Mutant Tamm-Horsfall glycoprotein accumulation in endoplasmic reticulum induces apoptosis reversed by colchicine and sodium 4-phenylbutyrate

Journal of the American Society of Nephrology

Volumn 16, Issue 10, 2005, Pages 3006-3014

  Choi, Sung Won ^a   Ryu, Ok Hee ^a   Choi, Sun Jin ^a   Song, In Sun ^a   Bleyer, Anthony J ^b   Hart, Thomas C ^a  

^a NATIONAL INSTITUTE OF DENTAL AND CRANIOFACIAL RESEARCH   (United States)

^b WAKE FOREST SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

4 PHENYLBUTYRIC ACID; COLCHICINE; TAMM HORSFALL GLYCOPROTEIN; 4-PHENYLBUTYRIC ACID; ARYLBUTYRIC ACID DERIVATIVE; BLOOD GROUP ANTIGEN; MUCOPROTEIN; TAMM-HORSFALL PROTEIN;

APOPTOSIS; ARTICLE; CELL DEATH; CELL MEMBRANE; CELL VIABILITY; CONTROLLED STUDY; CULTURE MEDIUM; DEGLYCOSYLATION; DISEASE COURSE; ENDOPLASMIC RETICULUM; ENZYME LINKED IMMUNOSORBENT ASSAY; FLUORESCENCE ACTIVATED CELL SORTING; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; IMMUNOCYTOCHEMISTRY; KIDNEY CELL; KIDNEY DISEASE; PRIORITY JOURNAL; PROTEIN FOLDING; PROTEIN SECRETION; CELL CULTURE; CYTOLOGY; DRUG EFFECT; GENETICS; KIDNEY; METABOLISM; MUTATION; PRENATAL DEVELOPMENT;

APOPTOSIS; BLOOD GROUP ANTIGENS; CELLS, CULTURED; COLCHICINE; ENDOPLASMIC RETICULUM; HUMANS; KIDNEY; MUCOPROTEINS; MUTATION; PHENYLBUTYRATES;

EID: 33645258309     PISSN: 10466673     EISSN: None     Source Type: Journal    
DOI: 10.1681/ASN.2005050461     Document Type: Article

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