-
2
-
-
0028922696
-
Etiology and pathogenesis of prion diseases
-
DeArmond SJ, Prusiner SB. Etiology and pathogenesis of prion diseases. Am J Pathol 1995;146(4):785-811
-
(1995)
Am J Pathol
, vol.146
, Issue.4
, pp. 785-811
-
-
DeArmond, S.J.1
Prusiner, S.B.2
-
3
-
-
0016398968
-
Letter: Possible person-to-person transmission of Creutzfeldt-Jakob disease
-
Duffy P, Wolf J, Collins G, et al. Letter: Possible person-to-person transmission of Creutzfeldt-Jakob disease. N Engl J Med 1974;290(12):692-693
-
(1974)
N Engl J Med
, vol.290
, Issue.12
, pp. 692-693
-
-
Duffy, P.1
Wolf, J.2
Collins, G.3
-
4
-
-
0017367439
-
Dangers of accidental person to person transmission of Creutzfeldt Jakob disease by surgery
-
Bernoulli C, Siegfried J, Baumgartner G, et al. Danger of accidental person-to-person transmission of Creutzfeldt-Jakob disease by surgery. Lancet 1977;1(8009):478-479 (Pubitemid 8045134)
-
(1977)
Lancet
, vol.1
, Issue.8009
, pp. 478-479
-
-
Bernoulli, C.1
Siegfried, J.2
Baumgartner, G.3
-
5
-
-
0022363507
-
Creutzfeldt-Jakob disease in a young adult with idiopathic hypopituitarism. Possible relation to the administration of cadaveric human growth hormone
-
Koch TK, Berg BO, De Armond SJ, Gravina RF. Creutzfeldt-Jakob disease in a young adult with idiopathic hypopituitarism. Possible relation to the administration of cadaveric human growth hormone. N Engl J Med 1985;313(12):731-733 (Pubitemid 15232428)
-
(1985)
New England Journal of Medicine
, vol.313
, Issue.12
, pp. 731-733
-
-
Koch, T.K.1
Berg, B.O.2
De Armond, S.J.3
Gravina, R.F.4
-
6
-
-
0023804449
-
Creutzfeldt-Jakob disease probably acquired from a cadaveric dura mater graft. Case report
-
Thadani V, Penar PL, Partington J, et al. Creutzfeldt-Jakob disease probably acquired from a cadaveric dura mater graft. Case report. J Neurosurg 1988;69(5):766-769 (Pubitemid 18258053)
-
(1988)
Journal of Neurosurgery
, vol.69
, Issue.5
, pp. 766-769
-
-
Thadani, V.1
Penar, P.L.2
Partington, J.3
Kalb, R.4
Janssen, R.5
Schonberger, L.B.6
Rabkin, C.S.7
Prichard, J.W.8
-
7
-
-
0017643758
-
Unconventional viruses and the origin and disappearance of Kuru
-
Gajdusek DC. Unconventional viruses and the origin and disappearance of kuru. Science 1977;197(4307):943-960 (Pubitemid 8166348)
-
(1977)
Science
, vol.197
, Issue.4307
, pp. 943-960
-
-
Gajdusek, D.C.1
-
8
-
-
0030775632
-
Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent
-
Describes probable transmission of BSE to humans.
-
Bruce ME, Will RG, Ironside JW, et al. Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent. Nature 1997;389(6650):498-501 • Describes probable transmission of BSE to humans.
-
(1997)
Nature
, vol.389
, Issue.6650
, pp. 498-501
-
-
Bruce, M.E.1
Will, R.G.2
Ironside, J.W.3
-
9
-
-
0030820354
-
The same prion strain causes vCJD and BSE
-
526 Describes probable transmission of BSE to humans.
-
Hill AF, Desbruslais M, Joiner S, et al. The same prion strain causes vCJD and BSE. Nature 1997;389(6650):448-450, 526 • Describes probable transmission of BSE to humans.
-
(1997)
Nature
, vol.389
, Issue.6650
, pp. 448-450
-
-
Hill, A.F.1
Desbruslais, M.2
Joiner, S.3
-
10
-
-
33746119584
-
Variant CJD (vCJD) and bovine spongiform encephalopathy (BSE): 10 and 20 years on: part 2
-
Collee JG, Bradley R, Liberski PP. Variant CJD (vCJD) and bovine spongiform encephalopathy (BSE): 10 and 20 years on: part 2. Folia Neuropathol 2006;44(2):102-110
-
(2006)
Folia Neuropathol
, vol.44
, Issue.2
, pp. 102-110
-
-
Collee, J.G.1
Bradley, R.2
Liberski, P.P.3
-
11
-
-
0030822582
-
Prion diseases and the BSE crisis
-
Prusiner SB. Prion diseases and the BSE crisis. Science 1997;278(5336):245-251
-
(1997)
Science
, vol.278
, Issue.5336
, pp. 245-251
-
-
Prusiner, S.B.1
-
12
-
-
67650455332
-
-
Available from
-
Available from: http://www.cjd.ed.ac.uk/figures.htm
-
-
-
-
13
-
-
67650420938
-
-
Available from
-
Available from: http://niah.naro.affrc.go.jp/disease/bse/count.html
-
-
-
-
14
-
-
24644500114
-
Chronic wasting disease
-
Williams ES. Chronic wasting disease. Vet Pathol 2005;42(5):530-549
-
(2005)
Vet Pathol
, vol.42
, Issue.5
, pp. 530-549
-
-
Williams, E.S.1
-
15
-
-
1142273431
-
Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion
-
Describes the first case of possible human-to-human transmission of vCJD via blood transfusion.
-
Llewelyn CA, Hewitt PE, Knight RS, et al. Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion. Lancet 2004;363(9407):417-421 •• Describes the first case of possible human-to-human transmission of vCJD via blood transfusion.
-
(2004)
Lancet
, vol.363
, Issue.9407
, pp. 417-421
-
-
Llewelyn, C.A.1
Hewitt, P.E.2
Knight, R.S.3
-
16
-
-
4043157677
-
Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient
-
Describes possible transmission of vCJD to human carrying an M/V 129 codon via blood transfusion.
-
Peden AH, Head MW, Ritchie DL, et al. Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient. Lancet 2004;364(9433):527-529 •• Describes possible transmission of vCJD to human carrying an M/V 129 codon via blood transfusion.
-
(2004)
Lancet
, vol.364
, Issue.9433
, pp. 527-529
-
-
Peden, A.H.1
Head, M.W.2
Ritchie, D.L.3
-
17
-
-
33845227845
-
Clinical presentation and pre-mortem diagnosis of variant Creutzfeldt-Jakob disease associated with blood transfusion: A case report
-
Wroe SJ, Pal S, Siddique D, et al. Clinical presentation and pre-mortem diagnosis of variant Creutzfeldt-Jakob disease associated with blood transfusion: a case report. Lancet 2006;368(9552):2061-2067
-
(2006)
Lancet
, vol.368
, Issue.9552
, pp. 2061-2067
-
-
Wroe, S.J.1
Pal, S.2
Siddique, D.3
-
18
-
-
36549012303
-
Transfusion Transmission of Human Prion Diseases
-
DOI 10.1016/j.tmrv.2007.09.003, PII S0887796307000867
-
Zou S, Fang CT, Schonberger LB. Transfusion transmission of human prion diseases. Transfus Med Rev 2008;22(1):58-69 (Pubitemid 350184249)
-
(2008)
Transfusion Medicine Reviews
, vol.22
, Issue.1
, pp. 58-69
-
-
Zou, S.1
Fang, C.T.2
Schonberger, L.B.3
-
19
-
-
0038304770
-
Distribution of codon 129 genotype in human growth hormone-treated CJD patients in France and the UK
-
DOI 10.1016/S0140-6736(03)13867-6
-
Brandel JP, Preece M, Brown P, et al. Distribution of codon 129 genotype in human growth hormone-treated CJD patients in France and the UK. Lancet 2003;362(9378):128-130 (Pubitemid 36831026)
-
(2003)
Lancet
, vol.362
, Issue.9378
, pp. 128-130
-
-
Brandel, J.-P.1
Preece, M.2
Brown, P.3
Croes, E.4
Laplanche, J.-L.5
Agid, Y.6
Will, R.7
Alperovitch, A.8
-
20
-
-
0032573211
-
Phenotype-genotype studies in kuru: Implications for new variant Creutzfeldt-Jakob disease
-
DOI 10.1073/pnas.95.22.13239
-
Cervenakova L, Goldfarb LG, Garruto R, et al. Phenotype-genotype studies in kuru: implications for new variant Creutzfeldt-Jakob disease. Proc Natl Acad Sci USA 1998;95(22):13239-13241 (Pubitemid 28509555)
-
(1998)
Proceedings of the National Academy of Sciences of the United States of America
, vol.95
, Issue.22
, pp. 13239-13241
-
-
Cervenakova, L.1
Goldfarb, L.G.2
Garruto, R.3
Lee, H.-S.4
Gajdusek, D.C.5
Brown, P.6
-
21
-
-
10044224475
-
Human prion protein with valine 129 prevents expression of variant CJD phenotype
-
DOI 10.1126/science.1103932
-
Wadsworth JD, Asante EA, Desbruslais M, et al. Human prion protein with valine 129 prevents expression of variant CJD phenotype. Science 2004;306(5702):1793-1796 (Pubitemid 39601400)
-
(2004)
Science
, vol.306
, Issue.5702
, pp. 1793-1796
-
-
Wadsworth, J.D.F.1
Asante, E.A.2
Desbruslais, M.3
Linehan, J.M.4
Joiner, S.5
Gowland, I.6
Welch, J.7
Stone, L.8
Lloyd, S.E.9
Hill, A.F.10
Brandner, S.11
Collinge, J.12
-
22
-
-
33646059507
-
Predicting susceptibility and incubation time of human-to-human transmission of vCJD
-
Bishop MT, Hart P, Aitchison L, et al. Predicting susceptibility and incubation time of human-to-human transmission of vCJD. Lancet Neurol 2006;5(5):393-398
-
(2006)
Lancet Neurol
, vol.5
, Issue.5
, pp. 393-398
-
-
Bishop, M.T.1
Hart, P.2
Aitchison, L.3
-
23
-
-
3242716876
-
Prevalence of lymphoreticular prion protein accumulation in UK tissue samples
-
Describes a possibility of a large number of people subclinically infected by vCJD.
-
Hilton DA, Ghani AC, Conyers L, et al. Prevalence of lymphoreticular prion protein accumulation in UK tissue samples. J Pathol 2004;203(3):733-9 •• Describes a possibility of a large number of people subclinically infected by vCJD.
-
(2004)
J Pathol
, vol.203
, Issue.3
, pp. 733-739
-
-
Hilton, D.A.1
Ghani, A.C.2
Conyers, L.3
-
24
-
-
0025910229
-
Molecular biology of prion diseases
-
Prusiner SB. Molecular biology of prion diseases. Science 1991;252(5012):1515-1522
-
(1991)
Science
, vol.252
, Issue.5012
, pp. 1515-1522
-
-
Prusiner, S.B.1
-
25
-
-
0022005315
-
A cellular gene encodes scrapie PrP 27-30 protein
-
Oesch B, Westaway D, Walchli M, et al. A cellular gene encodes scrapie PrP 27-30 protein. Cell 1985;40(4):735-746 (Pubitemid 15240279)
-
(1985)
Cell
, vol.40
, Issue.4
, pp. 735-746
-
-
Oesch, B.1
Westaway, D.2
Walchli, M.3
-
26
-
-
0027319326
-
Mice devoid of PrP are resistant to scrapie
-
DOI 10.1016/0092-8674(93)90360-3
-
Bueler H, Aguzzi A, Sailer A, et al. Mice devoid of PrP are resistant to scrapie. Cell 1993;73(7):1339-1347 (Pubitemid 23201147)
-
(1993)
Cell
, vol.73
, Issue.7
, pp. 1339-1347
-
-
Bueler, H.1
Aguzzi, A.2
Sailer, A.3
Greiner, R.-A.4
Autenried, P.5
Aguet, M.6
Weissmann, C.7
-
27
-
-
0027491308
-
Ablation of the prion protein (PrP) gene in mice prevents scrapie and facilitates production of anti-PrP antibodies
-
DOI 10.1073/pnas.90.22.10608
-
Prusiner SB, Groth D, Serban A, et al. Ablation of the prion protein (PrP) gene in mice prevents scrapie and facilitates production of anti-PrP antibodies. Proc Natl Acad Sci USA 1993;90(22):10608-10612 (Pubitemid 23347091)
-
(1993)
Proceedings of the National Academy of Sciences of the United States of America
, vol.90
, Issue.22
, pp. 10608-10612
-
-
Prusiner, S.B.1
Groth, D.2
Serban, A.3
Koehler, R.4
Foster, D.5
Torchia, M.6
Burton, D.7
Yang, S.-L.8
Dearmond, S.J.9
-
28
-
-
0028820122
-
Accumulation of proteinase K-resistant prion protein (PrP) is restricted by the expression level of normal PrP in mice inoculated with a mouse-adapted strain of the Creutzfeldt-Jakob disease agent
-
Sakaguchi S, Katamine S, Shigematsu K, et al. Accumulation of proteinase K-resistant prion protein (PrP) is restricted by the expression level of normal PrP in mice inoculated with a mouse-adapted strain of the Creutzfeldt-Jakob disease agent. J Virol 1995;69(12):7586-7592
-
(1995)
J Virol
, vol.69
, Issue.12
, pp. 7586-7592
-
-
Sakaguchi, S.1
Katamine, S.2
Shigematsu, K.3
-
29
-
-
0028703452
-
PrP gene dosage determines the timing but not the final intensity or distribution of lesions in scrapie pathology
-
Manson JC, Clarke AR, McBride PA, et al. PrP gene dosage determines the timing but not the final intensity or distribution of lesions in scrapie pathology. Neurodegeneration 1994;3(4):331-340
-
(1994)
Neurodegeneration
, vol.3
, Issue.4
, pp. 331-340
-
-
Manson, J.C.1
Clarke, A.R.2
McBride, P.A.3
-
30
-
-
0242363656
-
Depleting Neuronal PrP in Prion Infection Prevents Disease and Reverses Spongiosis
-
DOI 10.1126/science.1090187
-
Mallucci G, Dickinson A, Linehan J, et al. Depleting neuronal PrP in prion infection prevents disease and reverses spongiosis. Science 2003;302(5646):871-874 (Pubitemid 37339628)
-
(2003)
Science
, vol.302
, Issue.5646
, pp. 871-874
-
-
Mallucci, G.1
Dickinson, A.2
Linehan, J.3
Klohn, P.-C.4
Brandner, S.5
Collinge, J.6
-
31
-
-
33846538022
-
Targeting Cellular Prion Protein Reverses Early Cognitive Deficits and Neurophysiological Dysfunction in Prion-Infected Mice
-
DOI 10.1016/j.neuron.2007.01.005, PII S0896627307000086
-
Mallucci GR, White MD, Farmer M, et al. Targeting cellular prion protein reverses early cognitive deficits and neurophysiological dysfunction in prion-infected mice. Neuron 2007;53(3):325-335 (Pubitemid 46161264)
-
(2007)
Neuron
, vol.53
, Issue.3
, pp. 325-335
-
-
Mallucci, G.R.1
White, M.D.2
Farmer, M.3
Dickinson, A.4
Khatun, H.5
Powell, A.D.6
Brandner, S.7
Jefferys, J.G.R.8
Collinge, J.9
-
32
-
-
0035815709
-
In Vivo Conversion of Cellular Prion Protein to Pathogenic Isoforms, as Monitored by Conformation-specific Antibodies
-
DOI 10.1074/jbc.M008734200
-
Yokoyama T, Kimura KM, Ushiki Y, et al. Invivo conversion of cellular prion protein to pathogenic isoforms, as monitored by conformation-specific antibodies. J Biol Chem 2001;276(14):11265-11271 (Pubitemid 38089314)
-
(2001)
Journal of Biological Chemistry
, vol.276
, Issue.14
, pp. 11265-11271
-
-
Yokoyama, T.1
Kimura, K.M.2
Ushiki, Y.3
Yamada, S.4
Morooka, A.5
Nakashiba, T.6
Sassa, T.7
Itohara, S.8
-
33
-
-
15844421385
-
Altered circadian activity rhythms and sleep in mice devoid of prion protein
-
DOI 10.1038/380639a0
-
Tobler I, Gaus SE, Deboer T, et al. Altered circadian activity rhythms and sleep in mice devoid of prion protein. Nature 1996;380(6575):639-642 (Pubitemid 26119019)
-
(1996)
Nature
, vol.380
, Issue.6575
, pp. 639-642
-
-
Tobler, I.1
Gaus, S.E.2
Deboer, T.3
Achermann, P.4
Fischer, M.5
Rulicke, T.6
Moser, M.7
Oescht, B.8
McBride, P.A.9
Manson, J.C.10
-
34
-
-
0033049539
-
A mouse prion protein transgene rescues mice deficient for the prion protein gene from Purkinje cell degeneration and demyelination
-
Nishida N, Tremblay P, Sugimoto T, et al. A mouse prion protein transgene rescues mice deficient for the prion protein gene from purkinje cell degeneration and demyelination. Lab Invest 1999;79(6):689-697 (Pubitemid 29283422)
-
(1999)
Laboratory Investigation
, vol.79
, Issue.6
, pp. 689-697
-
-
Nishida, N.1
Tremblay, P.2
Sugimoto, T.3
Shigematsu, K.4
Shirabe, S.5
Petromilli, C.6
Erpel, S.P.7
Nakaoke, R.8
Atarashi, R.9
Houtani, T.10
Torchia, M.11
Sakaguchi, S.12
Dearmond, S.J.13
Prusiner, S.B.14
Katamine, S.15
-
35
-
-
0028835989
-
Fatal familial insomnia and familial Creutzfeldt-Jakob disease: Clinical, pathological and molecular features
-
Gambetti P, Parchi P, Petersen RB, et al. Fatal familial insomnia and familial Creutzfeldt-Jakob disease: clinical, pathological and molecular features. Brain Pathol 1995;5(1):43-51
-
(1995)
Brain Pathol
, vol.5
, Issue.1
, pp. 43-51
-
-
Gambetti, P.1
Parchi, P.2
Petersen, R.B.3
-
36
-
-
0026703146
-
Demyelinating peripheral neuropathy in Creutzfeldt-Jakob disease
-
Neufeld MY, Josiphov J, Korczyn AD. Demyelinating peripheral neuropathy in Creutzfeldt-Jakob disease. Muscle Nerve 1992;15(11):1234-1239
-
(1992)
Muscle Nerve
, vol.15
, Issue.11
, pp. 1234-1239
-
-
Neufeld, M.Y.1
Josiphov, J.2
Korczyn, A.D.3
-
37
-
-
0027483615
-
Neurotoxicity of a prion protein fragment
-
Forloni G, Angeretti N, Chiesa R, et al. Neurotoxicity of a prion protein fragment. Nature 1993;362(6420):543-546
-
(1993)
Nature
, vol.362
, Issue.6420
, pp. 543-546
-
-
Forloni, G.1
Angeretti, N.2
Chiesa, R.3
-
38
-
-
0027233992
-
Cytoprotective effect of NMDA receptor antagonists on prion protein (Prion (Sc))-induced toxicity in rat cortical cell cultures
-
DOI 10.1016/0922-4106(93)90040-G
-
Muller WE, Ushijima H, Schroder HC, et al. Cytoprotective effect of NMDA receptor antagonists on prion protein (PrionSc)-induced toxicity in rat cortical cell cultures. Eur J Pharmacol 1993;246(3):261-267 (Pubitemid 23253684)
-
(1993)
European Journal of Pharmacology - Molecular Pharmacology Section
, vol.246
, Issue.3
, pp. 261-267
-
-
Muller, W.E.G.1
Ushijima, H.2
Schroder, H.C.3
Forrest, J.M.S.4
Schatton, W.F.H.5
Rytik, P.G.6
Heffner-Lauc, M.7
-
39
-
-
0142105406
-
Caspase-12 and endoplasmic reticulum stress mediate neurotoxicity of pathological prion protein
-
DOI 10.1093/emboj/cdg537
-
Hetz C, Russelakis-Carneiro M, Maundrell K, et al. Caspase-12 and endoplasmic reticulum stress mediate neurotoxicity of pathological prion protein. EMBO J 2003;22(20):5435-5445 (Pubitemid 37279953)
-
(2003)
EMBO Journal
, vol.22
, Issue.20
, pp. 5435-5445
-
-
Hetz, C.1
Russelakis-Carneiro, M.2
Maundrell, K.3
Castilla, J.4
Soto, C.5
-
40
-
-
33749236787
-
A systematic review of prion therapeutics in experimental models
-
Systematically reviews anti-prion molecules.
-
Trevitt CR, Collinge J. A systematic review of prion therapeutics in experimental models. Brain 2006;129(Pt 9):2241-65 •• Systematically reviews anti-prion molecules.
-
(2006)
Brain
, vol.129
, Issue.PART 9
, pp. 2241-2265
-
-
Trevitt, C.R.1
Collinge, J.2
-
41
-
-
39749110601
-
Recent developments in therapeutics for prion diseases
-
Systematically reviews anti-prion molecules.
-
Sakaguchi S. Recent developments in therapeutics for prion diseases. Expert Opin Ther Patents 2008;18(1):35-59 •• Systematically reviews anti-prion molecules.
-
(2008)
Expert Opin Ther Patents
, vol.18
, Issue.1
, pp. 35-59
-
-
Sakaguchi, S.1
-
42
-
-
46749109619
-
The efficacy of tetracyclines in peripheral and intracerebral prion infection
-
DOI 10.1371/journal.pone.0001888
-
De Luigi A, Colombo L, Diomede L, et al. The efficacy of tetracyclines in peripheral and intracerebral prion infection. PLoS ONE 2008;3(3):e1888 (Pubitemid 351943730)
-
(2008)
PLoS ONE
, vol.3
, Issue.3
-
-
De Luigi, A.1
Colombo, L.2
Diomede, L.3
Capobianco, R.4
Mangieri, M.5
Miccolo, C.6
Limido, L.7
Forloni, G.8
Tagliavini, F.9
Salmona, M.10
-
43
-
-
33748074456
-
The 37-kDa/67-kDa laminin receptor acts as a receptor for infectious prions and is inhibited by polysulfated glycanes
-
DOI 10.1086/505914
-
Gauczynski S, Nikles D, El-Gogo S, et al. The 37-kDa/67-kDa laminin receptor acts as a receptor for infectious prions and is inhibited by polysulfated glycanes. J Infect Dis 2006;194(5):702-709 (Pubitemid 44297858)
-
(2006)
Journal of Infectious Diseases
, vol.194
, Issue.5
, pp. 702-709
-
-
Gauczynski, S.1
Nikles, D.2
El-Gogo, S.3
Papy-Garcia, D.4
Rey, C.5
Alban, S.6
Barritault, D.7
Lasmezas, C.I.8
Weiss, S.9
-
44
-
-
34248180644
-
Experimental treatments for human transmissible spongiform encephalopathies: Is there a role for pentosan polysulfate?
-
Rainov NG, Tsuboi Y, Krolak-Salmon P, et al. Experimental treatments for human transmissible spongiform encephalopathies: is there a role for pentosan polysulfate? Expert Opin Biol Ther 2007;7(5):713-726
-
(2007)
Expert Opin Biol Ther
, vol.7
, Issue.5
, pp. 713-726
-
-
Rainov, N.G.1
Tsuboi, Y.2
Krolak-Salmon, P.3
-
45
-
-
41849091490
-
Intraventricular pentosan polysulphate in human prion diseases: An observational study in the UK
-
Bone I, Belton L, Walker AS, Darbyshire J. Intraventricular pentosan polysulphate in human prion diseases: an observational study in the UK. Eur J Neurol 2008;15(5):458-464
-
(2008)
Eur J Neurol
, vol.15
, Issue.5
, pp. 458-464
-
-
Bone, I.1
Belton, L.2
Walker, A.S.3
Darbyshire, J.4
-
46
-
-
67650382891
-
-
Available from
-
Available from: http://www.ctu.mrc.ac.uk/studies/cjd.asp
-
-
-
-
47
-
-
1542405248
-
Results of quinacrine administration to patients with Creutzfeldt-Jakob disease
-
DOI 10.1159/000076350
-
Nakajima M, Yamada T, Kusuhara T, et al. Results of quinacrine administration to patients with Creutzfeldt-Jakob disease. Dement Geriatr Cogn Disord 2004;17(3):158-163 (Pubitemid 38339741)
-
(2004)
Dementia and Geriatric Cognitive Disorders
, vol.17
, Issue.3
, pp. 158-163
-
-
Nakajima, M.1
Yamada, T.2
Kusuhara, T.3
Furukawa, H.4
Takahashi, M.5
Yamauchi, A.6
Kataoka, Y.7
-
48
-
-
10744219944
-
Efficacy of flupirtine on cognitive function in patients with CJD: A double-blind study
-
Otto M, Cepek L, Ratzka P, et al. Efficacy of flupirtine on cognitive function in patients with CJD: a double-blind study. Neurology 2004;62(5):714-718 (Pubitemid 38298945)
-
(2004)
Neurology
, vol.62
, Issue.5
, pp. 714-718
-
-
Otto, M.1
Cepek, L.2
Ratzka, P.3
Doehlinger, S.4
Boekhoff, I.5
Wiltfang, J.6
Irle, E.7
Pergande, G.8
Ellers-Lenz, B.9
Windl, O.10
Kretzschmar, H.A.11
Poser, S.12
Prange, H.13
-
49
-
-
0035899413
-
Antibodies inhibit prion propagation and clear cell cultures of prion infectivity
-
The first paper describing a possibility of antibody-based immunotherapy against prion diseases.
-
Peretz D, Williamson RA, Kaneko K, et al. Antibodies inhibit prion propagation and clear cell cultures of prion infectivity. Nature 2001;412(6848):739-43 •• The first paper describing a possibility of antibody-based immunotherapy against prion diseases.
-
(2001)
Nature
, vol.412
, Issue.6848
, pp. 739-743
-
-
Peretz, D.1
Williamson, R.A.2
Kaneko, K.3
-
51
-
-
0032802332
-
Cellular biology of prion diseases
-
Harris DA. Cellular biology of prion diseases. Clin Microbiol Rev 1999;12(3):429-444
-
(1999)
Clin Microbiol Rev
, vol.12
, Issue.3
, pp. 429-444
-
-
Harris, D.A.1
-
52
-
-
0028867086
-
Prion protein (PrP) synthetic peptides induce cellular PrP to acquire properties of the scrapie isoform
-
Kaneko K, Peretz D, Pan KM, et al. Prion protein (PrP) synthetic peptides induce cellular PrP to acquire properties of the scrapie isoform. Proc Natl Acad Sci USA 1995;92(24):11160-11164
-
(1995)
Proc Natl Acad Sci USA
, vol.92
, Issue.24
, pp. 11160-11164
-
-
Kaneko, K.1
Peretz, D.2
Pan, K.M.3
-
53
-
-
0033564204
-
Specific binding of normal prion protein to the scrapie form via a localized domain initiates its conversion to the protease-resistant state
-
DOI 10.1093/emboj/18.12.3193
-
Horiuchi M, Caughey B. Specific binding of normal prion protein to the scrapie form via a localized domain initiates its conversion to the protease-resistant state. EMBO J 1999;18(12):3193-3203 (Pubitemid 29276566)
-
(1999)
EMBO Journal
, vol.18
, Issue.12
, pp. 3193-3203
-
-
Horiuchi, M.1
Caughey, B.2
-
54
-
-
7444235958
-
C by anti-PrP antibody prevents protease-resistant PrP formation
-
DOI 10.1099/vir.0.80113-0
-
Kim CL, Karino A, Ishiguro N, et al. Cell-surface retention of PrPC by anti-PrP antibody prevents protease-resistant PrP formation. J Gen Virol 2004;85(Pt 11):3473-3482 (Pubitemid 39445468)
-
(2004)
Journal of General Virology
, vol.85
, Issue.11
, pp. 3473-3482
-
-
Kim, C.-L.1
Karino, A.2
Ishiguro, N.3
Shinagawa, M.4
Sato, M.5
Horiuchi, M.6
-
55
-
-
1942519718
-
C degradation
-
DOI 10.1111/j.1471-4159.2004.02356.x
-
Perrier V, Solassol J, Crozet C, et al. Anti-PrP antibodies block PrPSc replication in prion-infected cell cultures by accelerating PrPC degradation. J Neurochem 2004;89(2):454-463 (Pubitemid 38495993)
-
(2004)
Journal of Neurochemistry
, vol.89
, Issue.2
, pp. 454-463
-
-
Perrier, V.1
Solassol, J.2
Crozet, C.3
Frobert, Y.4
Mourton-Gilles, C.5
Grassi, J.6
Lehmann, S.7
-
56
-
-
0031436335
-
The human 37-kDa laminin receptor precursor interacts with the prion protein in eukaryotic cells
-
The first paper describing interaction between LRP/LR and PrPC.
-
Rieger R, Edenhofer F, Lasmezas CI, Weiss S. The human 37-kDa laminin receptor precursor interacts with the prion protein in eukaryotic cells. Nat Med 1997;3(12):1383-8 •• The first paper describing interaction between LRP/LR and PrPC.
-
(1997)
Nat Med
, vol.3
, Issue.12
, pp. 1383-1388
-
-
Rieger, R.1
Edenhofer, F.2
Lasmezas, C.I.3
Weiss, S.4
-
57
-
-
17944377091
-
Identification of interaction domains of the prion protein with its 37-kDa/67-kDa laminin receptor
-
DOI 10.1093/emboj/20.21.5876
-
Hundt C, Peyrin JM, Haik S, et al. Identification of interaction domains of the prion protein with its 37-kDa/67-kDa laminin receptor. EMBO J 2001;20(21):5876-5886 (Pubitemid 33049263)
-
(2001)
EMBO Journal
, vol.20
, Issue.21
, pp. 5876-5886
-
-
Hundt, C.1
Peyrin, J.-M.2
Haik, S.3
Gauczynski, S.4
Leucht, C.5
Rieger, R.6
Riley, M.L.7
Deslys, J.-P.8
Dormont, D.9
Lasmezas, C.I.10
Weiss, S.11
-
58
-
-
17944363361
-
The 37-kDa/67-kDa laminin receptor acts as the cell-surface receptor for the cellular prion protein
-
Demonstrates LRP/LR as the receptor for PrPC.
-
Gauczynski S, Peyrin JM, Haik S, et al. The 37-kDa/67-kDa laminin receptor acts as the cell-surface receptor for the cellular prion protein. EMBO J 2001;20(21):5863-75 •• Demonstrates LRP/LR as the receptor for PrPC.
-
(2001)
EMBO J
, vol.20
, Issue.21
, pp. 5863-5875
-
-
Gauczynski, S.1
Peyrin, J.M.2
Haik, S.3
-
59
-
-
0242585507
-
Sc propagation in scrapie-infected neuronal cells
-
DOI 10.1038/sj.embor.embor768
-
Leucht C, Simoneau S, Rey C, et al. The 37 kDa/67 kDa laminin receptor is required for PrP(Sc) propagation in scrapie-infected neuronal cells. EMBO Rep 2003;4(3):290-295 (Pubitemid 36511726)
-
(2003)
EMBO Reports
, vol.4
, Issue.3
, pp. 290-295
-
-
Leucht, C.1
Simoneau, S.2
Rey, C.3
Vana, K.4
Rieger, R.5
Lasmezas, C.I.6
Weiss, S.7
-
61
-
-
33846476657
-
Novel aspects of prions, their receptor molecules, and innovative approaches for TSE therapy
-
DOI 10.1007/s10571-006-9121-1
-
Vana K, Zuber C, Nikles D, Weiss S. Novel aspects of prions, their receptor molecules, and innovative approaches for TSE therapy. Cell Mol Neurobiol 2007;27(1):107-128 (Pubitemid 46169898)
-
(2007)
Cellular and Molecular Neurobiology
, vol.27
, Issue.1
, pp. 107-128
-
-
Vana, K.1
Zuber, C.2
Nikles, D.3
Weiss, S.4
-
62
-
-
67349175936
-
LRP/LR as an alternative promising target in therapy of prion diseases, Alzheimer's disease and cancer
-
Vana K, Zuber C, Pflanz H, et al. LRP/LR as an alternative promising target in therapy of prion diseases, Alzheimer's disease and cancer. Infect Disord Drug Targets 2009;9(1):69-80
-
(2009)
Infect Disord Drug Targets
, vol.9
, Issue.1
, pp. 69-80
-
-
Vana, K.1
Zuber, C.2
Pflanz, H.3
-
63
-
-
34447650047
-
Therapeutic approaches targeting the prion receptor LRP/LR
-
DOI 10.1016/j.vetmic.2007.04.005, PII S0378113507001757, Recent Progress in Prion Research Scientific Advances Reported at the Concluding Meeting of the German TSE Research Platform
-
Zuber C, Ludewigs H, Weiss S. Therapeutic approaches targeting the prion receptor LRP/LR. Vet Microbiol 2007;123(4):387-393 (Pubitemid 47088870)
-
(2007)
Veterinary Microbiology
, vol.123
, Issue.4
, pp. 387-393
-
-
Zuber, C.1
Ludewigs, H.2
Weiss, S.3
-
64
-
-
25144445863
-
Inhibition of prion propagation in scrapie-infected mouse neuroblastoma cell lines using mouse monoclonal antibodies against prion protein
-
DOI 10.1016/j.bbrc.2005.07.063, PII S0006291X05015421
-
Miyamoto K, Nakamura N, Aosasa M, et al. Inhibition of prion propagation in scrapie-infected mouse neuroblastoma cell lines using mouse monoclonal antibodies against prion protein. Biochem Biophys Res Commun 2005;335(1):197-204 (Pubitemid 41350780)
-
(2005)
Biochemical and Biophysical Research Communications
, vol.335
, Issue.1
, pp. 197-204
-
-
Miyamoto, K.1
Nakamura, N.2
Aosasa, M.3
Nishida, N.4
Yokoyama, T.5
Horiuchi, H.6
Furusawa, S.7
Matsuda, H.8
-
65
-
-
67650423355
-
-
Medical Res Council (GB). US2006280745
-
Medical Res Council (GB). US2006280745; 2006
-
(2006)
-
-
-
66
-
-
0037422133
-
Monoclonal antibodies inhibit prion replication and delay the development of prion disease
-
Describes the first successful passive immunization against prion disease.
-
White AR, Enever P, Tayebi M, et al. Monoclonal antibodies inhibit prion replication and delay the development of prion disease. Nature 2003;422(6927):80-3 •• Describes the first successful passive immunization against prion disease.
-
(2003)
Nature
, vol.422
, Issue.6927
, pp. 80-83
-
-
White, A.R.1
Enever, P.2
Tayebi, M.3
-
67
-
-
45949096622
-
Effect of intraventricular infusion of anti-prion protein monoclonal antibodies on disease progression in prion-infected mice
-
Song CH, Furuoka H, Kim CL, et al. Effect of intraventricular infusion of anti-prion protein monoclonal antibodies on disease progression in prion-infected mice. J Gen Virol 2008;89(Pt 6):1533-1544
-
(2008)
J Gen Virol
, vol.89
, Issue.PART 6
, pp. 1533-1544
-
-
Song, C.H.1
Furuoka, H.2
Kim, C.L.3
-
68
-
-
62449307945
-
Toxic effects of intracerebral PrP antibody administration during the course of BSE infection in mice
-
Lefebvre-Roque M, Kremmer E, Gilch S, et al. Toxic effects of intracerebral PrP antibody administration during the course of BSE infection in mice. Prion 2007;1(3):198-206
-
(2007)
Prion
, vol.1
, Issue.3
, pp. 198-206
-
-
Lefebvre-Roque, M.1
Kremmer, E.2
Gilch, S.3
-
69
-
-
67650428992
-
-
Kagoshima Univ (JP); Search Inst Juridical Foundati (JP); Sugimura Kazuhisa (JP); Nakashima Toshihiro (JP). WO2006046344
-
Kagoshima Univ (JP); Search Inst Juridical Foundati (JP); Sugimura Kazuhisa (JP); Nakashima Toshihiro (JP). WO2006046344; 2006
-
(2006)
-
-
-
70
-
-
20744448499
-
Paracrine inhibition of prion propagation by anti-PrP single-chain Fv miniantibodies
-
DOI 10.1128/JVI.79.13.8330-8338.2005
-
Donofrio G, Heppner FL, Polymenidou M, et al. Paracrine inhibition of prion propagation by anti-PrP single-chain Fv miniantibodies. J Virol 2005;79(13):8330-8338 (Pubitemid 40853536)
-
(2005)
Journal of Virology
, vol.79
, Issue.13
, pp. 8330-8338
-
-
Donofrio, G.1
Heppner, F.L.2
Polymenidou, M.3
Musahl, C.4
Aguzzi, A.5
-
71
-
-
62149145178
-
Development of antibody fragments for immunotherapy of prion diseases
-
Campana V, Zentilin L, Mirabile I, et al. Development of antibody fragments for immunotherapy of prion diseases. Biochem J 2008;418(3):507-515
-
(2008)
Biochem J
, vol.418
, Issue.3
, pp. 507-515
-
-
Campana, V.1
Zentilin, L.2
Mirabile, I.3
-
72
-
-
39849085645
-
CNS delivery of vectored prion-specific single-chain antibodies felays fisease onset
-
DOI 10.1038/sj.mt.6300387, PII 6300387
-
Wuertzer CA, Sullivan MA, Qiu X, Federoff HJ. CNS delivery of vectored prion-specific single-chain antibodies delays disease onset. Mol Ther 2008;16(3):481-486 (Pubitemid 351314986)
-
(2008)
Molecular Therapy
, vol.16
, Issue.3
, pp. 481-486
-
-
Wuertzer, C.A.1
Sullivan, M.A.2
Qiu, X.3
Federoff, H.J.4
-
73
-
-
32944470807
-
Recombinant adeno-associated viral vectors as therapeutic agents to treat neurological disorders
-
DOI 10.1016/j.ymthe.2005.11.009, PII S1525001605017028
-
Mandel RJ, Manfredsson FP, Foust KD, et al. Recombinant adeno-associated viral vectors as therapeutic agents to treat neurological disorders. Mol Ther 2006;13(3):463-483 (Pubitemid 43257615)
-
(2006)
Molecular Therapy
, vol.13
, Issue.3
, pp. 463-483
-
-
Mandel, R.J.1
Manfredsson, F.P.2
Foust, K.D.3
Rising, A.4
Reimsnider, S.5
Nash, K.6
Burger, C.7
-
74
-
-
4344702714
-
Recombinant AAV-mediated gene delivery to the central nervous system
-
DOI 10.1002/jgm.506
-
Tenenbaum L, Chtarto A, Lehtonen E, et al. Recombinant AAV-mediated gene delivery to the central nervous system. J Gene Med 2004;6(Suppl 1):S212-22 (Pubitemid 40228030)
-
(2004)
Journal of Gene Medicine
, vol.6
, Issue.SUPPL. 1
-
-
Tenenbaum, L.1
Chtarto, A.2
Lehtonen, E.3
Velu, T.4
Brotchi, J.5
Levivier, M.6
-
75
-
-
47949087638
-
RAAV vector-mediated gene therapy for experimental ischemic stroke
-
Li ZJ, Wang RZ. rAAV vector-mediated gene therapy for experimental ischemic stroke. Neurol India 2008;56(2):116-121
-
(2008)
Neurol India
, vol.56
, Issue.2
, pp. 116-121
-
-
Li, Z.J.1
Wang, R.Z.2
-
76
-
-
0032853032
-
Repeated delivery of adeno-associated virus vectors to the rabbit airway
-
Beck SE, Jones LA, Chesnut K, et al. Repeated delivery of adeno-associated virus vectors to the rabbit airway. J Virol 1999;73(11):9446-9455 (Pubitemid 29487100)
-
(1999)
Journal of Virology
, vol.73
, Issue.11
, pp. 9446-9455
-
-
Beck, S.E.1
Jones, L.A.2
Chesnut, K.3
Walsh, S.M.4
Reynolds, T.C.5
Carter, B.J.6
Askin, F.B.7
Flotte, T.R.8
Guggino, W.B.9
-
77
-
-
0033960160
-
Repeat transduction in the mouse lung by using adeno-associated virus vectors with different serotypes
-
DOI 10.1128/JVI.74.3.1524-1532.2000
-
Halbert CL, Rutledge EA, Allen JM, et al. Repeat transduction in the mouse lung by using adeno-associated virus vectors with different serotypes. J Virol 2000;74(3):1524-1532 (Pubitemid 30044103)
-
(2000)
Journal of Virology
, vol.74
, Issue.3
, pp. 1524-1532
-
-
Halbert, C.L.1
Rutledge, E.A.2
Allen, J.M.3
Russell, D.W.4
Miller, A.D.5
-
78
-
-
0033585514
-
Adeno-associated virus-mediated gene transfer to the brain: Duration and modulation of expression
-
DOI 10.1089/10430349950018995
-
Lo WD, Qu G, Sferra TJ, et al. Adeno-associated virus-mediated gene transfer to the brain: duration and modulation of expression. Hum Gene Ther 1999;10(2):201-213 (Pubitemid 29070634)
-
(1999)
Human Gene Therapy
, vol.10
, Issue.2
, pp. 201-213
-
-
Lo, W.D.1
Qu, G.2
Sferra, T.J.3
Clark, R.4
Chen, R.5
Johnson, P.R.6
-
79
-
-
0036315299
-
Immunological aspects of recombinant adeno-associated virus delivery to the mammalian brain
-
DOI 10.1128/JVI.76.16.8446-8454.2002
-
Mastakov MY, Baer K, Symes CW, et al. Immunological aspects of recombinant adeno-associated virus delivery to the mammalian brain. J Virol 2002;76(16):8446-8454 (Pubitemid 34809096)
-
(2002)
Journal of Virology
, vol.76
, Issue.16
, pp. 8446-8454
-
-
Mastakov, M.Y.1
Baer, K.2
Symes, C.W.3
Leichtlein, C.B.4
Kotin, R.M.5
During, M.J.6
-
80
-
-
12144291519
-
Cross-Linking Cellular Prion Protein Triggers Neuronal Apoptosis in Vivo
-
DOI 10.1126/science.1094273
-
Solforosi L, Criado JR, McGavern DB, et al. Cross-linking cellular prion protein triggers neuronal apoptosis invivo. Science 2004;303(5663):1514-1516 (Pubitemid 38314420)
-
(2004)
Science
, vol.303
, Issue.5663
, pp. 1514-1516
-
-
Solforosi, L.1
Criado, J.R.2
McGavern, D.B.3
Wirz, S.4
Sanchez-Alavez, M.5
Sugama, S.6
Degiorgio, L.A.7
Volpe, B.T.8
Wiseman, E.9
Abalos, G.10
Masliah, E.11
Gilden, D.12
Oldstone, M.B.13
Conti, B.14
Williamson, R.A.15
-
81
-
-
42449128073
-
Anti-LRP/LR antibody W3 hampers peripheral PrPSc propagation in scrapie infected mice
-
Zuber C, Mitteregger G, Pace C, et al. Anti-LRP/LR antibody W3 hampers peripheral PrPSc propagation in scrapie infected mice. Prion 2007;1(3):207-212
-
(2007)
Prion
, vol.1
, Issue.3
, pp. 207-212
-
-
Zuber, C.1
Mitteregger, G.2
Pace, C.3
-
82
-
-
34548331958
-
Single chain Fv antibodies directed against the 37 kDa/67 kDa laminin receptor as therapeutic tools in prion diseases
-
DOI 10.1016/j.molimm.2007.04.030, PII S0161589007001976
-
Zuber C, Knackmuss S, Rey C, et al. Single chain Fv antibodies directed against the 37 kDa/67 kDa laminin receptor as therapeutic tools in prion diseases. Mol Immunol 2008;45(1):144-151 (Pubitemid 47336972)
-
(2008)
Molecular Immunology
, vol.45
, Issue.1
, pp. 144-151
-
-
Zuber, C.1
Knackmuss, S.2
Rey, C.3
Reusch, U.4
Rottgen, P.5
Frohlich, T.6
Arnold, G.J.7
Pace, C.8
Mitteregger, G.9
Kretzschmar, H.A.10
Little, M.11
Weiss, S.12
-
83
-
-
67650397215
-
-
Weiss Stefan (DE); Little Melvyn (DE); Knackmuss Stefan (DE); Rey Clemence (DE); Roettgen Peter (DE); Buettner Claudia (DE); Reusch Uwe (DE). WO2005035580
-
Weiss Stefan (DE); Little Melvyn (DE); Knackmuss Stefan (DE); Rey Clemence (DE); Roettgen Peter (DE); Buettner Claudia (DE); Reusch Uwe (DE). WO2005035580; 2005
-
(2005)
-
-
-
84
-
-
50549104374
-
Delivery of single-chain antibodies (scFvs) directed against the 37/67 kDa laminin receptor into mice via recombinant adeno-associated viral vectors for prion disease gene therapy
-
Zuber C, Mitteregger G, Schuhmann N, et al. Delivery of single-chain antibodies (scFvs) directed against the 37/67 kDa laminin receptor into mice via recombinant adeno-associated viral vectors for prion disease gene therapy. J Gen Virol 2008;89(Pt 8):2055-2061
-
(2008)
J Gen Virol
, vol.89
, Issue.PART 8
, pp. 2055-2061
-
-
Zuber, C.1
Mitteregger, G.2
Schuhmann, N.3
-
85
-
-
0037418828
-
Sc in vivo and antagonizes prion disease
-
DOI 10.1016/S0092-8674(03)00201-0
-
Meier P, Genoud N, Prinz M, et al. Soluble dimeric prion protein binds PrP(Sc) invivo and antagonizes prion disease. Cell 2003;113(1):49-60 (Pubitemid 36411959)
-
(2003)
Cell
, vol.113
, Issue.1
, pp. 49-60
-
-
Meier, P.1
Genoud, N.2
Prinz, M.3
Maissen, M.4
Rulicke, T.5
Zurbriggen, A.6
Raeber, A.J.7
Aguzzi, A.8
-
86
-
-
43449112676
-
Antiprion prophylaxis by gene transfer of a soluble prion antagonist
-
DOI 10.2353/ajpath.2008.070836
-
Genoud N, Ott D, Braun N, et al. Antiprion prophylaxis by gene transfer of a soluble prion antagonist. Am J Pathol 2008;172(5):1287-1296 (Pubitemid 351671541)
-
(2008)
American Journal of Pathology
, vol.172
, Issue.5
, pp. 1287-1296
-
-
Genoud, N.1
Ott, D.2
Braun, N.3
Prinz, M.4
Schwarz, P.5
Suter, U.6
Trono, D.7
Aguzzi, A.8
|