A mouse prion protein transgene rescues mice deficient for the prion protein gene from Purkinje cell degeneration and demyelination

Laboratory Investigation

Volumn 79, Issue 6, 1999, Pages 689-697

  Nishida, Noriyuki ^a   Tremblay, Patrick ^b,c   Sugimoto, Tetsuo ^d   Shigematsu, Kazuto ^a   Shirabe, Susumu ^e   Petromilli, Chris ^b,c   Erpel, Susanne Pilkuhn ^b,c   Nakaoke, Ryota ^a   Atarashi, Ryuichiro ^a   Houtani, Takeshi ^d   Torchia, Marilyn ^b,c   Sakaguchi, Suehiro ^a   DeArmond, Stephen J ^b,c   Prusiner, Stanley B ^b,c   Katamine, Shigeru ^a  

^a NAGASAKI UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c UNIVERSITY OF CALIFORNIA   (United States)

^d KANSAI MEDICAL UNIVERSITY   (Japan)

^e NAGASAKI UNIVERSITY HOSPITAL   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

PRION PROTEIN;

ALLELE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ATAXIA; CELL DEGENERATION; CONTROLLED STUDY; DEMYELINATION; GENE DISRUPTION; HISTOPATHOLOGY; MOUSE; NONHUMAN; PRION DISEASE; PRIORITY JOURNAL; PROTEIN DEFECT; PROTEIN EXPRESSION; PURKINJE CELL; TRANSGENE;

3' UNTRANSLATED REGIONS; ALLELES; ANIMALS; BRAIN; CRICETINAE; DEMYELINATING DISEASES; EXONS; INTRONS; MESOCRICETUS; MICE; MICE, MUTANT STRAINS; MICE, TRANSGENIC; MOTOR ACTIVITY; PERIPHERAL NERVES; PRIONS; PSYCHOMOTOR PERFORMANCE; PURKINJE CELLS; SPINAL CORD; VACUOLES;

EID: 0033049539     PISSN: 00236837     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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