peptide-binding specificity of the molecular chaperone BiP. Nature 353 (1991) 726-730
-
(1991)
Nature
, vol.353
, pp. 726-730
-
-
Flynn, G.C.1
Pohl, J.2
Flocco, M.T.3
Rothman, J.E.4
-
8
-
-
0027484417
-
Affinity panning of a library of peptides displayed on bacteriophages reveals the binding specificity of BiP
-
Blond-Elguindi S., Cwirla S.E., Dower W.J., Lipshutz R.J., Sprang S.R., Sambrook J.F., et al. Affinity panning of a library of peptides displayed on bacteriophages reveals the binding specificity of BiP. Cell 75 November (1993) 717-728
-
(1993)
Cell
, vol.75
, Issue.November
, pp. 717-728
-
-
Blond-Elguindi, S.1
Cwirla, S.E.2
Dower, W.J.3
Lipshutz, R.J.4
Sprang, S.R.5
Sambrook, J.F.6
-
10
-
-
34948899397
-
Sequential steps and checkpoints in the early exocytic compartment during secretory IgM biogenesis
-
Anelli T., Ceppi S., Bergamelli L., Cortini M., Masciarelli S., Valetti C., et al. Sequential steps and checkpoints in the early exocytic compartment during secretory IgM biogenesis. Embo J 26 (2007) 4177-4188
-
(2007)
Embo J
, vol.26
, pp. 4177-4188
-
-
Anelli, T.1
Ceppi, S.2
Bergamelli, L.3
Cortini, M.4
Masciarelli, S.5
Valetti, C.6
-
11
-
-
38549103628
-
Protein quality control in the early secretory pathway
-
Anelli T., and Sitia R. Protein quality control in the early secretory pathway. Embo J 27 (2008) 315-327
-
(2008)
Embo J
, vol.27
, pp. 315-327
-
-
Anelli, T.1
Sitia, R.2
-
12
-
-
0141565928
-
Immunoglobulin assembly and secretion
-
Honjo T., Alt F.W., and Neuberger M.S. (Eds), Elsevier, London
-
Hendershot L., and Sitia R. Immunoglobulin assembly and secretion. In: Honjo T., Alt F.W., and Neuberger M.S. (Eds). Molecular biology of B cells (2005), Elsevier, London 261-273
-
(2005)
Molecular biology of B cells
, pp. 261-273
-
-
Hendershot, L.1
Sitia, R.2
-
13
-
-
0036911213
-
A subset of chaperones and folding enzymes form multiprotein complexes in endoplasmic reticulum to bind nascent proteins
-
Meunier L., Usherwood Y.K., Chung K.T., and Hendershot L.M. A subset of chaperones and folding enzymes form multiprotein complexes in endoplasmic reticulum to bind nascent proteins. Mol Biol Cell 13 (2002) 4456-4469
-
(2002)
Mol Biol Cell
, vol.13
, pp. 4456-4469
-
-
Meunier, L.1
Usherwood, Y.K.2
Chung, K.T.3
Hendershot, L.M.4
-
14
-
-
0035798550
-
Reduction of interchain disulfide bonds precedes the dislocation of Ig-mu chains from the endoplasmic reticulum to the cytosol for proteasomal degradation
-
Fagioli C., Mezghrani A., and Sitia R. Reduction of interchain disulfide bonds precedes the dislocation of Ig-mu chains from the endoplasmic reticulum to the cytosol for proteasomal degradation. J Biol Chem 276 (2001) 40962-40967
-
(2001)
J Biol Chem
, vol.276
, pp. 40962-40967
-
-
Fagioli, C.1
Mezghrani, A.2
Sitia, R.3
-
15
-
-
0039435285
-
Lectins and protein traffic early in the secretory pathway
-
Hauri H.P., Nufer O., Breuza L., Tekaya H.B., and Liang L. Lectins and protein traffic early in the secretory pathway. Biochem Soc Symp 69 (2002) 73-82
-
(2002)
Biochem Soc Symp
, vol.69
, pp. 73-82
-
-
Hauri, H.P.1
Nufer, O.2
Breuza, L.3
Tekaya, H.B.4
Liang, L.5
-
16
-
-
0027328703
-
ERGIC-53, a membrane protein of the ER-Golgi intermediate compartment, carries an ER retention motif
-
Schindler R., Itin C., Zerial M., Lottspeich F., and Hauri H.P. ERGIC-53, a membrane protein of the ER-Golgi intermediate compartment, carries an ER retention motif. Eur J Cell Biol 61 (1993) 1-9
-
(1993)
Eur J Cell Biol
, vol.61
, pp. 1-9
-
-
Schindler, R.1
Itin, C.2
Zerial, M.3
Lottspeich, F.4
Hauri, H.P.5
-
17
-
-
0141753993
-
Thiol-mediated protein retention in the endoplasmic reticulum: the role of ERp44
-
Anelli T., Alessio M., Bachi A., Bergamelli L., Bertoli G., Camerini S., et al. Thiol-mediated protein retention in the endoplasmic reticulum: the role of ERp44. Embo J 22 (2003) 5015-5022
-
(2003)
Embo J
, vol.22
, pp. 5015-5022
-
-
Anelli, T.1
Alessio, M.2
Bachi, A.3
Bergamelli, L.4
Bertoli, G.5
Camerini, S.6
-
18
-
-
0037083869
-
ERp44, a novel endoplasmic reticulum folding assistant of the thioredoxin family
-
Anelli T., Alessio M., Mezghrani A., Simmen T., Talamo F., Bachi A., et al. ERp44, a novel endoplasmic reticulum folding assistant of the thioredoxin family. Embo J 21 (2002) 835-844
-
(2002)
Embo J
, vol.21
, pp. 835-844
-
-
Anelli, T.1
Alessio, M.2
Mezghrani, A.3
Simmen, T.4
Talamo, F.5
Bachi, A.6
-
19
-
-
49649122527
-
Multistep, sequential control of the trafficking and function of the multiple sulfatase deficiency gene product, SUMF1 by PDI, ERGIC-53 and ERp44
-
Fraldi A., Zito E., Annunziata F., Lombardi A., Cozzolino M., Monti M., et al. Multistep, sequential control of the trafficking and function of the multiple sulfatase deficiency gene product, SUMF1 by PDI, ERGIC-53 and ERp44. Hum Mol Genet 17 (2008) 2610-2621
-
(2008)
Hum Mol Genet
, vol.17
, pp. 2610-2621
-
-
Fraldi, A.1
Zito, E.2
Annunziata, F.3
Lombardi, A.4
Cozzolino, M.5
Monti, M.6
-
20
-
-
33646699342
-
Dynamic retention of Ero1alpha and Ero1beta in the endoplasmic reticulum by interactions with PDI and ERp44
-
Otsu M., Bertoli G., Fagioli C., Guerini-Rocco E., Nerini-Molteni S., Ruffato E., et al. Dynamic retention of Ero1alpha and Ero1beta in the endoplasmic reticulum by interactions with PDI and ERp44. Antioxid Redox Signal 8 (2006) 274-282
-
(2006)
Antioxid Redox Signal
, vol.8
, pp. 274-282
-
-
Otsu, M.1
Bertoli, G.2
Fagioli, C.3
Guerini-Rocco, E.4
Nerini-Molteni, S.5
Ruffato, E.6
-
21
-
-
34347338702
-
Adiponectin secretion is regulated by SIRT1 and the ER oxidoreductase Ero1-Lalpha
-
Qiang L., Wang H., and Farmer S.R. Adiponectin secretion is regulated by SIRT1 and the ER oxidoreductase Ero1-Lalpha. Mol Cell Biol 27 (2007) 4698-4707
-
(2007)
Mol Cell Biol
, vol.27
, pp. 4698-4707
-
-
Qiang, L.1
Wang, H.2
Farmer, S.R.3
-
22
-
-
34248197560
-
Secretion of the adipocyte-specific secretory protein adiponectin critically depends on thiol-mediated protein retention
-
Wang Z.V., Schraw T.D., Kim J.Y., Khan T., Rajala M.W., Follenzi A., et al. Secretion of the adipocyte-specific secretory protein adiponectin critically depends on thiol-mediated protein retention. Mol Cell Biol 27 (2007) 3716-3731
-
(2007)
Mol Cell Biol
, vol.27
, pp. 3716-3731
-
-
Wang, Z.V.1
Schraw, T.D.2
Kim, J.Y.3
Khan, T.4
Rajala, M.W.5
Follenzi, A.6
-
23
-
-
54949131287
-
New insights into thiol-mediated regulation of adiponectin secretion
-
Wolf G. New insights into thiol-mediated regulation of adiponectin secretion. Nutr Rev 66 (2008) 642-645
-
(2008)
Nutr Rev
, vol.66
, pp. 642-645
-
-
Wolf, G.1
-
24
-
-
38949125405
-
Post-translational modifications of adiponectin: mechanisms and functional implications
-
Wang Y., Lam K.S., Yau M.H., and Xu A. Post-translational modifications of adiponectin: mechanisms and functional implications. Biochem J 409 (2008) 623-633
-
(2008)
Biochem J
, vol.409
, pp. 623-633
-
-
Wang, Y.1
Lam, K.S.2
Yau, M.H.3
Xu, A.4
-
25
-
-
56749176947
-
One step at a time: endoplasmic reticulum-associated degradation
-
Vembar S.S., and Brodsky J.L. One step at a time: endoplasmic reticulum-associated degradation. Nat Rev Mol Cell Biol 9 (2008) 944-957
-
(2008)
Nat Rev Mol Cell Biol
, vol.9
, pp. 944-957
-
-
Vembar, S.S.1
Brodsky, J.L.2
-
26
-
-
0032572582
-
Dislocation of type I membrane proteins from the ER to the cytosol is sensitive to changes in redox potential
-
Tortorella D., Story C.M., Huppa J.B., Wiertz E.J., Jones T.R., Bacik I., et al. Dislocation of type I membrane proteins from the ER to the cytosol is sensitive to changes in redox potential. J Cell Biol 27 142 (1998) 365-376
-
(1998)
J Cell Biol
, vol.27
, Issue.142
, pp. 365-376
-
-
Tortorella, D.1
Story, C.M.2
Huppa, J.B.3
Wiertz, E.J.4
Jones, T.R.5
Bacik, I.6
-
27
-
-
0038143181
-
Immunoglobulin light chains dictate vesicular transport-dependent and -independent routes for IgM degradation by the ubiquitin-proteasome pathway
-
Elkabetz Y., Kerem A., Tencer L., Winitz D., Kopito R.R., and Bar-Nun S. Immunoglobulin light chains dictate vesicular transport-dependent and -independent routes for IgM degradation by the ubiquitin-proteasome pathway. J Biol Chem 278 (2003) 18922-18929
-
(2003)
J Biol Chem
, vol.278
, pp. 18922-18929
-
-
Elkabetz, Y.1
Kerem, A.2
Tencer, L.3
Winitz, D.4
Kopito, R.R.5
Bar-Nun, S.6
-
28
-
-
43549087339
-
Segregation and rapid turnover of EDEM1 by an autophagy-like mechanism modulates standard ERAD and folding activities
-
Cali T., Galli C., Olivari S., and Molinari M. Segregation and rapid turnover of EDEM1 by an autophagy-like mechanism modulates standard ERAD and folding activities. Biochem Biophys Res Commun 371 (2008) 405-410
-
(2008)
Biochem Biophys Res Commun
, vol.371
, pp. 405-410
-
-
Cali, T.1
Galli, C.2
Olivari, S.3
Molinari, M.4
-
29
-
-
0034039901
-
Degradation of unassembled soluble Ig subunits by cytosolic proteasomes: evidence that retrotranslocation and degradation are coupled events
-
Mancini R., Fagioli C., Fra A.M., Maggioni C., and Sitia R. Degradation of unassembled soluble Ig subunits by cytosolic proteasomes: evidence that retrotranslocation and degradation are coupled events. Faseb J 14 (2000) 769-778
-
(2000)
Faseb J
, vol.14
, pp. 769-778
-
-
Mancini, R.1
Fagioli, C.2
Fra, A.M.3
Maggioni, C.4
Sitia, R.5
-
30
-
-
69749123786
-
Fine-tuning of the unfolded protein response: assembling the IRE1alpha interactome
-
Hetz C., and Glimcher L.H. Fine-tuning of the unfolded protein response: assembling the IRE1alpha interactome. Mol Cell 35 (2009) 551-561
-
(2009)
Mol Cell
, vol.35
, pp. 551-561
-
-
Hetz, C.1
Glimcher, L.H.2
-
31
-
-
33751333201
-
Substrate-specific translocational attenuation during ER stress defines a pre-emptive quality control pathway
-
Kang S.W., Rane N.S., Kim S.J., Garrison J.L., Taunton J., and Hegde R.S. Substrate-specific translocational attenuation during ER stress defines a pre-emptive quality control pathway. Cell 127 (2006) 999-1013
-
(2006)
Cell
, vol.127
, pp. 999-1013
-
-
Kang, S.W.1
Rane, N.S.2
Kim, S.J.3
Garrison, J.L.4
Taunton, J.5
Hegde, R.S.6
-
32
-
-
33750087269
-
Conditions of endoplasmic reticulum stress favor the accumulation of cytosolic prion protein
-
Orsi A., Fioriti L., Chiesa R., and Sitia R. Conditions of endoplasmic reticulum stress favor the accumulation of cytosolic prion protein. J Biol Chem 281 (2006) 30431-30438
-
(2006)
J Biol Chem
, vol.281
, pp. 30431-30438
-
-
Orsi, A.1
Fioriti, L.2
Chiesa, R.3
Sitia, R.4
-
33
-
-
33745893809
-
Decay of endoplasmic reticulum-localized mRNAs during the unfolded protein response
-
Hollien J., and Weissman J.S. Decay of endoplasmic reticulum-localized mRNAs during the unfolded protein response. Science 313 (2006) 104-107
-
(2006)
Science
, vol.313
, pp. 104-107
-
-
Hollien, J.1
Weissman, J.S.2
-
34
-
-
36248949141
-
The endoplasmic reticulum and the unfolded protein response
-
Malhotra J.D., and Kaufman R.J. The endoplasmic reticulum and the unfolded protein response. Semin Cell Dev Biol 18 (2007) 716-731
-
(2007)
Semin Cell Dev Biol
, vol.18
, pp. 716-731
-
-
Malhotra, J.D.1
Kaufman, R.J.2
-
35
-
-
34548512233
-
The role of p58IPK in protecting the stressed endoplasmic reticulum
-
Rutkowski D.T., Kang S.W., Goodman A.G., Garrison J.L., Taunton J., Katze M.G., et al. The role of p58IPK in protecting the stressed endoplasmic reticulum. Mol Biol Cell 18 (2007) 3681-3691
-
(2007)
Mol Biol Cell
, vol.18
, pp. 3681-3691
-
-
Rutkowski, D.T.1
Kang, S.W.2
Goodman, A.G.3
Garrison, J.L.4
Taunton, J.5
Katze, M.G.6
-
36
-
-
33751159209
-
Intracellular signaling by the unfolded protein response
-
Bernales S., Papa F.R., and Walter P. Intracellular signaling by the unfolded protein response. Annu Rev Cell Dev Biol 22 (2006) 487-508
-
(2006)
Annu Rev Cell Dev Biol
, vol.22
, pp. 487-508
-
-
Bernales, S.1
Papa, F.R.2
Walter, P.3
-
37
-
-
26844511378
-
Expression clustering reveals detailed co-expression patterns of functionally related proteins during B cell differentiation: a proteomic study using a combination of one-dimensional gel electrophoresis, LC-MS/MS, and stable isotope labeling by amino acids in cell culture (SILAC)
-
Romijn E.P., Christis C., Wieffer M., Gouw J.W., Fullaondo A., van der Sluijs P., et al. Expression clustering reveals detailed co-expression patterns of functionally related proteins during B cell differentiation: a proteomic study using a combination of one-dimensional gel electrophoresis, LC-MS/MS, and stable isotope labeling by amino acids in cell culture (SILAC). Mol Cell Proteom 4 (2005) 1297-1310
-
(2005)
Mol Cell Proteom
, vol.4
, pp. 1297-1310
-
-
Romijn, E.P.1
Christis, C.2
Wieffer, M.3
Gouw, J.W.4
Fullaondo, A.5
van der Sluijs, P.6
-
38
-
-
0037332128
-
Sequential waves of functionally related proteins are expressed when B cells prepare for antibody secretion
-
van Anken E., Romijn E.P., Maggioni C., Mezghrani A., Sitia R., Braakman I., et al. Sequential waves of functionally related proteins are expressed when B cells prepare for antibody secretion. Immunity 18 (2003) 243-253
-
(2003)
Immunity
, vol.18
, pp. 243-253
-
-
van Anken, E.1
Romijn, E.P.2
Maggioni, C.3
Mezghrani, A.4
Sitia, R.5
Braakman, I.6
-
39
-
-
0035913294
-
Plasma cell differentiation requires the transcription factor XBP-1
-
Reimold A.M., Iwakoshi N.N., Manis J., Vallabhajosyula P., Szomolanyi-Tsuda E., Gravallese E.M., et al. Plasma cell differentiation requires the transcription factor XBP-1. Nature 412 (2001) 300-307
-
(2001)
Nature
, vol.412
, pp. 300-307
-
-
Reimold, A.M.1
Iwakoshi, N.N.2
Manis, J.3
Vallabhajosyula, P.4
Szomolanyi-Tsuda, E.5
Gravallese, E.M.6
-
40
-
-
14944371187
-
The unfolded protein response sensor IRE1alpha is required at 2 distinct steps in B cell lymphopoiesis
-
Zhang K., Wong H.N., Song B., Miller C.N., Scheuner D., and Kaufman R.J. The unfolded protein response sensor IRE1alpha is required at 2 distinct steps in B cell lymphopoiesis. J Clin Invest 115 (2005) 268-281
-
(2005)
J Clin Invest
, vol.115
, pp. 268-281
-
-
Zhang, K.1
Wong, H.N.2
Song, B.3
Miller, C.N.4
Scheuner, D.5
Kaufman, R.J.6
-
41
-
-
76949099567
-
CHOP-independent apoptosis and pathway-selective induction of the UPR in developing plasmacells
-
10.1016/j.molimm.2009.12.003
-
Masciarelli S., Fra A.M., Pengo N., Bertolotti M., Cenci S., Fagioli C., et al. CHOP-independent apoptosis and pathway-selective induction of the UPR in developing plasmacells. Mol Immunol (2009) 10.1016/j.molimm.2009.12.003
-
(2009)
Mol Immunol
-
-
Masciarelli, S.1
Fra, A.M.2
Pengo, N.3
Bertolotti, M.4
Cenci, S.5
Fagioli, C.6
-
42
-
-
33644871448
-
Progressively impaired proteasomal capacity during terminal plasma cell differentiation
-
Cenci S., Mezghrani A., Cascio P., Bianchi G., Cerruti F., Fra A., et al. Progressively impaired proteasomal capacity during terminal plasma cell differentiation. Embo J 25 (2006) 1104-1113
-
(2006)
Embo J
, vol.25
, pp. 1104-1113
-
-
Cenci, S.1
Mezghrani, A.2
Cascio, P.3
Bianchi, G.4
Cerruti, F.5
Fra, A.6
-
43
-
-
63849281664
-
The proteasome load versus capacity balance determines apoptotic sensitivity of multiple myeloma cells to proteasome inhibition
-
Bianchi G., Oliva L., Cascio P., Pengo N., Fontana F., Cerruti F., et al. The proteasome load versus capacity balance determines apoptotic sensitivity of multiple myeloma cells to proteasome inhibition. Blood 113 (2009) 3040-3049
-
(2009)
Blood
, vol.113
, pp. 3040-3049
-
-
Bianchi, G.1
Oliva, L.2
Cascio, P.3
Pengo, N.4
Fontana, F.5
Cerruti, F.6
-
44
-
-
33745238126
-
Cubic membranes: a legend beyond the Flatland of cell membrane organization
-
Almsherqi Z.A., Kohlwein S.D., and Deng Y. Cubic membranes: a legend beyond the Flatland of cell membrane organization. J Cell Biol 173 (2006) 839-844
-
(2006)
J Cell Biol
, vol.173
, pp. 839-844
-
-
Almsherqi, Z.A.1
Kohlwein, S.D.2
Deng, Y.3
-
45
-
-
0242266921
-
Formation of stacked ER cisternae by low affinity protein interactions
-
Snapp E.L., Hegde R.S., Francolini M., Lombardo F., Colombo S., Pedrazzini E., et al. Formation of stacked ER cisternae by low affinity protein interactions. J Cell Biol 163 (2003) 257-269
-
(2003)
J Cell Biol
, vol.163
, pp. 257-269
-
-
Snapp, E.L.1
Hegde, R.S.2
Francolini, M.3
Lombardo, F.4
Colombo, S.5
Pedrazzini, E.6
-
46
-
-
32044445021
-
A class of membrane proteins shaping the tubular endoplasmic reticulum
-
Voeltz G.K., Prinz W.A., Shibata Y., Rist J.M., and Rapoport T.A. A class of membrane proteins shaping the tubular endoplasmic reticulum. Cell 10 124 (2006) 573-586
-
(2006)
Cell
, vol.10
, Issue.124
, pp. 573-586
-
-
Voeltz, G.K.1
Prinz, W.A.2
Shibata, Y.3
Rist, J.M.4
Rapoport, T.A.5
-
47
-
-
61949239472
-
Knockdown of p180 eliminates the terminal differentiation of a secretory cell line
-
Benyamini P., Webster P., and Meyer D.I. Knockdown of p180 eliminates the terminal differentiation of a secretory cell line. Mol Biol Cell 20 (2009) 732-744
-
(2009)
Mol Biol Cell
, vol.20
, pp. 732-744
-
-
Benyamini, P.1
Webster, P.2
Meyer, D.I.3
-
48
-
-
27844451115
-
Pathways for protein transport to seed storage vacuoles
-
Jolliffe N.A., Craddock C.P., and Frigerio L. Pathways for protein transport to seed storage vacuoles. Biochem Soc Trans 33 (2005) 1016-1018
-
(2005)
Biochem Soc Trans
, vol.33
, pp. 1016-1018
-
-
Jolliffe, N.A.1
Craddock, C.P.2
Frigerio, L.3
-
50
-
-
27744464921
-
Seed maturation: developing an intrusive phase to accomplish a quiescent state
-
Vicente-Carbajosa J., and Carbonero P. Seed maturation: developing an intrusive phase to accomplish a quiescent state. Int J Dev Biol 49 (2005) 645-651
-
(2005)
Int J Dev Biol
, vol.49
, pp. 645-651
-
-
Vicente-Carbajosa, J.1
Carbonero, P.2
-
51
-
-
0024971433
-
Elevated synthesis of human alpha 1-antitrypsin hinders the secretion of murine alpha 1-antitrypsin from hepatocytes of transgenic mice
-
Sifers R.N., Rogers B.B., Hawkins H.K., Finegold M.J., and Woo S.L. Elevated synthesis of human alpha 1-antitrypsin hinders the secretion of murine alpha 1-antitrypsin from hepatocytes of transgenic mice. J Biol Chem ß264 (1989) 15696-15700
-
(1989)
J Biol Chem
, vol.-264
, pp. 15696-15700
-
-
Sifers, R.N.1
Rogers, B.B.2
Hawkins, H.K.3
Finegold, M.J.4
Woo, S.L.5
-
52
-
-
67650713938
-
Conformational pathology of the serpins: themes, variations, and therapeutic strategies
-
Gooptu B., and Lomas D.A. Conformational pathology of the serpins: themes, variations, and therapeutic strategies. Annu Rev Biochem 78 (2009) 147-176
-
(2009)
Annu Rev Biochem
, vol.78
, pp. 147-176
-
-
Gooptu, B.1
Lomas, D.A.2
-
54
-
-
0036707542
-
Novel fibrinogen gamma375 Arg → Trp mutation (fibrinogen aguadilla) causes hepatic endoplasmic reticulum storage and hypofibrinogenemia
-
Brennan S.O., Maghzal G., Shneider B.L., Gordon R., Magid M.S., and George P.M. Novel fibrinogen gamma375 Arg → Trp mutation (fibrinogen aguadilla) causes hepatic endoplasmic reticulum storage and hypofibrinogenemia. Hepatology 36 (2002) 652-658
-
(2002)
Hepatology
, vol.36
, pp. 652-658
-
-
Brennan, S.O.1
Maghzal, G.2
Shneider, B.L.3
Gordon, R.4
Magid, M.S.5
George, P.M.6
-
55
-
-
41449111489
-
Uromodulin storage disease
-
Nasr S.H., Lucia J.P., Galgano S.J., Markowitz G.S., and D'Agati V.D. Uromodulin storage disease. Kidney Int 73 (2008) 971-976
-
(2008)
Kidney Int
, vol.73
, pp. 971-976
-
-
Nasr, S.H.1
Lucia, J.P.2
Galgano, S.J.3
Markowitz, G.S.4
D'Agati, V.D.5
-
56
-
-
0036914069
-
Mutations of the UMOD gene are responsible for medullary cystic kidney disease 2 and familial juvenile hyperuricaemic nephropathy
-
Hart T.C., Gorry M.C., Hart P.S., Woodard A.S., Shihabi Z., Sandhu J., et al. Mutations of the UMOD gene are responsible for medullary cystic kidney disease 2 and familial juvenile hyperuricaemic nephropathy. J Med Genet 39 (2002) 882-892
-
(2002)
J Med Genet
, vol.39
, pp. 882-892
-
-
Hart, T.C.1
Gorry, M.C.2
Hart, P.S.3
Woodard, A.S.4
Shihabi, Z.5
Sandhu, J.6
-
57
-
-
33749532096
-
Defective intracellular trafficking of uromodulin mutant isoforms
-
Bernascone I., Vavassori S., Di Pentima A., Santambrogio S., Lamorte G., Amoroso A., et al. Defective intracellular trafficking of uromodulin mutant isoforms. Traffic 7 (2006) 1567-1579
-
(2006)
Traffic
, vol.7
, pp. 1567-1579
-
-
Bernascone, I.1
Vavassori, S.2
Di Pentima, A.3
Santambrogio, S.4
Lamorte, G.5
Amoroso, A.6
-
58
-
-
33645258309
-
Mutant tamm-horsfall glycoprotein accumulation in endoplasmic reticulum induces apoptosis reversed by colchicine and sodium 4-phenylbutyrate
-
Choi S.W., Ryu O.H., Choi S.J., Song I.S., Bleyer A.J., and Hart T.C. Mutant tamm-horsfall glycoprotein accumulation in endoplasmic reticulum induces apoptosis reversed by colchicine and sodium 4-phenylbutyrate. J Am Soc Nephrol 6 (2005) 3006-3014
-
(2005)
J Am Soc Nephrol
, vol.6
, pp. 3006-3014
-
-
Choi, S.W.1
Ryu, O.H.2
Choi, S.J.3
Song, I.S.4
Bleyer, A.J.5
Hart, T.C.6
-
59
-
-
0346752171
-
Allelism of MCKD FJHN and GCKD caused by impairment of uromodulin export dynamics
-
Rampoldi L., Caridi G., Santon D., Boaretto F., Bernascone I., Lamorte G., et al. Allelism of MCKD FJHN and GCKD caused by impairment of uromodulin export dynamics. Hum Mol Genet 12 (2003) 123369-123384
-
(2003)
Hum Mol Genet
, vol.12
, pp. 123369-123384
-
-
Rampoldi, L.1
Caridi, G.2
Santon, D.3
Boaretto, F.4
Bernascone, I.5
Lamorte, G.6
-
60
-
-
0032250506
-
Is the hemochromatosis gene a modifier locus for cystic fibrosis?
-
Rohlfs E.M., Shaheen N.J., and Silverman L.M. Is the hemochromatosis gene a modifier locus for cystic fibrosis?. Genet Test 2 (1998) 85-88
-
(1998)
Genet Test
, vol.2
, pp. 85-88
-
-
Rohlfs, E.M.1
Shaheen, N.J.2
Silverman, L.M.3
-
61
-
-
42349086509
-
The unfolded protein response in hereditary haemochromatosis
-
de Almeida S.F., and de Sousa M. The unfolded protein response in hereditary haemochromatosis. J Cell Mol Med 12 (2008) 421-434
-
(2008)
J Cell Mol Med
, vol.12
, pp. 421-434
-
-
de Almeida, S.F.1
de Sousa, M.2
-
62
-
-
14444283397
-
Identification of a gene that causes primary open angle glaucoma
-
Stone E.M., Fingert J.H., Alward W.L., Nguyen T.D., Polansky J.R., Sunden S.L., et al. Identification of a gene that causes primary open angle glaucoma. Science 275 (1997) 668-670
-
(1997)
Science
, vol.275
, pp. 668-670
-
-
Stone, E.M.1
Fingert, J.H.2
Alward, W.L.3
Nguyen, T.D.4
Polansky, J.R.5
Sunden, S.L.6
-
63
-
-
4644359640
-
Intracellular sequestration of hetero-oligomers formed by wild-type and glaucoma-causing myocilin mutants
-
Gobeil S., Rodrigue M.A., Moisan S., Nguyen T.D., Polansky J.R., Morissette J., et al. Intracellular sequestration of hetero-oligomers formed by wild-type and glaucoma-causing myocilin mutants. Invest Ophthalmol Vis Sci 45 (2004) 3560-3567
-
(2004)
Invest Ophthalmol Vis Sci
, vol.45
, pp. 3560-3567
-
-
Gobeil, S.1
Rodrigue, M.A.2
Moisan, S.3
Nguyen, T.D.4
Polansky, J.R.5
Morissette, J.6
-
64
-
-
33847045670
-
Aggregated myocilin induces Russell bodies and causes apoptosis: implications for the pathogenesis of myocilin-caused primary open-angle glaucoma
-
Yam G.H., Gaplovska-Kysela K., Zuber C., and Roth J. Aggregated myocilin induces Russell bodies and causes apoptosis: implications for the pathogenesis of myocilin-caused primary open-angle glaucoma. Am J Pathol 170 (2007) 100-109
-
(2007)
Am J Pathol
, vol.170
, pp. 100-109
-
-
Yam, G.H.1
Gaplovska-Kysela, K.2
Zuber, C.3
Roth, J.4
-
65
-
-
0031567985
-
Mapping of a gene for the increased susceptibility of B1 cells to Mott cell formation in murine autoimmune disease
-
Jiang Y., Hirose S., Hamano Y., Kodera S., Tsurui H., Abe M., et al. Mapping of a gene for the increased susceptibility of B1 cells to Mott cell formation in murine autoimmune disease. J Immunol 158 (1997) 992-997
-
(1997)
J Immunol
, vol.158
, pp. 992-997
-
-
Jiang, Y.1
Hirose, S.2
Hamano, Y.3
Kodera, S.4
Tsurui, H.5
Abe, M.6
-
66
-
-
0026347810
-
Russell bodies: a general response of secretory cells to synthesis of a mutant immunoglobulin which can neither exit from, nor be degraded in, the endoplasmic reticulum
-
Valetti C., Grossi C.E., Milstein C., and Sitia R. Russell bodies: a general response of secretory cells to synthesis of a mutant immunoglobulin which can neither exit from, nor be degraded in, the endoplasmic reticulum. J Cell Biol 115 (1991) 983-994
-
(1991)
J Cell Biol
, vol.115
, pp. 983-994
-
-
Valetti, C.1
Grossi, C.E.2
Milstein, C.3
Sitia, R.4
-
67
-
-
33746032588
-
ER storage diseases: a role for ERGIC-53 in controlling the formation and shape of Russell bodies
-
Mattioli L., Anelli T., Fagioli C., Tacchetti C., Sitia R., and Valetti C. ER storage diseases: a role for ERGIC-53 in controlling the formation and shape of Russell bodies. J Cell Sci 119 (2006) 2532-2541
-
(2006)
J Cell Sci
, vol.119
, pp. 2532-2541
-
-
Mattioli, L.1
Anelli, T.2
Fagioli, C.3
Tacchetti, C.4
Sitia, R.5
Valetti, C.6
-
68
-
-
75649140280
-
Immunoglobulin aggregation leading to Russell body formation is prevented by the antibody light chain
-
Corcos D., Osborn M.J., Matheson L.S., Santos F., Zou X., Smith J.A., et al. Immunoglobulin aggregation leading to Russell body formation is prevented by the antibody light chain. Blood 115 (2010) 282-288
-
(2010)
Blood
, vol.115
, pp. 282-288
-
-
Corcos, D.1
Osborn, M.J.2
Matheson, L.S.3
Santos, F.4
Zou, X.5
Smith, J.A.6
-
69
-
-
33947183940
-
Conventional light chains inhibit the autonomous signaling capacity of the B cell receptor
-
Meixlsperger S., Kohler F., Wossning T., Reppel M., Muschen M., and Jumaa H. Conventional light chains inhibit the autonomous signaling capacity of the B cell receptor. Immunity 26 (2007) 323-333
-
(2007)
Immunity
, vol.26
, pp. 323-333
-
-
Meixlsperger, S.1
Kohler, F.2
Wossning, T.3
Reppel, M.4
Muschen, M.5
Jumaa, H.6
-
70
-
-
36448958570
-
RET(MEN 2B) is active in the endoplasmic reticulum before reaching the cell surface
-
Runeberg-Roos P., Virtanen H., and Saarma M. RET(MEN 2B) is active in the endoplasmic reticulum before reaching the cell surface. Oncogene 26 (2007) 7909-7915
-
(2007)
Oncogene
, vol.26
, pp. 7909-7915
-
-
Runeberg-Roos, P.1
Virtanen, H.2
Saarma, M.3
-
71
-
-
0038349592
-
Mouse proteome analysis
-
Kanapin A., Batalov S., Davis M.J., Gough J., Grimmond S., Kawaji H., et al. Mouse proteome analysis. Genome Res 13 (2003) 1335-1344
-
(2003)
Genome Res
, vol.13
, pp. 1335-1344
-
-
Kanapin, A.1
Batalov, S.2
Davis, M.J.3
Gough, J.4
Grimmond, S.5
Kawaji, H.6
-
72
-
-
0034643336
-
Rapid degradation of a large fraction of newly synthesized proteins by proteasomes
-
Schubert U., Anton L.C., Gibbs J., Norbury C.C., Yewdell J.W., and Bennink J.R. Rapid degradation of a large fraction of newly synthesized proteins by proteasomes. Nature 404 (2000) 770-774
-
(2000)
Nature
, vol.404
, pp. 770-774
-
-
Schubert, U.1
Anton, L.C.2
Gibbs, J.3
Norbury, C.C.4
Yewdell, J.W.5
Bennink, J.R.6
-
73
-
-
57849136841
-
Autophagy: principles and significance in health and disease
-
Todde V., Veenhuis M., and van der Klei I.J. Autophagy: principles and significance in health and disease. Biochim Biophys Acta 1792 (2009) 3-13
-
(2009)
Biochim Biophys Acta
, vol.1792
, pp. 3-13
-
-
Todde, V.1
Veenhuis, M.2
van der Klei, I.J.3
-
74
-
-
0037470410
-
Role of EDEM in the release of misfolded glycoproteins from the calnexin cycle
-
Molinari M., Calanca V., Galli C., Lucca P., and Paganetti P. Role of EDEM in the release of misfolded glycoproteins from the calnexin cycle. Science 299 (2003) 1397-1400
-
(2003)
Science
, vol.299
, pp. 1397-1400
-
-
Molinari, M.1
Calanca, V.2
Galli, C.3
Lucca, P.4
Paganetti, P.5
-
75
-
-
67349266215
-
Basal autophagy is involved in the degradation of the ERAD component EDEM1
-
Le Fourn V., Gaplovska-Kysela K., Guhl B., Santimaria R., Zuber C., and Roth J. Basal autophagy is involved in the degradation of the ERAD component EDEM1. Cell Mol Life Sci 66 (2009) 1434-1445
-
(2009)
Cell Mol Life Sci
, vol.66
, pp. 1434-1445
-
-
Le Fourn, V.1
Gaplovska-Kysela, K.2
Guhl, B.3
Santimaria, R.4
Zuber, C.5
Roth, J.6
-
76
-
-
34548402513
-
Stimulation of ERAD of misfolded null Hong Kong alpha1-antitrypsin by Golgi alpha1,2-mannosidases
-
Hosokawa N., You Z., Tremblay L.O., Nagata K., and Herscovics A. Stimulation of ERAD of misfolded null Hong Kong alpha1-antitrypsin by Golgi alpha1,2-mannosidases. Biochem Biophys Res Commun 362 (2007) 626-632
-
(2007)
Biochem Biophys Res Commun
, vol.362
, pp. 626-632
-
-
Hosokawa, N.1
You, Z.2
Tremblay, L.O.3
Nagata, K.4
Herscovics, A.5
-
77
-
-
33846211417
-
ER stress (PERK/eIF2alpha phosphorylation) mediates the polyglutamine-induced LC3 conversion, an essential step for autophagy formation
-
Kouroku Y., Fujita E., Tanida I., Ueno T., Isoai A., Kumagai H., et al. ER stress (PERK/eIF2alpha phosphorylation) mediates the polyglutamine-induced LC3 conversion, an essential step for autophagy formation. Cell Death Differ 14 (2007) 230-239
-
(2007)
Cell Death Differ
, vol.14
, pp. 230-239
-
-
Kouroku, Y.1
Fujita, E.2
Tanida, I.3
Ueno, T.4
Isoai, A.5
Kumagai, H.6
-
78
-
-
33947386684
-
Endoplasmic reticulum stress: a new pathway to induce autophagy
-
Yorimitsu T., and Klionsky D.J. Endoplasmic reticulum stress: a new pathway to induce autophagy. Autophagy 3 (2007) 160-162
-
(2007)
Autophagy
, vol.3
, pp. 160-162
-
-
Yorimitsu, T.1
Klionsky, D.J.2
-
79
-
-
33749579383
-
Endoplasmic reticulum stress triggers autophagy
-
Yorimitsu T., Nair U., Yang Z., and Klionsky D.J. Endoplasmic reticulum stress triggers autophagy. J Biol Chem 281 (2006) 30299-30304
-
(2006)
J Biol Chem
, vol.281
, pp. 30299-30304
-
-
Yorimitsu, T.1
Nair, U.2
Yang, Z.3
Klionsky, D.J.4
-
80
-
-
0029788023
-
Degradation of a mutant secretory protein, alpha1-antitrypsin Z, in the endoplasmic reticulum requires proteasome activity
-
Qu D., Teckman J.H., Omura S., and Perlmutter D.H. Degradation of a mutant secretory protein, alpha1-antitrypsin Z, in the endoplasmic reticulum requires proteasome activity. J Biol Chem 271 (1996) 22791-22795
-
(1996)
J Biol Chem
, vol.271
, pp. 22791-22795
-
-
Qu, D.1
Teckman, J.H.2
Omura, S.3
Perlmutter, D.H.4
-
81
-
-
0035976919
-
The proteasome participates in degradation of mutant alpha 1-antitrypsin Z in the endoplasmic reticulum of hepatoma-derived hepatocytes
-
Teckman J.H., Burrows J., Hidvegi T., Schmidt B., Hale P.D., and Perlmutter D.H. The proteasome participates in degradation of mutant alpha 1-antitrypsin Z in the endoplasmic reticulum of hepatoma-derived hepatocytes. J Biol Chem 276 (2001) 44865-44872
-
(2001)
J Biol Chem
, vol.276
, pp. 44865-44872
-
-
Teckman, J.H.1
Burrows, J.2
Hidvegi, T.3
Schmidt, B.4
Hale, P.D.5
Perlmutter, D.H.6
-
82
-
-
0033671965
-
Retention of mutant alpha(1)-antitrypsin Z in endoplasmic reticulum is associated with an autophagic response
-
Teckman J.H., and Perlmutter D.H. Retention of mutant alpha(1)-antitrypsin Z in endoplasmic reticulum is associated with an autophagic response. Am J Physiol Gastrointest Liver Physiol 279 (2000) G961-G974
-
(2000)
Am J Physiol Gastrointest Liver Physiol
, vol.279
-
-
Teckman, J.H.1
Perlmutter, D.H.2
-
83
-
-
33645216184
-
Intracellular inclusions containing mutant alpha1-antitrypsin Z are propagated in the absence of autophagic activity
-
Kamimoto T., Shoji S., Hidvegi T., Mizushima N., Umebayashi K., Perlmutter D.H., et al. Intracellular inclusions containing mutant alpha1-antitrypsin Z are propagated in the absence of autophagic activity. J Biol Chem 281 (2006) 4467-4476
-
(2006)
J Biol Chem
, vol.281
, pp. 4467-4476
-
-
Kamimoto, T.1
Shoji, S.2
Hidvegi, T.3
Mizushima, N.4
Umebayashi, K.5
Perlmutter, D.H.6
-
84
-
-
73449083755
-
Autophagy eliminates a specific species of misfolded procollagen and plays a protective role in cell survival against ER stress
-
Ishida Y., and Nagata K. Autophagy eliminates a specific species of misfolded procollagen and plays a protective role in cell survival against ER stress. Autophagy 5 (2009) 1217-1219
-
(2009)
Autophagy
, vol.5
, pp. 1217-1219
-
-
Ishida, Y.1
Nagata, K.2
-
85
-
-
34247113888
-
Two endoplasmic reticulum-associated degradation (ERAD) systems for the novel variant of the mutant dysferlin: ubiquitin/proteasome ERAD(I) and autophagy/lysosome ERAD(II)
-
Fujita E., Kouroku Y., Isoai A., Kumagai H., Misutani A., Matsuda C., et al. Two endoplasmic reticulum-associated degradation (ERAD) systems for the novel variant of the mutant dysferlin: ubiquitin/proteasome ERAD(I) and autophagy/lysosome ERAD(II). Hum Mol Genet 16 (2007) 618-629
-
(2007)
Hum Mol Genet
, vol.16
, pp. 618-629
-
-
Fujita, E.1
Kouroku, Y.2
Isoai, A.3
Kumagai, H.4
Misutani, A.5
Matsuda, C.6
-
86
-
-
33645451010
-
Mutant fibrinogen cleared from the endoplasmic reticulum via endoplasmic reticulum-associated protein degradation and autophagy: an explanation for liver disease
-
quiz 404-5
-
Kruse K.B., Dear A., Kaltenbrun E.R., Crum B.E., George P.M., Brennan S.O., et al. Mutant fibrinogen cleared from the endoplasmic reticulum via endoplasmic reticulum-associated protein degradation and autophagy: an explanation for liver disease. Am J Pathol 168 (2006) 1299-1308 quiz 404-5
-
(2006)
Am J Pathol
, vol.168
, pp. 1299-1308
-
-
Kruse, K.B.1
Dear, A.2
Kaltenbrun, E.R.3
Crum, B.E.4
George, P.M.5
Brennan, S.O.6
-
87
-
-
66349112572
-
Autophagic elimination of misfolded procollagen aggregates in the endoplasmic reticulum as a means of cell protection
-
Ishida Y., Yamamoto A., Kitamura A., Lamande S.R., Yoshimori T., Bateman J.F., et al. Autophagic elimination of misfolded procollagen aggregates in the endoplasmic reticulum as a means of cell protection. Mol Biol Cell 20 (2009) 2744-2754
-
(2009)
Mol Biol Cell
, vol.20
, pp. 2744-2754
-
-
Ishida, Y.1
Yamamoto, A.2
Kitamura, A.3
Lamande, S.R.4
Yoshimori, T.5
Bateman, J.F.6
-
88
-
-
0025258970
-
Accumulation of the insoluble PiZ variant of human alpha 1-antitrypsin within the hepatic endoplasmic reticulum does not elevate the steady-state level of grp78/BiP
-
Graham K.S., Le A., and Sifers R.N. Accumulation of the insoluble PiZ variant of human alpha 1-antitrypsin within the hepatic endoplasmic reticulum does not elevate the steady-state level of grp78/BiP. J Biol Chem 265 (1990) 20463-20468
-
(1990)
J Biol Chem
, vol.265
, pp. 20463-20468
-
-
Graham, K.S.1
Le, A.2
Sifers, R.N.3
-
89
-
-
34948871658
-
Regulator of G Signaling 16 is a marker for the distinct endoplasmic reticulum stress state associated with aggregated mutant alpha1-antitrypsin Z in the classical form of alpha1-antitrypsin deficiency
-
Hidvegi T., Mirnics K., Hale P., Ewing M., Beckett C., and Perlmutter D.H. Regulator of G Signaling 16 is a marker for the distinct endoplasmic reticulum stress state associated with aggregated mutant alpha1-antitrypsin Z in the classical form of alpha1-antitrypsin deficiency. J Biol Chem 282 (2007) 27769-27780
-
(2007)
J Biol Chem
, vol.282
, pp. 27769-27780
-
-
Hidvegi, T.1
Mirnics, K.2
Hale, P.3
Ewing, M.4
Beckett, C.5
Perlmutter, D.H.6
-
90
-
-
34547964642
-
Expression of hereditary hemochromatosis C282Y HFE protein in HEK293 cells activates specific endoplasmic reticulum stress responses
-
Lawless M.W., Mankan A.K., White M., O'Dwyer M.J., and Norris S. Expression of hereditary hemochromatosis C282Y HFE protein in HEK293 cells activates specific endoplasmic reticulum stress responses. BMC Cell Biol 8 (2007) 30
-
(2007)
BMC Cell Biol
, vol.8
, pp. 30
-
-
Lawless, M.W.1
Mankan, A.K.2
White, M.3
O'Dwyer, M.J.4
Norris, S.5
-
91
-
-
0031081340
-
The ER-overload response: activation of NF-kappa B
-
Pahl H.L., and Baeuerle P.A. The ER-overload response: activation of NF-kappa B. Trends Biochem Sci 22 (1997) 63-67
-
(1997)
Trends Biochem Sci
, vol.22
, pp. 63-67
-
-
Pahl, H.L.1
Baeuerle, P.A.2
-
92
-
-
53849089575
-
High data output automated 3D correlative light-electron microscopy method
-
Vicidomini G., Gagliani M.C., Canfora M., Cortese K., Frosi F., Santangelo C., et al. High data output automated 3D correlative light-electron microscopy method. Traffic 9 (2008) 1-11
-
(2008)
Traffic
, vol.9
, pp. 1-11
-
-
Vicidomini, G.1
Gagliani, M.C.2
Canfora, M.3
Cortese, K.4
Frosi, F.5
Santangelo, C.6
-
93
-
-
77953148190
-
-
Cortini M, Sitia R. ERp44 and ERGIC-53 synergize in coupling efficiency and fidelity of IgM polymerization and secretion. Traffic 2010, in press.
-
Cortini M, Sitia R. ERp44 and ERGIC-53 synergize in coupling efficiency and fidelity of IgM polymerization and secretion. Traffic 2010, in press.
-
-
-
|